IRF7 (Interferon regulatory factor 7) variants and mutations
IRF7 (also known as Interferon regulatory factor 7) is a human protein-coding gene encoding an interferon regulatory factor 7 protein. During viral infection, it drives type I interferon production, especially in plasmacytoid dendritic cells. Loss-of-function variants can predispose otherwise healthy individuals to life-threatening influenza or other severe viral infections. This analysis covers 1,188 IRF7 variants and mutations. Of these, 87% have computational variant effect predictions. Disease context includes immunodeficiency 39, hypothyroidism, and systemic lupus erythematosus. Example IRF7 variants include A2V, L3P, and A4T.
Variant analysis overview
- Gene: IRF7
- Protein: Interferon regulatory factor 7
- UniProt accession: Q92985
- Organism: Homo sapiens
- Variants analyzed: 1188
- Variant scope: all variants
- Completed: 2026-08-20
Variant and mutation evidence
- Variant composition: 871 unspecified-consequence records; 1 stop lost; 7 in-frame deletions; 143 missense variants; 130 synonymous variants; 21 frameshift variants; 1 in-frame insertions; 7 stop-gained variants; 3 splice-region variants; 4 substitution
- Prediction scores: 1,028 variants have prediction scores (87% of the analyzed set).
Clinical, disease, and population context
- Disease context: 25 disease associations are represented. Top associations: immunodeficiency 39, hypothyroidism, systemic lupus erythematosus, myxedema, type 2 diabetes mellitus, diabetes mellitus, COVID-19, systemic sclerosis, rheumatoid arthritis, myositis disease, thalassemia, autoimmune disease.
Protein structure and variant hotspots
- Protein features: 9 post-translational modification sites.
- PTM context: 21 variants overlap post-translational modification sites.
Data sources
Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, MaveDB, LitVar.
Notable IRF7 variants
Examples include A2V, L3P, A4T, A4V, P5S, E6K, E6Q, R7G. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.
- A2V (p.Ala2Val), TOPMed rs1856783835, AlphaMissense 0.62, MetaLR 0.92
- L3P (p.Leu3Pro), cosmic curated COSV52761, TOPMed rs1286419696
- A4T (p.Ala4Thr), TOPMed rs1397894327, gnomAD rs1397894327, AlphaMissense 0.16, MetaLR 0.76
- A4V (p.Ala4Val), ExAC rs776893144, gnomAD rs776893144, AlphaMissense 0.23, MetaLR 0.79
- P5S (p.Pro5Ser), Ensembl rs1856783299, AlphaMissense 0.08, MetaLR 0.61
- E6K (p.Glu6Lys), 1000Genomes rs368440136, ExAC rs368440136, TOPMed rs368440136, gnomAD rs368440136, AlphaMissense 0.30, MetaLR 0.67
- E6Q (p.Glu6Gln), 1000Genomes rs368440136, ExAC rs368440136, TOPMed rs368440136, gnomAD rs368440136
- R7G (p.Arg7Gly), TOPMed rs1367244124, AlphaMissense 0.09, MetaLR 0.79
- R7K (p.Arg7Lys), ExAC rs773962790, TOPMed rs773962790, gnomAD rs773962790, AlphaMissense 0.18, MetaLR 0.85
