WEE1 (Wee1-like protein kinase) variants and mutations
WEE1 (also known as Wee1-like protein kinase) is a human protein-coding gene encoding a wee1-like protein kinase protein. It restrains entry into mitosis by inhibitory phosphorylation of CDK1, giving cells time to complete DNA replication and repair damage. Tumor cells under high replication stress can depend heavily on this checkpoint, making WEE1 inhibition an anticancer strategy. This analysis covers 1,095 WEE1 variants and mutations. Of these, 87% have computational variant effect predictions. Disease context includes neurodegenerative disease, actinic keratosis, and autoimmune disorder of central nervous system. Example WEE1 variants include S2R, S2C, and S2G.
Variant analysis overview
- Gene: WEE1
- Protein: Wee1-like protein kinase
- UniProt accession: P30291
- Organism: Homo sapiens
- Variants analyzed: 1095
- Variant scope: all variants
- Completed: 2026-08-20
Variant and mutation evidence
- Variant composition: 574 unspecified-consequence records; 340 missense variants; 99 synonymous variants; 37 frameshift variants; 29 stop-gained variants; 13 in-frame deletions; 2 in-frame insertions; 1 substitution
- Prediction scores: 951 variants have prediction scores (87% of the analyzed set).
Clinical, disease, and population context
- Disease context: 25 disease associations are represented. Top associations: neurodegenerative disease, actinic keratosis, autoimmune disorder of central nervous system, squamous cell carcinoma, cutaneous squamous cell carcinoma, ovarian cancer, skin cancer, fallopian tube cancer, primary peritoneal carcinoma, skin neoplasm, skin disorder, Alzheimer disease.
Protein structure and variant hotspots
- Protein features: 1 domains; 6 binding sites; 16 post-translational modification sites.
- Structural context: 193 variants have structural context.
- PTM context: 28 variants overlap post-translational modification sites.
Data sources
Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, MaveDB, LitVar.
Notable WEE1 variants
Examples include S2R, S2C, S2G, S2I, S2T, S2N, S2S, F3L. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.
- S2R (p.Ser2Arg), gnomAD 11-9573937-A-C, REVEL 0.10, CADD 25.00
- S2C (p.Ser2Cys), gnomAD 11-9573937-A-T, REVEL 0.13, CADD 25.20
- S2G (p.Ser2Gly), gnomAD 11-9573937-A-G, REVEL 0.09, CADD 23.20
- S2I (p.Ser2Ile), gnomAD 11-9573938-G-T, REVEL 0.09, CADD 25.20
- S2T (p.Ser2Thr), gnomAD 11-9573938-G-C, REVEL 0.05, CADD 23.10
- S2N (p.Ser2Asn), gnomAD 11-9573938-G-A, REVEL 0.10, CADD 23.20
- S2S (p.Ser2Ser), rs1158607974, gnomAD 11-9573939-C-T, CADD 12.70
- F3L (p.Phe3Leu), gnomAD 11-9573940-T-C, REVEL 0.09, CADD 23.30
- F3S (p.Phe3Ser), gnomAD 11-9573941-T-C, REVEL 0.08, CADD 22.50
- F3Y (p.Phe3Tyr), gnomAD 11-9573941-T-A, REVEL 0.07, CADD 22.00
- F3F (p.Phe3Phe), rs1266159962, gnomAD 11-9573942-C-T, CADD 11.50
- L4P (p.Leu4Pro), NCI-TCGA TCGA novel, REVEL 0.17, CADD 22.90, Variant assessed as somatic; moderate impact.
