IRS1 (Insulin receptor substrate 1) variants and mutations
IRS1 (also known as Insulin receptor substrate 1) is a human protein-coding gene encoding an insulin receptor substrate 1 protein. It acts as a major intracellular docking protein for insulin and IGF-1 receptors, transmitting signals to PI3K-AKT and other metabolic pathways. Common and rare variation can influence insulin sensitivity and type 2 diabetes risk, although effects are often context dependent. This analysis covers 2,074 IRS1 variants and mutations. Of these, 88% have computational variant effect predictions. Disease context includes type 2 diabetes mellitus, Abnormality of the skeletal system, and cancer. Example IRS1 variants include A2E, A2T, and P4S.
Variant analysis overview
- Gene: IRS1
- Protein: Insulin receptor substrate 1
- UniProt accession: P35568
- Organism: Homo sapiens
- Variants analyzed: 2074
- Variant scope: all variants
- Completed: 2026-08-22
Variant and mutation evidence
- Variant composition: 1,603 unspecified-consequence records; 1 stop retained variant; 201 synonymous variants; 210 missense variants; 11 stop-gained variants; 27 frameshift variants; 18 in-frame deletions; 3 in-frame insertions; 1 substitution
- Prediction scores: 1,826 variants have prediction scores (88% of the analyzed set).
Clinical, disease, and population context
- Disease context: 25 disease associations are represented. Top associations: type 2 diabetes mellitus, Abnormality of the skeletal system, cancer, diabetes mellitus, Hypercholesterolemia, neurodegenerative disease, metabolic syndrome, hypertensive disorder, sign or symptom, coronary artery disorder, obesity disorder, nodular goiter.
Protein structure and variant hotspots
- Protein features: 2 domains; 30 post-translational modification sites.
- Structural context: 231 variants have structural context.
- PTM context: 47 variants overlap post-translational modification sites.
Data sources
Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, MaveDB, LitVar.
Notable IRS1 variants
Examples include A2E, A2T, P4S, P5L, P5R, P5S, E6K, S7I. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.
- A2E (p.Ala2Glu), ExAC rs775030251, TOPMed rs775030251, gnomAD rs775030251, REVEL 0.24, CADD 27.70
- A2T (p.Ala2Thr), ESP rs146417400, ExAC rs146417400, TOPMed rs146417400, gnomAD rs146417400, REVEL 0.19, CADD 26.90
- P4S (p.Pro4Ser), rs1222939491, ClinGen CA350858056, ClinVar RCV004287565, TOPMed rs1222939491, REVEL 0.15, CADD 26.20, Uncertain significance, not specified
- P5L (p.Pro5Leu), gnomAD rs1379631379
- P5R (p.Pro5Arg), gnomAD rs1379631379, REVEL 0.14, CADD 23.70
- P5S (p.Pro5Ser), TOPMed rs1939817418, REVEL 0.05, CADD 21.10
- E6K (p.Glu6Lys), rs1412843577, gnomAD rs1412843577, REVEL 0.06, CADD 22.40, Variant assessed as somatic; moderate impact.
- S7I (p.Ser7Ile), Ensembl rs1939816815, REVEL 0.06, CADD 20.80
- D8H (p.Asp8His), ExAC rs745389011, gnomAD rs745389011, REVEL 0.07, CADD 22.70
- D8V (p.Asp8Val), 1000Genomes rs576335148, ExAC rs576335148, gnomAD rs576335148, REVEL 0.12, CADD 23.10
- F10V (p.Phe10Val), TOPMed rs1336606386
- S11L (p.Ser11Leu), rs747368142, NCI-TCGA Cosmic COSV5933, ExAC rs747368142, TOPMed rs747368142, REVEL 0.21, CADD 24.70, Uncertain significance, not specified
- D12E (p.Asp12Glu), TOPMed rs1204376978
- D12Y (p.Asp12Tyr), TOPMed rs1325691401, gnomAD rs1325691401, REVEL 0.57, CADD 28.00
- V13E (p.Val13Glu), TOPMed rs1482198491, REVEL 0.84, CADD 25.80
- V13L (p.Val13Leu), ExAC rs758617015, TOPMed rs758617015, gnomAD rs758617015, REVEL 0.57, CADD 25.70
- V13M (p.Val13Met), ExAC rs758617015, TOPMed rs758617015, gnomAD rs758617015, REVEL 0.67, CADD 26.60
- R14C (p.Arg14Cys), gnomAD rs1255375129
- R14G (p.Arg14Gly), gnomAD rs1255375129
- R14H (p.Arg14His), ExAC rs752822640, TOPMed rs752822640, gnomAD rs752822640, REVEL 0.46, CADD 28.90
- R14S (p.Arg14Ser), gnomAD rs1255375129
- Y18H (p.Tyr18His), TOPMed rs1939814464, REVEL 0.77, CADD 32.00
- Y18S (p.Tyr18Ser), Ensembl rs1559160372, REVEL 0.81, CADD 32.00, Uncertain significance, not specified
- R20C (p.Arg20Cys), rs1044702955, NCI-TCGA Cosmic COSV5933, TOPMed rs1044702955, MutPred 0.65, Variant assessed as somatic; moderate impact.