- R7M (p.Arg7Met), ExAC rs773962790, TOPMed rs773962790, gnomAD rs773962790, AlphaMissense 0.44, MetaLR 0.86
- R7T (p.Arg7Thr), ExAC rs773962790, TOPMed rs773962790, gnomAD rs773962790, AlphaMissense 0.17, MetaLR 0.90
- A8T (p.Ala8Thr), rs759529456, ClinGen CA5784113, ClinVar RCV001963766, ExAC rs759529456, AlphaMissense 0.12, MetaLR 0.60, Uncertain significance, Immunodeficiency 39
- A9T (p.Ala9Thr), rs1589925152, ClinGen CA378985075, ClinVar RCV000794388, TOPMed rs1589925152, AlphaMissense 0.10, MetaLR 0.56, Uncertain significance, Immunodeficiency 39
- P10A (p.Pro10Ala), TOPMed rs906854821, gnomAD rs906854821, AlphaMissense 0.09, MetaLR 0.73, Uncertain significance, Immunodeficiency 39
- P10L (p.Pro10Leu), ESP rs375150065, ExAC rs375150065, TOPMed rs375150065, gnomAD rs375150065, AlphaMissense 0.31, MetaLR 0.86
- P10R (p.Pro10Arg), ESP rs375150065, ExAC rs375150065, TOPMed rs375150065, gnomAD rs375150065, AlphaMissense 0.13, MetaLR 0.75
- R11P (p.Arg11Pro), TOPMed rs1856773081, gnomAD rs1856773081, AlphaMissense 0.47, MetaLR 0.96
- R11L (p.Arg11Leu), cosmic curated COSV52761
- V12L (p.Val12Leu), rs746593118, ClinGen CA378985025, ClinVar RCV001915518, ExAC rs746593118, AlphaMissense 0.27, MetaLR 0.78, Uncertain significance, Immunodeficiency 39
- V12M (p.Val12Met), ExAC rs746593118, TOPMed rs746593118, gnomAD rs746593118, AlphaMissense 0.52, MetaLR 0.74, Uncertain significance
- L13P (p.Leu13Pro), 1000Genomes rs532509180, ExAC rs532509180, TOPMed rs532509180, gnomAD rs532509180, AlphaMissense 0.45, MetaLR 0.93
- L13R (p.Leu13Arg), 1000Genomes rs532509180, ExAC rs532509180, TOPMed rs532509180, gnomAD rs532509180, AlphaMissense 0.12, MetaLR 0.66
- G15A (p.Gly15Ala), TOPMed rs1244336930, gnomAD rs1244336930, AlphaMissense 0.23, MetaLR 0.90
- G15E (p.Gly15Glu), TOPMed rs1244336930, gnomAD rs1244336930, cosmic curated COSV52752, AlphaMissense 0.86, MetaLR 0.93
- G15R (p.Gly15Arg), rs2493950663, ClinGen CA378984973, ClinVar RCV004359626, AlphaMissense 0.82, MetaLR 0.85, Uncertain significance, not specified
- G15V (p.Gly15Val), TOPMed rs1244336930, gnomAD rs1244336930, AlphaMissense 0.76, MetaLR 0.91
- E16D (p.Glu16Asp), TOPMed rs1487053331, gnomAD rs1487053331, AlphaMissense 0.12, MetaLR 0.65
- E16K (p.Glu16Lys), rs748516995, ClinGen CA5784107, ClinVar RCV002659619, ExAC rs748516995, AlphaMissense 0.46, MetaLR 0.85, Uncertain significance, Immunodeficiency 39
- W17* (p.Trp17Ter), ExAC rs779476655, TOPMed rs779476655, gnomAD rs779476655, CADD 38.00
- W17C (p.Trp17Cys), rs2493950396, ClinGen CA378984900, ClinVar RCV003828053, Uncertain significance, Immunodeficiency 39
- L18I (p.Leu18Ile), Ensembl rs2133151784, AlphaMissense 0.62, MetaLR 0.97
- G20E (p.Gly20Glu), TOPMed rs898220003, gnomAD rs898220003, AlphaMissense 0.23, MetaLR 0.80
- G20R (p.Gly20Arg), rs371777089, ClinGen CA5784105, cosmic curated COSV10727, ClinVar RCV003845533, AlphaMissense 0.21, MetaLR 0.86, Uncertain significance, Immunodeficiency 39