- L4* (p.Leu4Ter), gnomAD 11-9573941-TC-T, CADD 21.70
- L4M (p.Leu4Met), gnomAD 11-9573943-C-A, REVEL 0.02, CADD 16.30
- L4L (p.Leu4Leu), gnomAD 11-9573943-C-T, CADD 11.10
- S5G (p.Ser5Gly), rs1490413296, ClinGen CA379640713, ClinVar RCV004269670, gnomAD rs1490413296, REVEL 0.08, CADD 22.10, Uncertain significance, not specified
- S5C (p.Ser5Cys), gnomAD 11-9573946-A-T, REVEL 0.16, CADD 23.80
- S5N (p.Ser5Asn), gnomAD 11-9573947-G-A, REVEL 0.08, CADD 23.30
- S5I (p.Ser5Ile), gnomAD 11-9573947-G-T, REVEL 0.08, CADD 25.70
- S5R (p.Ser5Arg), gnomAD 11-9573948-C-A, REVEL 0.08, CADD 22.60
- S5S (p.Ser5Ser), gnomAD 11-9573948-C-T, CADD 13.20
- R6G (p.Arg6Gly), gnomAD rs1235774372, REVEL 0.11, CADD 20.80
- R6L (p.Arg6Leu), TOPMed rs1456968233, gnomAD rs1456968233, REVEL 0.06, CADD 23.70
- R6Q (p.Arg6Gln), TOPMed rs1456968233, gnomAD rs1456968233, REVEL 0.05, CADD 23.80
- R6* (p.Arg6Ter), gnomAD 11-9573949-C-T, CADD 35.00
- R6R (p.Arg6Arg), gnomAD 11-9573949-C-A, CADD 12.90
- R6P (p.Arg6Pro), gnomAD 11-9573950-G-C, REVEL 0.11, CADD 22.90
- Q7K (p.Gln7Lys), TOPMed rs1201221715, gnomAD rs1201221715, REVEL 0.06, CADD 21.00
- Q7* (p.Gln7Ter), gnomAD 11-9573952-C-T, CADD 36.00
- Q7E (p.Gln7Glu), gnomAD 11-9573952-C-G, REVEL 0.06, CADD 22.60
- Q7R (p.Gln7Arg), gnomAD 11-9573953-A-G, REVEL 0.10, CADD 21.50
- Q7Q (p.Gln7Gln), rs1849533318, gnomAD 11-9573954-G-A, CADD 13.00
- Q7H (p.Gln7His), gnomAD 11-9573954-G-T, REVEL 0.08, CADD 20.40
- Q8H (p.Gln8His), Ensembl rs2134336890, REVEL 0.05, CADD 23.40
- Q8K (p.Gln8Lys), gnomAD 11-9573955-C-A, REVEL 0.04, CADD 21.70
- Q8* (p.Gln8Ter), gnomAD 11-9573955-C-T, CADD 36.00
- Q8R (p.Gln8Arg), gnomAD 11-9573956-A-G, REVEL 0.06, CADD 19.00
- Q8Q (p.Gln8Gln), gnomAD 11-9573957-G-A, CADD 13.10
- P9L (p.Pro9Leu), gnomAD rs1487399032, REVEL 0.04, CADD 23.90
- P9Q (p.Pro9Gln), gnomAD rs1487399032, REVEL 0.06, CADD 25.30
- P9T (p.Pro9Thr), gnomAD 11-9573958-C-A, REVEL 0.04, CADD 20.80
- P9S (p.Pro9Ser), gnomAD 11-9573958-C-T, REVEL 0.03, CADD 21.70
- P9P (p.Pro9Pro), gnomAD 11-9573960-G-C, CADD 14.30
- P10T (p.Pro10Thr), gnomAD 11-9573961-C-A, REVEL 0.03, CADD 21.30
- P10S (p.Pro10Ser), gnomAD 11-9573961-C-T, REVEL 0.03, CADD 22.00
- P10A (p.Pro10Ala), gnomAD 11-9573961-C-G, REVEL 0.04, CADD 22.90
- P10Q (p.Pro10Gln), gnomAD 11-9573962-C-A, REVEL 0.07, CADD 24.00