- R20H (p.Arg20His), rs754992737, ExAC rs754992737, TOPMed rs754992737, gnomAD rs754992737, MutPred 0.65, Uncertain significance
- R20L (p.Arg20Leu), rs754992737, ClinGen CA2143596, ClinVar RCV004403312, ExAC rs754992737, REVEL 0.55, CADD 29.20, Uncertain significance, not specified
- P22H (p.Pro22His), Ensembl rs1574667777, REVEL 0.38, CADD 25.60
- P22S (p.Pro22Ser), gnomAD rs1188313973, REVEL 0.34, CADD 25.30
- K23M (p.Lys23Met), gnomAD rs1260297833, REVEL 0.73, CADD 31.00
- S24G (p.Ser24Gly), TOPMed rs1198168717, gnomAD rs1198168717, REVEL 0.40, CADD 25.10
- S24N (p.Ser24Asn), 1000Genomes rs557991154, REVEL 0.24, CADD 24.00
- M25V (p.Met25Val), TOPMed rs1426755201, gnomAD rs1426755201, REVEL 0.49, CADD 24.10
- H26R (p.His26Arg), TOPMed rs1939812834
- R28H (p.Arg28His), 1000Genomes rs539464951, ExAC rs539464951, gnomAD rs539464951
- R28P (p.Arg28Pro), 1000Genomes rs539464951, ExAC rs539464951, gnomAD rs539464951, REVEL 0.93, CADD 32.00
- R33C (p.Arg33Cys), rs762833254, NCI-TCGA Cosmic COSV1005, ExAC rs762833254, TOPMed rs762833254, REVEL 0.72, CADD 32.00, Variant assessed as somatic; moderate impact.
- R33G (p.Arg33Gly), ExAC rs762833254, TOPMed rs762833254, gnomAD rs762833254, REVEL 0.69, CADD 28.90
- R33P (p.Arg33Pro), TOPMed rs971687069, gnomAD rs971687069, REVEL 0.81, CADD 29.90
- R33S (p.Arg33Ser), ExAC rs762833254, TOPMed rs762833254, gnomAD rs762833254, REVEL 0.66, CADD 28.30
- A34T (p.Ala34Thr), ESP rs373040435, ExAC rs373040435, TOPMed rs373040435, gnomAD rs373040435, REVEL 0.27, CADD 24.70, Uncertain significance, not specified
- A34V (p.Ala34Val), Ensembl rs2106188028, REVEL 0.45, CADD 28.40
- S36N (p.Ser36Asn), NCI-TCGA Cosmic COSV1005, Variant assessed as somatic; moderate impact.
- E37* (p.Glu37Ter), TOPMed rs1024227751, gnomAD rs1024227751
- E37D (p.Glu37Asp), rs1939811520, ClinGen CA350857239, ClinVar RCV004110139, TOPMed rs1939811520, REVEL 0.10, CADD 19.80, Uncertain significance, not specified
- E37K (p.Glu37Lys), rs1024227751, NCI-TCGA Cosmic COSV5933, TOPMed rs1024227751, REVEL 0.30, CADD 24.80, Variant assessed as somatic; moderate impact.