- I22T (p.Ile22Thr), gnomAD rs1298692550
- S23G (p.Ser23Gly), TOPMed rs1420766879, gnomAD rs1420766879, AlphaMissense 0.16, MetaLR 0.90
- S23N (p.Ser23Asn), cosmic curated COSV99042, ExAC rs754397896, TOPMed rs754397896, gnomAD rs754397896, AlphaMissense 0.32, MetaLR 0.83
- S23C (p.Ser23Cys), rs778688039, []
- S24T (p.Ser24Thr), gnomAD rs1362327953, AlphaMissense 0.20, MetaLR 0.95
- G25A (p.Gly25Ala), ESP rs368359584, ExAC rs368359584, TOPMed rs368359584, gnomAD rs368359584, AlphaMissense 0.44, MetaLR 0.95
- G25D (p.Gly25Asp), ESP rs368359584, ExAC rs368359584, TOPMed rs368359584, gnomAD rs368359584, AlphaMissense 0.59, MetaLR 0.96
- G25S (p.Gly25Ser), rs756244722, ClinGen CA5784102, ClinVar RCV002833483, ExAC rs756244722, AlphaMissense 0.36, MetaLR 0.96, Uncertain significance, Immunodeficiency 39
- C26S (p.Cys26Ser), Ensembl rs1856769625, AlphaMissense 0.15, MetaLR 0.61, Uncertain significance, Immunodeficiency 39
- C26W (p.Cys26Trp), rs767751130, ClinGen CA5784100, ClinVar RCV003750952, ClinVar RCV004262011, AlphaMissense 0.21, MetaLR 0.86, Uncertain significance, Immunodeficiency 39; not specified
- C26Y (p.Cys26Tyr), rs1856769625, ClinGen CA378984722, ClinVar RCV004099106, AlphaMissense 0.14, MetaLR 0.70, Uncertain significance, not specified
- Y27* (p.Tyr27Ter), gnomAD rs1856768842, CADD 24.90
- Y27F (p.Tyr27Phe), rs1856769021, ClinGen CA378984705, ClinVar RCV002040354, TOPMed rs1856769021, AlphaMissense 0.19, MetaLR 0.91, Uncertain significance, Immunodeficiency 39
- E28D (p.Glu28Asp), 1000Genomes rs11544075, ESP rs11544075, ExAC rs11544075, TOPMed rs11544075, AlphaMissense 0.26, MetaLR 0.88, Benign
- E28Q (p.Glu28Gln), ExAC rs762093032, gnomAD rs762093032, AlphaMissense 0.16, MetaLR 0.84
- Q31* (p.Gln31Ter), rs2493949409, ClinGen CA378984642, ClinVar RCV003065829, CADD 35.00, Uncertain significance
- Q31H (p.Gln31His), gnomAD rs987116011
- W32* (p.Trp32Ter), TOPMed rs918048724, gnomAD rs918048724, CADD 38.00
- W32X, rs918048724, []
- D34E (p.Asp34Glu), TOPMed rs878869194, gnomAD rs878869194, AlphaMissense 0.90, MetaLR 0.92
- E35K (p.Glu35Lys), rs757640469, ClinGen CA5783962, cosmic curated COSV52752, ClinVar RCV004355389, AlphaMissense 0.09, MetaLR 0.82, Uncertain significance
- E35A (p.Glu35Ala), ExAC rs776661844, gnomAD rs776661844, AlphaMissense 0.08, MetaLR 0.81
- E35D (p.Glu35Asp), TOPMed rs1483910273, gnomAD rs1483910273, AlphaMissense 0.11, MetaLR 0.83
- A36V (p.Ala36Val), cosmic curated COSV52754
- A36D (p.Ala36Asp), gnomAD rs1253897149, AlphaMissense 0.12, MetaLR 0.85
- A36T (p.Ala36Thr), TOPMed rs1856766807, AlphaMissense 0.10, MetaLR 0.93
- R37C (p.Arg37Cys), rs1208973721, ClinGen CA378984533, ClinVar RCV001300816, gnomAD rs1208973721, AlphaMissense 0.15, MetaLR 0.95, Uncertain significance, Immunodeficiency 39
