KRT16 (Keratin, type I cytoskeletal 16) variants and mutations

KRT16 (also known as Keratin, type I cytoskeletal 16) is a human protein-coding gene encoding a keratin, type I cytoskeletal 16 protein. It is induced in mechanically stressed and repairing epithelia and helps reinforce keratinocyte intermediate filaments. Dominant pathogenic variants can cause pachyonychia congenita and focal palmoplantar keratoderma with painful hyperkeratosis. This analysis covers 910 KRT16 variants and mutations. Of these, 81% have computational variant effect predictions. Disease context includes pachyonychia congenita, palmoplantar keratoderma, nonepidermolytic, focal 1, and pachyonychia congenita 1. Example KRT16 variants include T2I, T2N, and T2P.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, AlphaFold DB, gnomAD constraint, Open Targets, MaveDB, LitVar.

Notable KRT16 variants

Examples include T2I, T2N, T2P, T2S, T3I, T3P, C4G, S5N. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.