PON1 (Serum paraoxonase/arylesterase 1) variants and mutations

PON1 (also known as Serum paraoxonase/arylesterase 1) is a human protein-coding gene encoding a serum paraoxonase/arylesterase 1 protein. It hydrolyzes organophosphate metabolites and oxidized lipid products while circulating mainly on HDL particles. Common functional variants and environmental factors strongly influence enzyme activity, affecting toxicant metabolism and possibly oxidative cardiovascular processes. This analysis covers 644 PON1 variants and mutations. Of these, 80% have computational variant effect predictions. Disease context includes amyotrophic lateral sclerosis, diabetic retinopathy, and atopic eczema. Example PON1 variants include A2V, K3N, and K3R.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, AlphaFold DB, gnomAD constraint, Open Targets, MaveDB, LitVar.

Notable PON1 variants

Examples include A2V, K3N, K3R, I5T, A6V, T8I, T8S, L9F. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.