- P10R (p.Pro10Arg), gnomAD 11-9573962-C-G, REVEL 0.12, CADD 24.00
- P10L (p.Pro10Leu), gnomAD 11-9573962-C-T, REVEL 0.06, CADD 23.90
- P10P (p.Pro10Pro), gnomAD 11-9573963-G-A, CADD 13.10
- P11S (p.Pro11Ser), TOPMed rs1240021878, gnomAD rs1240021878, REVEL 0.03, CADD 17.80
- P11H (p.Pro11His), gnomAD 11-9573963-GC-G, CADD 24.40
- P11T (p.Pro11Thr), gnomAD 11-9573964-C-A, REVEL 0.09, CADD 17.30
- P11A (p.Pro11Ala), gnomAD 11-9573964-C-G, REVEL 0.03, CADD 17.30
- P11Q (p.Pro11Gln), gnomAD 11-9573965-C-A, REVEL 0.06, CADD 22.70
- P11R (p.Pro11Arg), gnomAD 11-9573965-C-G, REVEL 0.05, CADD 22.80
- P11L (p.Pro11Leu), gnomAD 11-9573965-C-T, REVEL 0.06, CADD 22.90
- P11P (p.Pro11Pro), rs918794101, gnomAD 11-9573966-A-G, CADD 12.30
- P12A (p.Pro12Ala), 1000Genomes rs1849533491, REVEL 0.04, CADD 14.00
- P12S (p.Pro12Ser), 1000Genomes rs1849533491, REVEL 0.06, CADD 15.00
- P12del (p.Pro12del), gnomAD 11-9573956-AGCC-A, CADD 20.30
- p.Pro12dup, gnomAD 11-9573956-A-AGCC, CADD 19.90
- P12T (p.Pro12Thr), gnomAD 11-9573967-C-A, REVEL 0.04, CADD 14.40
- P12L (p.Pro12Leu), gnomAD 11-9573968-C-T, REVEL 0.06, CADD 22.80
- P12R (p.Pro12Arg), gnomAD 11-9573968-C-G, REVEL 0.07, CADD 22.60
- P12H (p.Pro12His), gnomAD 11-9573968-C-A, REVEL 0.04, CADD 22.80
- P12P (p.Pro12Pro), gnomAD 11-9573969-C-G, CADD 12.70
- R13C (p.Arg13Cys), TOPMed rs1849533540, REVEL 0.10, CADD 23.60, Uncertain significance, not specified
- R13A (p.Arg13Ala), rs1248973455, gnomAD 11-9573966-AC-A, CADD 23.40
- R13P (p.Arg13Pro), gnomAD 11-9573966-A-AC, CADD 23.80
- R13G (p.Arg13Gly), gnomAD 11-9573970-C-G, REVEL 0.08, CADD 22.90
- R13S (p.Arg13Ser), gnomAD 11-9573970-C-A, REVEL 0.06, CADD 22.70
- R13H (p.Arg13His), gnomAD 11-9573971-G-A, REVEL 0.10, CADD 23.40
- R13L (p.Arg13Leu), gnomAD 11-9573971-G-T, REVEL 0.10, CADD 22.10
- R13R (p.Arg13Arg), gnomAD 11-9573972-C-A, CADD 7.78
- R14C (p.Arg14Cys), ExAC rs758698298, gnomAD rs758698298, REVEL 0.21, CADD 24.20
- R14S (p.Arg14Ser), ExAC rs758698298, gnomAD rs758698298, REVEL 0.08, CADD 22.30
- R14A (p.Arg14Ala), gnomAD 11-9573971-GC-G, CADD 14.80
- R14G (p.Arg14Gly), gnomAD 11-9573973-C-G, REVEL 0.11, CADD 22.30
- R14L (p.Arg14Leu), gnomAD 11-9573974-G-T, REVEL 0.02, CADD 21.50
- R14H (p.Arg14His), gnomAD 11-9573974-G-A, REVEL 0.12, CADD 23.50