- R37H (p.Arg37His), rs146681075, ClinGen CA5784094, ClinVar RCV000970773, ClinVar RCV003943206, AlphaMissense 0.08, MetaLR 0.84, Benign, Immunodeficiency 39
- C39R (p.Cys39Arg), ExAC rs772662853, TOPMed rs772662853, gnomAD rs772662853, AlphaMissense 0.10, MetaLR 0.55
- C39S (p.Cys39Ser), TOPMed rs1264475945, AlphaMissense 0.19, MetaLR 0.73, Uncertain significance, Immunodeficiency 39
- F40C (p.Phe40Cys), ExAC rs771740350, TOPMed rs771740350, gnomAD rs771740350, AlphaMissense 0.99, MetaLR 0.98, Uncertain significance, not specified
- R41C (p.Arg41Cys), gnomAD rs1397863257, AlphaMissense 0.62, MetaLR 0.95
- R41H (p.Arg41His), ExAC rs747813321, gnomAD rs747813321, AlphaMissense 0.71, MetaLR 0.96
- V42E (p.Val42Glu), Ensembl rs1856764764
- V42M (p.Val42Met), TOPMed rs1856764940, AlphaMissense 0.92, MetaLR 0.94
- W44* (p.Trp44Ter), ExAC rs774787715, TOPMed rs774787715, gnomAD rs774787715, CADD 44.00
- W44R (p.Trp44Arg), Ensembl rs1235007874, AlphaMissense 1.00, MetaLR 0.99
- K45N (p.Lys45Asn), cosmic curated COSV52755
- H46N (p.His46Asn), Ensembl rs1856764070, AlphaMissense 0.96, MetaLR 0.97
- H46Q (p.His46Gln), TOPMed rs959601641, gnomAD rs959601641, AlphaMissense 0.99, MetaLR 0.97
- F47S (p.Phe47Ser), ESP rs149672084, ExAC rs149672084, gnomAD rs149672084
- F47Y (p.Phe47Tyr), cosmic curated COSV52752, gnomAD rs1467978455
- R49H (p.Arg49His), ExAC rs749759655, TOPMed rs749759655, gnomAD rs749759655, AlphaMissense 0.70, MetaLR 0.96
- R49P (p.Arg49Pro), ExAC rs749759655, TOPMed rs749759655, gnomAD rs749759655, AlphaMissense 0.97, MetaLR 0.96
- K50R (p.Lys50Arg), Ensembl rs1856762995, AlphaMissense 0.10, MetaLR 0.74
- D51N (p.Asp51Asn), TOPMed rs1856762706, AlphaMissense 0.56, MetaLR 0.94
- L52M (p.Leu52Met), TOPMed rs1180965387, gnomAD rs1180965387, AlphaMissense 0.37, MetaLR 0.92
- S53N (p.Ser53Asn), TOPMed rs1308688027, gnomAD rs1308688027, AlphaMissense 0.20, MetaLR 0.70
- S53R (p.Ser53Arg), rs561433488, ClinGen CA5784084, ClinVar RCV003750581, ClinVar RCV006428108, AlphaMissense 0.61, MetaLR 0.74, Uncertain significance, not specified; Immunodeficiency 39
- E54D (p.Glu54Asp), rs2493947679, ClinGen CA378983585, ClinVar RCV003751131, AlphaMissense 0.30, MetaLR 0.87, Uncertain significance, Immunodeficiency 39
- E54K (p.Glu54Lys), rs1856761964, ClinGen CA378983589, ClinVar RCV003750355, TOPMed rs1856761964, AlphaMissense 0.44, MetaLR 0.95, Uncertain significance, Immunodeficiency 39
- A55E (p.Ala55Glu), cosmic curated COSV52764
- A55T (p.Ala55Thr), rs1196559888, ClinGen CA378983581, ClinVar RCV001968084, ClinVar RCV004631852, AlphaMissense 0.15, MetaLR 0.75, Uncertain significance, Immunodeficiency 39; not specified
- D56N (p.Asp56Asn), ExAC rs764976479, TOPMed rs764976479, gnomAD rs764976479, AlphaMissense 0.91, MetaLR 0.97
- A57G (p.Ala57Gly), rs1320063877, ClinGen CA378983566, ClinVar RCV003040097, AlphaMissense 0.49, MetaLR 0.88, Uncertain significance, Immunodeficiency 39
