CD276 (CD276 antigen) variants and mutations
CD276 (also known as CD276 antigen) is a human protein-coding gene encoding a CD276 antigen protein. It modulates immune responses and is frequently overexpressed on tumor cells and tumor-associated vasculature. Its restricted expression in many normal tissues and high expression in several cancers make it an active target for antibody, CAR-T, and radioligand strategies. This analysis covers 913 CD276 variants and mutations. Of these, 82% have computational variant effect predictions. Disease context includes response to statin, Abnormality of the skeletal system, and head and neck squamous cell carcinoma. Example CD276 variants include L2V, L2L, and L2R.
Variant analysis overview
- Gene: CD276
- Protein: CD276 antigen
- UniProt accession: Q5ZPR3
- Organism: Homo sapiens
- Variants analyzed: 913
- Variant scope: all variants
- Completed: 2026-08-21
Variant and mutation evidence
- Variant composition: 675 unspecified-consequence records; 117 missense variants; 18 frameshift variants; 89 synonymous variants; 3 in-frame insertions; 5 stop-gained variants; 3 splice-region variants; 2 in-frame deletions; 2 substitution
- Prediction scores: 745 variants have prediction scores (82% of the analyzed set).
Clinical, disease, and population context
- Disease context: 25 disease associations are represented. Top associations: response to statin, Abnormality of the skeletal system, head and neck squamous cell carcinoma, prostate cancer, cancer, non-small cell lung carcinoma, neuroblastoma, neoplasm, colorectal carcinoma, osteosarcoma, breast cancer, glioblastoma.
Protein structure and variant hotspots
- Protein features: 1 transmembrane segments; 4 domains; 7 post-translational modification sites.
- Structural context: 720 variants have structural context.
- PTM context: 9 variants overlap post-translational modification sites.
Data sources
Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, MaveDB, LitVar.
Notable CD276 variants
Examples include L2V, L2L, L2R, R3C, R3H, R3P, R4G, R4L. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.
- L2V (p.Leu2Val), NCI-TCGA Cosmic COSV1005, cosmic curated COSV10057, NCI-TCGA Cosmic COSV5920, REVEL 0.05, CADD 16.60, Variant assessed as somatic; moderate impact.
- L2L (p.Leu2Leu), gnomAD 15-73699643-C-T, CADD 6.38
- L2R (p.Leu2Arg), gnomAD 15-73699644-T-G, REVEL 0.08, CADD 10.40
- R3C (p.Arg3Cys), rs770116040, NCI-TCGA Cosmic COSV5920, cosmic curated COSV59204, ExAC rs770116040, REVEL 0.04, CADD 10.80, Variant assessed as somatic; moderate impact.
- R3H (p.Arg3His), ExAC rs775892211, TOPMed rs775892211, gnomAD rs775892211, REVEL 0.02, CADD 0.31
- R3P (p.Arg3Pro), ExAC rs775892211, TOPMed rs775892211, gnomAD rs775892211, REVEL 0.03, CADD 0.64
- R4G (p.Arg4Gly), TOPMed rs1363489468, gnomAD rs1363489468, REVEL 0.03, CADD 5.17
- R4L (p.Arg4Leu), TOPMed rs1232227175, gnomAD rs1232227175, REVEL 0.01, CADD 5.32
- R4P (p.Arg4Pro), TOPMed rs1232227175, gnomAD rs1232227175
- R4Q (p.Arg4Gln), NCI-TCGA TCGA novel, TOPMed rs1232227175, gnomAD rs1232227175, REVEL 0.02, CADD 5.34, Variant assessed as somatic; moderate impact.