- R14P (p.Arg14Pro), gnomAD 11-9573974-G-C, REVEL 0.13, CADD 22.70
- R14R (p.Arg14Arg), gnomAD 11-9573975-C-T, CADD 11.70
- A15P (p.Ala15Pro), TOPMed rs1331216603, gnomAD rs1331216603, REVEL 0.04, CADD 17.00, Uncertain significance
- A15S (p.Ala15Ser), TOPMed rs1331216603, gnomAD rs1331216603, REVEL 0.02, CADD 14.80, Uncertain significance, not specified
- A15T (p.Ala15Thr), TOPMed rs1331216603, gnomAD rs1331216603, REVEL 0.02, CADD 16.90, Uncertain significance
- A15V (p.Ala15Val), Ensembl rs1849533712, REVEL 0.04, CADD 17.30
- p.Ala15 Ser48del, gnomAD 11-9573973-CGCGCC, CADD 21.30
- A15G (p.Ala15Gly), rs1216431643, gnomAD 11-9573973-CGCGCC, CADD 24.80
- A15D (p.Ala15Asp), gnomAD 11-9573977-C-A, REVEL 0.02, CADD 18.30
- A15A (p.Ala15Ala), gnomAD 11-9573978-C-A, CADD 10.40
- G16A (p.Gly16Ala), Ensembl rs1589975648, REVEL 0.10, CADD 13.40
- G16R (p.Gly16Arg), gnomAD 11-9573979-G-A, REVEL 0.03, CADD 19.20
- G16W (p.Gly16Trp), gnomAD 11-9573979-G-T, REVEL 0.06, CADD 23.30
- G16E (p.Gly16Glu), gnomAD 11-9573980-G-A, REVEL 0.04, CADD 17.50
- G16V (p.Gly16Val), gnomAD 11-9573980-G-T, REVEL 0.05, CADD 17.20
- G16G (p.Gly16Gly), gnomAD 11-9573981-G-T, CADD 12.80
- A17R (p.Ala17Arg), gnomAD 11-9573976-GC-G, CADD 23.30
- A17G (p.Ala17Gly), gnomAD 11-9573978-C-CG, CADD 24.40
- A17T (p.Ala17Thr), gnomAD 11-9573982-G-A, REVEL 0.03, CADD 20.90
- A17S (p.Ala17Ser), gnomAD 11-9573982-G-T, REVEL 0.02, CADD 22.50
- A17E (p.Ala17Glu), gnomAD 11-9573983-C-A, REVEL 0.02, CADD 22.00
- A17V (p.Ala17Val), gnomAD 11-9573983-C-T, REVEL 0.03, CADD 18.30
- A17A (p.Ala17Ala), gnomAD 11-9573984-G-T, CADD 13.50
- A18T (p.Ala18Thr), TOPMed rs1323782444, gnomAD rs1323782444, REVEL 0.03, CADD 22.90
- A18S (p.Ala18Ser), gnomAD 11-9573985-G-T, REVEL 0.04, CADD 16.90
- A18P (p.Ala18Pro), gnomAD 11-9573985-G-C, REVEL 0.05, CADD 23.00
- A18D (p.Ala18Asp), gnomAD 11-9573986-C-A, REVEL 0.06, CADD 23.10
- A18G (p.Ala18Gly), gnomAD 11-9573986-C-G, REVEL 0.05, CADD 21.70
- A18V (p.Ala18Val), gnomAD 11-9573986-C-T, REVEL 0.06, CADD 21.20
- A18A (p.Ala18Ala), gnomAD 11-9573987-C-A, CADD 12.90
- C19G (p.Cys19Gly), gnomAD 11-9573988-T-G, REVEL 0.05, CADD 22.60
- C19S (p.Cys19Ser), gnomAD 11-9573988-TG-T, CADD 25.50
- C19R (p.Cys19Arg), gnomAD 11-9573988-T-C, REVEL 0.07, CADD 22.70