- A57V (p.Ala57Val), gnomAD rs1320063877, AlphaMissense 0.49, MetaLR 0.88
- R58H (p.Arg58His), rs766334448, ClinGen CA5784077, ClinVar RCV003588195, ExAC rs766334448, AlphaMissense 0.17, MetaLR 0.78, Uncertain significance, Immunodeficiency 39
- R58P (p.Arg58Pro), ExAC rs766334448, TOPMed rs766334448, gnomAD rs766334448, AlphaMissense 0.84, MetaLR 0.86, Uncertain significance
- F60L (p.Phe60Leu), gnomAD rs1446529694, AlphaMissense 1.00, MetaLR 0.98
- W63R (p.Trp63Arg), ExAC rs775868835
- A64D (p.Ala64Asp), ExAC rs770061476, AlphaMissense 0.99, MetaLR 0.98
- V65A (p.Val65Ala), Ensembl rs1589924013, AlphaMissense 0.35, MetaLR 0.93
- V65L (p.Val65Leu), gnomAD rs1464411215, AlphaMissense 0.37, MetaLR 0.84
- V65M (p.Val65Met), gnomAD rs1464411215, AlphaMissense 0.26, MetaLR 0.90
- A66V (p.Ala66Val), gnomAD rs1194352093, AlphaMissense 0.38, MetaLR 0.88
- G68E (p.Gly68Glu), cosmic curated COSV10958, ExAC rs759635258, TOPMed rs759635258, gnomAD rs759635258
- G68V (p.Gly68Val), cosmic curated COSV52752
- G68D (p.Gly68Asp), TOPMed rs1284583225, gnomAD rs1284583225, AlphaMissense 0.84, MetaLR 0.97
- G68S (p.Gly68Ser), ExAC rs760049350, gnomAD rs760049350, AlphaMissense 0.70, MetaLR 0.97, Uncertain significance, not specified
- G68C (p.Gly68Cys), cosmic curated COSV52757
- R69K (p.Arg69Lys), TOPMed rs1023236849, gnomAD rs1023236849, AlphaMissense 0.53, MetaLR 0.83
- W70* (p.Trp70Ter), TOPMed rs1056641712, gnomAD rs1056641712, CADD 38.00
- W70C (p.Trp70Cys), rs1344827949, ClinGen CA378983472, ClinVar RCV001372776, gnomAD rs1344827949, AlphaMissense 0.96, MetaLR 0.93, Uncertain significance, Immunodeficiency 39
- W70G (p.Trp70Gly), cosmic curated COSV10635, ExAC rs747086616, gnomAD rs747086616, AlphaMissense 0.74, MetaLR 0.94
- P71H (p.Pro71His), cosmic curated COSV52759
- P71T (p.Pro71Thr), ExAC rs777886720, TOPMed rs777886720, gnomAD rs777886720, AlphaMissense 0.47, MetaLR 0.86
- S73R (p.Ser73Arg), rs926854541, ClinGen CA216913168, ClinVar RCV001989560, Ensembl rs926854541, AlphaMissense 0.30, MetaLR 0.76, Uncertain significance, Immunodeficiency 39
- S73T (p.Ser73Thr), ExAC rs748320261, gnomAD rs748320261, AlphaMissense 0.12, MetaLR 0.83
- S74I (p.Ser74Ile), gnomAD rs1278054382, AlphaMissense 0.20, MetaLR 0.76
- R75K (p.Arg75Lys), ExAC rs779855922, TOPMed rs779855922, gnomAD rs779855922, AlphaMissense 0.15, MetaLR 0.70, Uncertain significance, Immunodeficiency 39
- R75S (p.Arg75Ser), ExAC rs755880396, gnomAD rs755880396
- R75T (p.Arg75Thr), rs779855922, ClinGen CA5784036, ClinVar RCV003073761, ExAC rs779855922, AlphaMissense 0.09, MetaLR 0.69, Uncertain significance, Immunodeficiency 39
- G76E (p.Gly76Glu), rs781248490, ClinGen CA5784033, ClinVar RCV003750590, ExAC rs781248490, AlphaMissense 0.11, MetaLR 0.66, Uncertain significance, Immunodeficiency 39
