F13A1 (Coagulation factor XIII A chain) variants and mutations

F13A1 (also known as Coagulation factor XIII A chain) is a human protein-coding gene encoding a coagulation factor XIII A chain protein. After thrombin activation, it crosslinks fibrin strands and other proteins to stabilize the newly formed blood clot. Biallelic deficiency causes severe bleeding with poor wound healing and a characteristic risk of delayed bleeding and intracranial hemorrhage. This analysis covers 1,133 F13A1 variants and mutations. Of these, 93% have computational variant effect predictions. Disease context includes Factor XIII subunit A deficiency, factor XIII, A subunit, deficiency of, and congenital factor XIII deficiency. Example F13A1 variants include S2A, S2L, and S2P.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, ClinGen, MaveDB, LitVar.

Notable F13A1 variants

Examples include S2A, S2L, S2P, E3G, R6K, R6M, R6S, T7I. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.