- C19Y (p.Cys19Tyr), gnomAD 11-9573989-G-A, REVEL 0.07, CADD 19.60
- C19F (p.Cys19Phe), gnomAD 11-9573989-G-T, REVEL 0.05, CADD 21.40
- C19* (p.Cys19Ter), gnomAD 11-9573990-C-A, CADD 35.00
- C19C (p.Cys19Cys), rs1476909544, gnomAD 11-9573990-C-T, CADD 14.70
- C19W (p.Cys19Trp), gnomAD 11-9573990-C-G, REVEL 0.07, CADD 22.60
- T20A (p.Thr20Ala), rs2494216086, ClinGen CA379640808, ClinVar RCV004480872, REVEL 0.03, CADD 21.50, Uncertain significance, not specified
- T20I (p.Thr20Ile), gnomAD rs1302989028, REVEL 0.03, CADD 19.40, Uncertain significance, not specified
- T20S (p.Thr20Ser), gnomAD 11-9573991-A-T, REVEL 0.04, CADD 17.50
- T20N (p.Thr20Asn), gnomAD 11-9573992-C-A, REVEL 0.01, CADD 17.80
- T20T (p.Thr20Thr), gnomAD 11-9573993-C-G, CADD 11.40
- L21C (p.Leu21Cys), gnomAD 11-9573993-CT-C, CADD 24.00
- L21L (p.Leu21Leu), gnomAD 11-9573994-T-C, CADD 13.80
- L21W (p.Leu21Trp), gnomAD 11-9573995-T-G, REVEL 0.16, CADD 28.20
- L21S (p.Leu21Ser), gnomAD 11-9573995-T-C, REVEL 0.11, CADD 27.20
- L21F (p.Leu21Phe), gnomAD 11-9573996-G-T, REVEL 0.05, CADD 23.80
- R22G (p.Arg22Gly), TOPMed rs1217796362, gnomAD rs1217796362, REVEL 0.17, CADD 23.50
- R22W (p.Arg22Trp), TOPMed rs1217796362, gnomAD rs1217796362, REVEL 0.27, CADD 26.90
- R22R (p.Arg22Arg), gnomAD 11-9573997-C-A, CADD 14.40
- R22L (p.Arg22Leu), gnomAD 11-9573998-G-T, REVEL 0.14, CADD 25.20
- R22P (p.Arg22Pro), gnomAD 11-9573998-G-C, REVEL 0.18, CADD 31.00
- R22Q (p.Arg22Gln), gnomAD 11-9573998-G-A, REVEL 0.13, CADD 29.20
- Q23E (p.Gln23Glu), TOPMed rs1456140670, gnomAD rs1456140670, REVEL 0.16, CADD 23.10
- Q23K (p.Gln23Lys), TOPMed rs1456140670, gnomAD rs1456140670, REVEL 0.14, CADD 22.30
- Q23* (p.Gln23Ter), gnomAD 11-9574000-C-T, CADD 36.00
- Q23R (p.Gln23Arg), gnomAD 11-9574001-A-G, REVEL 0.14, CADD 23.70
- Q23L (p.Gln23Leu), gnomAD 11-9574001-A-T, REVEL 0.21, CADD 24.10
- Q23H (p.Gln23His), gnomAD 11-9574002-G-T, REVEL 0.10, CADD 23.20
- Q23Q (p.Gln23Gln), rs1050412778, gnomAD 11-9574002-G-A, CADD 13.60
- K24M (p.Lys24Met), 1000Genomes rs2134336977, REVEL 0.19, CADD 28.90
- K24S (p.Lys24Ser), gnomAD 11-9574002-GA-G, CADD 27.80
- K24E (p.Lys24Glu), gnomAD 11-9574003-A-G, REVEL 0.20, CADD 28.10
- K24* (p.Lys24Ter), gnomAD 11-9574003-A-T, CADD 37.00
- K24R (p.Lys24Arg), gnomAD 11-9574004-A-G, REVEL 0.12, CADD 24.90