- G76R (p.Gly76Arg), rs750277291, ClinGen CA5784034, ClinVar RCV001976156, ExAC rs750277291, AlphaMissense 0.19, MetaLR 0.71, Uncertain significance, Immunodeficiency 39
- G77D (p.Gly77Asp), ExAC rs757334669, TOPMed rs757334669, gnomAD rs757334669, AlphaMissense 0.10, MetaLR 0.93
- G77V (p.Gly77Val), ExAC rs757334669, TOPMed rs757334669, gnomAD rs757334669, AlphaMissense 0.13, MetaLR 0.90
- G78C (p.Gly78Cys), TOPMed rs1038112872, gnomAD rs1038112872, AlphaMissense 0.12, MetaLR 0.87
- G78D (p.Gly78Asp), rs751103357, ClinGen CA5784031, ClinVar RCV000800016, ExAC rs751103357, AlphaMissense 0.06, MetaLR 0.46, Uncertain significance, Immunodeficiency 39
- G78S (p.Gly78Ser), TOPMed rs1038112872, gnomAD rs1038112872, AlphaMissense 0.09, MetaLR 0.75
- G78V (p.Gly78Val), ExAC rs751103357, TOPMed rs751103357, gnomAD rs751103357, AlphaMissense 0.09, MetaLR 0.78, Uncertain significance
- P79L (p.Pro79Leu), gnomAD rs868179711, AlphaMissense 0.08, MetaLR 0.77
- P79Q (p.Pro79Gln), gnomAD rs868179711, AlphaMissense 0.10, MetaLR 0.75
- P80L (p.Pro80Leu), rs2493942461, ClinGen CA378983417, ClinVar RCV004403274, AlphaMissense 0.08, MetaLR 0.84, Uncertain significance, not specified
- P80T (p.Pro80Thr), ExAC rs762601707, gnomAD rs762601707, AlphaMissense 0.08, MetaLR 0.85
- P81A (p.Pro81Ala), gnomAD rs1368969102, AlphaMissense 0.06, MetaLR 0.78
- P81H (p.Pro81His), ExAC rs752325699, TOPMed rs752325699, gnomAD rs752325699, AlphaMissense 0.09, MetaLR 0.74, Uncertain significance
- P81L (p.Pro81Leu), rs752325699, ClinGen CA5784028, ClinVar RCV001917913, ExAC rs752325699, AlphaMissense 0.09, MetaLR 0.74, Uncertain significance, Immunodeficiency 39
- E82K (p.Glu82Lys), ExAC rs765588606, AlphaMissense 0.18, MetaLR 0.67, Uncertain significance, Immunodeficiency 39
- A83S (p.Ala83Ser), rs759798143, ClinGen CA5784025, ClinVar RCV001368112, ClinVar RCV004037034, AlphaMissense 0.12, MetaLR 0.74, Uncertain significance, Immunodeficiency 39; not specified
- E84A (p.Glu84Ala), rs777045773, ClinGen CA5784024, ClinVar RCV001208083, ExAC rs777045773, AlphaMissense 0.30, MetaLR 0.71, Uncertain significance, Immunodeficiency 39
- E84D (p.Glu84Asp), 1000Genomes rs545822500, TOPMed rs545822500, gnomAD rs545822500, AlphaMissense 0.56, MetaLR 0.73
- E84K (p.Glu84Lys), rs751995586, ClinGen CA216913071, ClinVar RCV001317479, TOPMed rs751995586, AlphaMissense 0.56, MetaLR 0.78, Uncertain significance, Immunodeficiency 39
- E84Q (p.Glu84Gln), TOPMed rs751995586, gnomAD rs751995586, AlphaMissense 0.34, MetaLR 0.79, Uncertain significance
- T85S (p.Thr85Ser), TOPMed rs1285426444, gnomAD rs1285426444, AlphaMissense 0.10, MetaLR 0.63
- A86E (p.Ala86Glu), ExAC rs771414323, TOPMed rs771414323, gnomAD rs771414323, AlphaMissense 0.23, MetaLR 0.77, Uncertain significance
- A86V (p.Ala86Val), rs771414323, ClinGen CA5784022, cosmic curated COSV52763, ClinVar RCV001224394, AlphaMissense 0.16, MetaLR 0.68, Uncertain significance, Immunodeficiency 39; not specified