- E37Q (p.Glu37Gln), TOPMed rs1024227751, gnomAD rs1024227751, REVEL 0.24, CADD 26.00
- A38S (p.Ala38Ser), TOPMed rs1299700780, gnomAD rs1299700780, REVEL 0.09, CADD 16.60
- A38T (p.Ala38Thr), TOPMed rs1299700780, gnomAD rs1299700780
- A38V (p.Ala38Val), TOPMed rs1359256482, gnomAD rs1359256482, REVEL 0.14, CADD 23.20
- G40D (p.Gly40Asp), ExAC rs769578293, TOPMed rs769578293, gnomAD rs769578293, REVEL 0.32, CADD 24.10
- P41L (p.Pro41Leu), ExAC rs747512782, TOPMed rs747512782, gnomAD rs747512782, REVEL 0.67, CADD 24.90
- P41Q (p.Pro41Gln), ExAC rs747512782, TOPMed rs747512782, gnomAD rs747512782, REVEL 0.73, CADD 24.60
- P41R (p.Pro41Arg), ExAC rs747512782, TOPMed rs747512782, gnomAD rs747512782, REVEL 0.67, CADD 28.10
- P41T (p.Pro41Thr), Ensembl rs1205551108
- A42E (p.Ala42Glu), ExAC rs772277263, gnomAD rs772277263
- A42G (p.Ala42Gly), ExAC rs772277263, gnomAD rs772277263, REVEL 0.45, CADD 23.60
- A42T (p.Ala42Thr), NCI-TCGA Cosmic COSV5933, Variant assessed as somatic; moderate impact.
- A42V (p.Ala42Val), NCI-TCGA Cosmic COSV5933, Variant assessed as somatic; moderate impact.
- Y46* (p.Tyr46Ter), NCI-TCGA Cosmic COSV1005, Variant assessed as somatic; high impact.
- Y46C (p.Tyr46Cys), NCI-TCGA TCGA novel, gnomAD rs1939809926, REVEL 0.74, CADD 32.00, Variant assessed as somatic; moderate impact.
- Y46N (p.Tyr46Asn), NCI-TCGA Cosmic COSV5933, Variant assessed as somatic; moderate impact.
- Y47* (p.Tyr47Ter), TOPMed rs894297593, gnomAD rs894297593, CADD 35.00
- E48K (p.Glu48Lys), gnomAD rs1427330157, REVEL 0.52, CADD 31.00
- N49D (p.Asn49Asp), gnomAD rs1261115213
- E50D (p.Glu50Asp), TOPMed rs1251410242, gnomAD rs1251410242, REVEL 0.61, CADD 24.80
- E50K (p.Glu50Lys), gnomAD rs1469971676, REVEL 0.67, CADD 31.00
- K51N (p.Lys51Asn), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- K52R (p.Lys52Arg), gnomAD rs1939808529, REVEL 0.66, CADD 31.00
- W53* (p.Trp53Ter), Ensembl rs1574667668, CADD 38.00, Likely pathogenic
- R54L (p.Arg54Leu), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- R54Q (p.Arg54Gln), TOPMed rs1333900690, gnomAD rs1333900690, REVEL 0.31, CADD 24.80
- R54W (p.Arg54Trp), rs753900721, NCI-TCGA Cosmic COSV5933, ExAC rs753900721, TOPMed rs753900721, REVEL 0.60, CADD 27.40, Uncertain significance, not specified
- H55D (p.His55Asp), Ensembl rs2106187930
- H55Q (p.His55Gln), rs1251747307, NCI-TCGA Cosmic COSV1005, gnomAD rs1251747307, REVEL 0.28, CADD 25.70, Variant assessed as somatic; moderate impact.
- K56E (p.Lys56Glu), gnomAD rs1229507945, REVEL 0.49, CADD 30.00
- K56N (p.Lys56Asn), ExAC rs780154777, gnomAD rs780154777, REVEL 0.40, CADD 26.70
- S57L (p.Ser57Leu), NCI-TCGA TCGA novel, TOPMed rs1294206506, gnomAD rs1294206506, Variant assessed as somatic; moderate impact.
