MAP2K1 (Q02750) variants and mutations

MAP2K1 (also known as Q02750) is a human protein-coding gene encoding a dual specificity mitogen-activated protein kinase kinase 1 protein. It phosphorylates ERK1 and ERK2 downstream of RAF and thereby propagates RAS-MAPK growth and developmental signals. Activating somatic variants occur in several cancers, while germline activating variants can cause cardio-facio-cutaneous syndrome and related RASopathies. This analysis covers 1,428 MAP2K1 variants and mutations. Of these, 55% have computational variant effect predictions. Disease context includes cardiofaciocutaneous syndrome, cardiofaciocutaneous syndrome 3, and melanoma. Example MAP2K1 variants include P2L, P2R, and P2T.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, ClinGen, MaveDB, LitVar.

Notable MAP2K1 variants

Examples include P2L, P2R, P2T, P2S, P2H, P2P, K3R, K3E. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.