- R88C (p.Arg88Cys), rs772072942, ClinGen CA5784019, cosmic curated COSV10458, ClinVar RCV004351086, AlphaMissense 0.75, MetaLR 0.93, Uncertain significance, not specified
- R88H (p.Arg88His), rs766683434, ClinGen CA5784018, ClinVar RCV004131313, ClinVar RCV005099709, AlphaMissense 0.69, MetaLR 0.93, Uncertain significance, Immunodeficiency 39; not specified
- A89P (p.Ala89Pro), TOPMed rs1327288971, gnomAD rs1327288971, AlphaMissense 0.50, MetaLR 0.92
- A89T (p.Ala89Thr), TOPMed rs1327288971, gnomAD rs1327288971, AlphaMissense 0.48, MetaLR 0.91
- A89V (p.Ala89Val), rs748572013, ClinGen CA5783898, cosmic curated COSV52757, ClinVar RCV003750313, AlphaMissense 0.13, MetaLR 0.83, Uncertain significance
- G90D (p.Gly90Asp), ExAC rs745658182, TOPMed rs745658182, gnomAD rs745658182, AlphaMissense 0.82, MetaLR 0.86
- G90R (p.Gly90Arg), 1000Genomes rs768959432, ExAC rs768959432, TOPMed rs768959432, gnomAD rs768959432, AlphaMissense 0.62, MetaLR 0.79, Uncertain significance
- G90S (p.Gly90Ser), rs768959432, ClinGen CA5784015, cosmic curated COSV52756, ClinVar RCV002589028, AlphaMissense 0.16, MetaLR 0.56, Uncertain significance, Immunodeficiency 39
- G90V (p.Gly90Val), ExAC rs745658182, TOPMed rs745658182, gnomAD rs745658182, AlphaMissense 0.37, MetaLR 0.79
- W91* (p.Trp91Ter), rs1416109339, ClinGen CA378983285, ClinVar RCV003750293, gnomAD rs1416109339, CADD 43.00, Uncertain significance
- T93A (p.Thr93Ala), rs953876367, TOPMed rs953876367, gnomAD rs953876367, AlphaMissense 0.81, MetaLR 0.91, Variant assessed as somatic; moderate impact.
- T93I (p.Thr93Ile), gnomAD rs1472484462, AlphaMissense 0.97, MetaLR 0.96
- T93P (p.Thr93Pro), TOPMed rs953876367, gnomAD rs953876367, AlphaMissense 0.93, MetaLR 0.96
- F95C (p.Phe95Cys), TOPMed rs1185952202, gnomAD rs1185952202, AlphaMissense 1.00, MetaLR 0.97, Uncertain significance, not specified
- F95L (p.Phe95Leu), rs781195360, ClinGen CA378983225, ClinVar RCV004094511, ExAC rs781195360, AlphaMissense 0.99, MetaLR 0.89, Uncertain significance, not specified
- F95S (p.Phe95Ser), UniProt VAR 084075, Uncertain significance
- F95Y (p.Phe95Tyr), rs1185952202, ClinGen CA378983229, ClinVar RCV004094510, TOPMed rs1185952202, AlphaMissense 0.91, MetaLR 0.97, Uncertain significance, not specified
- R96P (p.Arg96Pro), TOPMed rs1473212917, gnomAD rs1473212917, AlphaMissense 0.98, MetaLR 0.97
- L99V (p.Leu99Val), gnomAD rs943352970, AlphaMissense 0.71, MetaLR 0.97, Uncertain significance
- R100C (p.Arg100Cys), cosmic curated COSV99199, ExAC rs757871091, TOPMed rs757871091, gnomAD rs757871091, AlphaMissense 0.24, MetaLR 0.93
- R100G (p.Arg100Gly), ExAC rs757871091, TOPMed rs757871091, gnomAD rs757871091, AlphaMissense 0.31, MetaLR 0.89