- S57W (p.Ser57Trp), TOPMed rs1294206506, gnomAD rs1294206506, REVEL 0.61, CADD 32.00
- S58I (p.Ser58Ile), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- S58R (p.Ser58Arg), TOPMed rs942929290, REVEL 0.27, CADD 27.10
- A59S (p.Ala59Ser), rs1939807252, ClinGen CA350856899, ClinVar RCV004273773, TOPMed rs1939807252, MutPred 0.33, Uncertain significance, not specified
- K61E (p.Lys61Glu), TOPMed rs1939807150
- S63A (p.Ser63Ala), TOPMed rs1490732590, gnomAD rs1490732590, REVEL 0.31, CADD 21.80
- S63L (p.Ser63Leu), TOPMed rs1234435076, gnomAD rs1234435076, REVEL 0.42, CADD 25.00
- S63W (p.Ser63Trp), TOPMed rs1234435076, gnomAD rs1234435076, REVEL 0.67, CADD 29.50, Uncertain significance, not specified
- P65H (p.Pro65His), rs764111957, ClinGen CA2143572, ClinVar RCV004221428, ExAC rs764111957, REVEL 0.58, CADD 29.70, Uncertain significance, not specified
- P65L (p.Pro65Leu), ExAC rs764111957, TOPMed rs764111957, gnomAD rs764111957, REVEL 0.58, CADD 26.30, Uncertain significance
- P65S (p.Pro65Ser), 1000Genomes rs149830479, ESP rs149830479, ExAC rs149830479, TOPMed rs149830479
- P65T (p.Pro65Thr), 1000Genomes rs149830479, ESP rs149830479, ExAC rs149830479, TOPMed rs149830479, REVEL 0.54, CADD 22.70
- L66F (p.Leu66Phe), TOPMed rs1277167453, gnomAD rs1277167453, REVEL 0.82, CADD 25.30
- L66V (p.Leu66Val), TOPMed rs1277167453, gnomAD rs1277167453, REVEL 0.76, CADD 24.70
- E67K (p.Glu67Lys), ExAC rs758065603, TOPMed rs758065603, gnomAD rs758065603, REVEL 0.46, CADD 27.70
- S68C (p.Ser68Cys), ExAC rs752608556, gnomAD rs752608556, REVEL 0.37, CADD 24.30
- S68N (p.Ser68Asn), TOPMed rs1346780306, gnomAD rs1346780306, REVEL 0.32, CADD 23.50
- S68R (p.Ser68Arg), TOPMed rs1460898587, gnomAD rs1460898587, REVEL 0.50, CADD 28.70
- C69G (p.Cys69Gly), TOPMed rs887876961, REVEL 0.89, CADD 31.00
- C69R (p.Cys69Arg), TOPMed rs887876961
- F70C (p.Phe70Cys), TOPMed rs1373053992, gnomAD rs1373053992, REVEL 0.70, CADD 31.00
- F70V (p.Phe70Val), TOPMed rs1939805502, gnomAD rs1939805502, REVEL 0.58, CADD 28.50
- I72V (p.Ile72Val), Ensembl rs1939805202
- N73S (p.Asn73Ser), ExAC rs764972527, TOPMed rs764972527, gnomAD rs764972527
- N73T (p.Asn73Thr), ExAC rs764972527, TOPMed rs764972527, gnomAD rs764972527, REVEL 0.52, CADD 27.30
- N73Y (p.Asn73Tyr), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- R75W (p.Arg75Trp), NCI-TCGA Cosmic COSV5934, REVEL 0.81, CADD 29.80, Variant assessed as somatic; moderate impact.
- S78C (p.Ser78Cys), ExAC rs776250632
- K79N (p.Lys79Asn), ExAC rs765949576, gnomAD rs765949576
- K79R (p.Lys79Arg), TOPMed rs1288365568, gnomAD rs1288365568, REVEL 0.43, CADD 28.20
- K79T (p.Lys79Thr), TOPMed rs1288365568, gnomAD rs1288365568, REVEL 0.78, CADD 29.80
- N80Y (p.Asn80Tyr), TOPMed rs1359882606
- K81T (p.Lys81Thr), NCI-TCGA Cosmic COSV1005, Variant assessed as somatic; moderate impact.
- H82R (p.His82Arg), TOPMed rs1216390122
- A85V (p.Ala85Val), TOPMed rs1939803326
- R89Q (p.Arg89Gln), NCI-TCGA Cosmic COSV5933, Variant assessed as somatic; moderate impact.