- K24N (p.Lys24Asn), gnomAD 11-9574005-G-C, REVEL 0.16, CADD 25.70
- K24K (p.Lys24Lys), rs2134336979, gnomAD 11-9574005-G-A, CADD 13.70
- L25L (p.Leu25Leu), gnomAD 11-9574006-C-T, CADD 14.30
- L25V (p.Leu25Val), gnomAD 11-9574006-C-G, REVEL 0.12, CADD 25.20
- L25M (p.Leu25Met), gnomAD 11-9574006-C-A, REVEL 0.12, CADD 25.60
- L25Q (p.Leu25Gln), gnomAD 11-9574007-T-A, REVEL 0.19, CADD 28.50
- L25P (p.Leu25Pro), gnomAD 11-9574007-T-C, REVEL 0.25, CADD 29.30
- I26L (p.Ile26Leu), gnomAD rs1849534084, REVEL 0.05, CADD 20.60, Uncertain significance, not specified
- I26S (p.Ile26Ser), gnomAD 11-9574007-TG-T, CADD 24.60
- I26F (p.Ile26Phe), gnomAD 11-9574009-A-T, REVEL 0.09, CADD 21.50
- I26V (p.Ile26Val), gnomAD 11-9574009-A-G, REVEL 0.04, CADD 20.10
- I26T (p.Ile26Thr), gnomAD 11-9574010-T-C, REVEL 0.04, CADD 22.50
- I26I (p.Ile26Ile), gnomAD 11-9574011-C-T, CADD 14.60
- F27L (p.Phe27Leu), Ensembl rs1849534139, REVEL 0.11, CADD 29.80
- F27del (p.Phe27del), rs1162433889, gnomAD 11-9574009-ATCT-A, CADD 21.20
- F27S (p.Phe27Ser), gnomAD 11-9574011-CT-C, CADD 29.20
- F27I (p.Phe27Ile), gnomAD 11-9574012-T-A, REVEL 0.13, CADD 29.30
- F27Y (p.Phe27Tyr), gnomAD 11-9574013-T-A, REVEL 0.13, CADD 27.50
- F27F (p.Phe27Phe), gnomAD 11-9574014-C-T, CADD 14.50
- S28L (p.Ser28Leu), TOPMed rs1470356965, gnomAD rs1470356965, REVEL 0.05, CADD 23.90
- S28P (p.Ser28Pro), TOPMed rs1319947021, REVEL 0.06, CADD 22.70
- S28A (p.Ser28Ala), gnomAD 11-9574012-TTC-T, CADD 27.80
- S28T (p.Ser28Thr), gnomAD 11-9574015-T-A, REVEL 0.05, CADD 19.50
- S28W (p.Ser28Trp), gnomAD 11-9574016-C-G, REVEL 0.17, CADD 26.70
- S28* (p.Ser28Ter), gnomAD 11-9574016-C-A, CADD 36.00
- S28S (p.Ser28Ser), gnomAD 11-9574017-G-T, CADD 9.36
- P29T (p.Pro29Thr), gnomAD 11-9574018-C-A, REVEL 0.16, CADD 23.80
- P29A (p.Pro29Ala), gnomAD 11-9574018-C-G, REVEL 0.12, CADD 23.50
- P29S (p.Pro29Ser), gnomAD 11-9574018-C-T, REVEL 0.11, CADD 24.00
- P29H (p.Pro29His), gnomAD 11-9574019-C-A, REVEL 0.20, CADD 24.40
- P29L (p.Pro29Leu), gnomAD 11-9574019-C-T, REVEL 0.18, CADD 24.70
- P29R (p.Pro29Arg), gnomAD 11-9574019-C-G, REVEL 0.18, CADD 24.40
- P29P (p.Pro29Pro), rs1178883175, gnomAD 11-9574020-C-T, CADD 9.00
Public WEE1 analysis runs
- WEE1 analysis run — WEE1 (1,095 variants) — completed 2026-08-20