- R100H (p.Arg100His), ExAC rs752300122, TOPMed rs752300122, gnomAD rs752300122, AlphaMissense 0.07, MetaLR 0.80, Uncertain significance, Immunodeficiency 39
- R100P (p.Arg100Pro), rs752300122, ClinGen CA5784007, ClinVar RCV000698192, ClinVar RCV004026434, AlphaMissense 0.90, MetaLR 0.92, Uncertain significance, Immunodeficiency 39; not specified
- S101T (p.Ser101Thr), TOPMed rs1856734240, AlphaMissense 0.50, MetaLR 0.95
- T102P (p.Thr102Pro), ExAC rs764792303, gnomAD rs764792303
- T102R (p.Thr102Arg), ExAC rs754717443, TOPMed rs754717443, gnomAD rs754717443, AlphaMissense 0.86, MetaLR 0.94
- R103C (p.Arg103Cys), rs754142854, ClinGen CA5784004, ClinVar RCV000820939, ClinVar RCV004029054, AlphaMissense 0.25, MetaLR 0.93, Uncertain significance, not specified; Immunodeficiency 39
- R103G (p.Arg103Gly), ExAC rs754142854, TOPMed rs754142854, gnomAD rs754142854, AlphaMissense 0.08, MetaLR 0.84, Uncertain significance
- R103H (p.Arg103His), rs370737637, ESP rs370737637, ExAC rs370737637, gnomAD rs370737637, AlphaMissense 0.14, MetaLR 0.89, Variant assessed as somatic; moderate impact.
- R104C (p.Arg104Cys), rs11544074, ClinGen CA216912910, ClinVar RCV003751592, TOPMed rs11544074, AlphaMissense 0.21, MetaLR 0.93, Uncertain significance, Immunodeficiency 39
- R104H (p.Arg104His), rs773728605, ExAC rs773728605, gnomAD rs773728605, AlphaMissense 0.21, MetaLR 0.92, Variant assessed as somatic; moderate impact.
- R104L (p.Arg104Leu), ExAC rs773728605, gnomAD rs773728605, AlphaMissense 0.17, MetaLR 0.85
- V106A (p.Val106Ala), 1000Genomes rs376350717, ESP rs376350717, ExAC rs376350717, TOPMed rs376350717, AlphaMissense 0.32, MetaLR 0.84, Uncertain significance
- V106E (p.Val106Glu), rs376350717, ClinGen CA5783998, ClinVar RCV000684860, 1000Genomes rs376350717, AlphaMissense 0.25, MetaLR 0.75, Uncertain significance, Immunodeficiency 39
- V106L (p.Val106Leu), 1000Genomes rs576761308, ExAC rs576761308, TOPMed rs576761308, gnomAD rs576761308, AlphaMissense 0.25, MetaLR 0.80, Uncertain significance
- V106M (p.Val106Met), rs576761308, ClinGen CA5783999, ClinVar RCV001239070, ClinVar RCV005851766, AlphaMissense 0.31, MetaLR 0.87, Uncertain significance, Immunodeficiency 39; not specified
- M107I (p.Met107Ile), rs1856731863, Ensembl rs1856731863, ClinGen CA378983081, ClinVar RCV001242798, REVEL 0.61, AlphaMissense 0.92, Uncertain significance, Immunodeficiency 39
- M107T (p.Met107Thr), Ensembl rs1856732031
- M107V (p.Met107Val), rs2133147870, ClinGen CA378983092, ClinVar RCV001971247, Ensembl rs2133147870, REVEL 0.51, AlphaMissense 0.51, Uncertain significance, Immunodeficiency 39
- L108M (p.Leu108Met), gnomAD rs1160725232, REVEL 0.38, AlphaMissense 0.32
- L108R (p.Leu108Arg), rs1286419696, ClinGen CA378983073, ClinVar RCV003752582, REVEL 0.39, AlphaMissense 0.22, Uncertain significance, Immunodeficiency 39
Public IRF7 analysis runs
- IRF7 analysis run — IRF7 (1,188 variants) — completed 2026-08-20