- R89W (p.Arg89Trp), gnomAD rs1349427791, REVEL 0.66, CADD 32.00
- D90G (p.Asp90Gly), ExAC rs748457020, gnomAD rs748457020
- D90N (p.Asp90Asn), ExAC rs772637039, TOPMed rs772637039, gnomAD rs772637039, REVEL 0.72, CADD 28.70
- E91D (p.Glu91Asp), ExAC rs768842504, TOPMed rs768842504, gnomAD rs768842504, REVEL 0.52, CADD 22.50
- E91G (p.Glu91Gly), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- H92Q (p.His92Gln), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- H92R (p.His92Arg), TOPMed rs1390063552, gnomAD rs1390063552, REVEL 0.53, CADD 26.30
- F93L (p.Phe93Leu), ExAC rs749548805, gnomAD rs749548805, REVEL 0.55, CADD 22.80
- A94T (p.Ala94Thr), ExAC rs780282946, TOPMed rs780282946, gnomAD rs780282946, REVEL 0.60, CADD 25.40
- I95M (p.Ile95Met), NCI-TCGA Cosmic COSV1005, Variant assessed as somatic; moderate impact.
- A96P (p.Ala96Pro), rs2469369590, ClinGen CA350856604, ClinVar RCV004354032, Uncertain significance, not specified
- A97S (p.Ala97Ser), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- D98N (p.Asp98Asn), NCI-TCGA TCGA novel, REVEL 0.50, CADD 28.50, Variant assessed as somatic; moderate impact.
- D98V (p.Asp98Val), ExAC rs756094077, gnomAD rs756094077, REVEL 0.90, CADD 29.90
- S99G (p.Ser99Gly), TOPMed rs1559160175, REVEL 0.63, CADD 26.90
- E100K (p.Glu100Lys), 1000Genomes rs570775459, ExAC rs570775459, gnomAD rs570775459, REVEL 0.81, CADD 29.00
- E102D (p.Glu102Asp), rs139921079, ClinGen CA2143553, ClinVar RCV004403307, 1000Genomes rs139921079, REVEL 0.64, CADD 23.60, Uncertain significance, not specified
- E102K (p.Glu102Lys), ESP rs377203122, ExAC rs377203122, gnomAD rs377203122, REVEL 0.84, CADD 29.50
- E102Q (p.Glu102Gln), ESP rs377203122, ExAC rs377203122, gnomAD rs377203122, REVEL 0.78, CADD 27.10
- D104G (p.Asp104Gly), NCI-TCGA TCGA novel, REVEL 0.68, CADD 31.00, Variant assessed as somatic; moderate impact.
- S105C (p.Ser105Cys), TOPMed rs1939799305
- S105I (p.Ser105Ile), gnomAD rs1249658550
- S105R (p.Ser105Arg), TOPMed rs1939799305, REVEL 0.39, CADD 24.10
- Y107* (p.Tyr107Ter), gnomAD rs1211505539, CADD 37.00
- A109P (p.Ala109Pro), gnomAD rs1486646288, REVEL 0.80, CADD 28.90
- A109S (p.Ala109Ser), gnomAD rs1486646288, REVEL 0.50, CADD 27.00
- L110F (p.Leu110Phe), NCI-TCGA Cosmic COSV1005, Variant assessed as somatic; moderate impact.
- L111P (p.Leu111Pro), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- L111V (p.Leu111Val), TOPMed rs1277545067, gnomAD rs1277545067, REVEL 0.34, CADD 18.30
- H114Y (p.His114Tyr), TOPMed rs1939798638, REVEL 0.32, CADD 24.20
- N115S (p.Asn115Ser), ExAC rs754853763, gnomAD rs754853763, REVEL 0.04, CADD 18.20
- R116C (p.Arg116Cys), rs910703300, ClinGen CA66574148, ClinVar RCV004403311, TOPMed rs910703300, REVEL 0.25, CADD 31.00, Uncertain significance, not specified
- R116G (p.Arg116Gly), TOPMed rs910703300, gnomAD rs910703300, REVEL 0.24, CADD 27.10, Uncertain significance
- R116H (p.Arg116His), 1000Genomes rs142957124, ESP rs142957124, ExAC rs142957124, TOPMed rs142957124, REVEL 0.16, CADD 24.30
- G119A (p.Gly119Ala), ESP rs372506005, ExAC rs372506005, TOPMed rs372506005, gnomAD rs372506005, REVEL 0.03, CADD 14.60
- G119S (p.Gly119Ser), Ensembl rs1939798013
- H120R (p.His120Arg), Ensembl rs1939797834, REVEL 0.06, CADD 22.70
- H120Y (p.His120Tyr), ExAC rs760035936, gnomAD rs760035936, REVEL 0.14, CADD 22.10
- H121D (p.His121Asp), TOPMed rs1294358621, gnomAD rs1294358621, REVEL 0.15, CADD 23.80
- H121Q (p.His121Gln), ExAC rs772845560, gnomAD rs772845560, REVEL 0.24, CADD 23.00
- D122E (p.Asp122Glu), 1000Genomes rs566380529, ExAC rs566380529, gnomAD rs566380529, REVEL 0.02, CADD 1.01
- D122H (p.Asp122His), TOPMed rs559822183, gnomAD rs559822183, REVEL 0.06, CADD 20.40
- D122N (p.Asp122Asn), TOPMed rs559822183, gnomAD rs559822183, REVEL 0.14, CADD 22.00
- G123* (p.Gly123Ter), TOPMed rs1401391365, gnomAD rs1401391365
- G123A (p.Gly123Ala), ESP rs200009513, ExAC rs200009513, TOPMed rs200009513, gnomAD rs200009513, REVEL 0.04, CADD 9.10
- G123E (p.Gly123Glu), ESP rs200009513, ExAC rs200009513, TOPMed rs200009513, gnomAD rs200009513, REVEL 0.05, CADD 12.00
- G123R (p.Gly123Arg), TOPMed rs1401391365, gnomAD rs1401391365, NCI-TCGA Cosmic COSV1005, REVEL 0.09, CADD 17.90, Variant assessed as somatic; moderate impact.
- A124G (p.Ala124Gly), TOPMed rs1158727052, gnomAD rs1158727052, REVEL 0.02, CADD 18.40
- A124V (p.Ala124Val), TOPMed rs1158727052, gnomAD rs1158727052
- A125E (p.Ala125Glu), ExAC rs768966933, TOPMed rs768966933, gnomAD rs768966933, REVEL 0.09, CADD 1.07
- A125V (p.Ala125Val), ExAC rs768966933, TOPMed rs768966933, gnomAD rs768966933, REVEL 0.05, CADD 4.25
- A126G (p.Ala126Gly), TOPMed rs1451271200, gnomAD rs1451271200, REVEL 0.06, CADD 6.17
- L127R (p.Leu127Arg), gnomAD rs1188452881, REVEL 0.04, CADD 9.45
- G128A (p.Gly128Ala), TOPMed rs1255364686, gnomAD rs1255364686, REVEL 0.09, CADD 14.80
- G128R (p.Gly128Arg), rs1382730133, TOPMed rs1382730133, gnomAD rs1382730133, REVEL 0.21, CADD 18.00, Uncertain significance, not specified
- A129T (p.Ala129Thr), gnomAD rs1939795940, REVEL 0.06, CADD 9.12, Uncertain significance, not specified
- A129V (p.Ala129Val), rs745927014, ExAC rs745927014, gnomAD rs745927014, REVEL 0.04, CADD 5.28, Variant assessed as somatic; moderate impact.
- G132C (p.Gly132Cys), Ensembl rs1939795710
- G132D (p.Gly132Asp), NCI-TCGA Cosmic COSV5934, Variant assessed as somatic; moderate impact.
- G133W (p.Gly133Trp), ExAC rs758241055, TOPMed rs758241055, gnomAD rs758241055, REVEL 0.17, CADD 23.70
- C136Y (p.Cys136Tyr), TOPMed rs1223567998
- S137N (p.Ser137Asn), TOPMed rs1349574681, gnomAD rs1349574681, REVEL 0.15, CADD 23.10
- S137R (p.Ser137Arg), ExAC rs748060885, TOPMed rs748060885, gnomAD rs748060885, REVEL 0.28, CADD 19.50
- G138C (p.Gly138Cys), 1000Genomes rs376142568, ESP rs376142568, ExAC rs376142568, TOPMed rs376142568, REVEL 0.23, CADD 23.00
- G138R (p.Gly138Arg), 1000Genomes rs376142568, ESP rs376142568, ExAC rs376142568, TOPMed rs376142568, REVEL 0.26, CADD 23.70
- G138S (p.Gly138Ser), 1000Genomes rs376142568, ESP rs376142568, ExAC rs376142568, TOPMed rs376142568, REVEL 0.18, CADD 16.30
- S139N (p.Ser139Asn), 1000Genomes rs529797752, ExAC rs529797752, TOPMed rs529797752, gnomAD rs529797752, REVEL 0.05, CADD 19.90
Public IRS1 analysis runs
- IRS1 analysis run — IRS1 (2,074 variants) — completed 2026-08-22