- R4W (p.Arg4Trp), TOPMed rs1363489468, gnomAD rs1363489468, REVEL 0.06, CADD 14.40
- R4R (p.Arg4Arg), gnomAD 15-73699651-G-A, CADD 1.62
- R5P (p.Arg5Pro), 1000Genomes rs139808700, ESP rs139808700, ExAC rs139808700, TOPMed rs139808700
- R5Q (p.Arg5Gln), cosmic curated COSV59205, 1000Genomes rs139808700, ESP rs139808700, ExAC rs139808700, REVEL 0.01, CADD 0.41
- R5W (p.Arg5Trp), cosmic curated COSV10964, ExAC rs563669074, TOPMed rs563669074, gnomAD rs563669074, REVEL 0.05, CADD 5.36, Uncertain significance, not specified
- R5R (p.Arg5Arg), gnomAD 15-73699634-A-C, CADD 2.51
- R5G (p.Arg5Gly), rs1253236351, gnomAD 15-73699634-A-G, CADD 2.93
- R5K (p.Arg5Lys), rs759707686, gnomAD 15-73699635-G-A, CADD 9.67
- G6C (p.Gly6Cys), TOPMed rs1900300698
- G6A (p.Gly6Ala), gnomAD 15-73699652-CG-C, CADD 6.89
- G6D (p.Gly6Asp), gnomAD 15-73699656-G-A, REVEL 0.04, CADD 11.90
- G6G (p.Gly6Gly), rs1206041292, gnomAD 15-73699657-C-T, CADD 5.09
- S7I (p.Ser7Ile), gnomAD 15-73690718-G-T, CADD 0.53
- p.Ser9dup, rs1480474599, gnomAD 15-73690734-G-GTC, CADD 1.86
- S7S (p.Ser7Ser), rs1899955871, gnomAD 15-73690740-T-G, CADD 5.31
- S7T (p.Ser7Thr), gnomAD 15-73699659-G-C, REVEL 0.02, CADD 0.98
- P8S (p.Pro8Ser), ExAC rs762313492, TOPMed rs762313492, gnomAD rs762313492, REVEL 0.03, CADD 8.07
- P8T (p.Pro8Thr), rs548160217, gnomAD 15-73690729-C-A, CADD 0.57
- P8P (p.Pro8Pro), gnomAD 15-73690731-C-A, CADD 0.88
- G9S (p.Gly9Ser), gnomAD rs1900301058, REVEL 0.02, CADD 1.41
- G9G (p.Gly9Gly), rs1353825966, gnomAD 15-73699666-C-T, CADD 3.87
- M10C (p.Met10Cys), gnomAD 15-73690728-AC-A, CADD 0.19
- M10V (p.Met10Val), rs927764047, gnomAD 15-73690732-A-G, CADD 6.04
- M10L (p.Met10Leu), rs927764047, gnomAD 15-73690732-A-T, CADD 5.13
- M10S (p.Met10Ser), gnomAD 15-73699666-CATGG, CADD 25.40
- M10T (p.Met10Thr), gnomAD 15-73699668-T-C, REVEL 0.01, CADD 0.01
- M10I (p.Met10Ile), gnomAD 15-73699669-G-T, REVEL 0.01, CADD 1.07
- G11D (p.Gly11Asp), gnomAD rs1461076482
- G11R (p.Gly11Arg), gnomAD 15-73699670-G-C, REVEL 0.07, CADD 14.20
- G11V (p.Gly11Val), gnomAD 15-73699671-G-T, REVEL 0.11, CADD 19.50
- G11G (p.Gly11Gly), rs1900301422, gnomAD 15-73699672-T-G, CADD 8.57
- V12L (p.Val12Leu), ExAC rs768034811, gnomAD rs768034811, REVEL 0.02, CADD 12.20
- V12M (p.Val12Met), ExAC rs768034811, gnomAD rs768034811, REVEL 0.03, CADD 15.30
- H13L (p.His13Leu), TOPMed rs895216823, gnomAD rs895216823
- H13P (p.His13Pro), TOPMed rs895216823, gnomAD rs895216823, REVEL 0.07, CADD 0.66
- H13R (p.His13Arg), cosmic curated COSV10057, TOPMed rs895216823, gnomAD rs895216823, REVEL 0.04, CADD 0.16
- H13Q (p.His13Gln), rs1899956718, gnomAD 15-73690770-C-A, CADD 1.27
- H13N (p.His13Asn), gnomAD 15-73699601-C-A, CADD 9.29
- H13Y (p.His13Tyr), rs1900297314, gnomAD 15-73699601-C-T, CADD 9.77
- H13H (p.His13His), gnomAD 15-73699603-C-T, CADD 8.50
- V14M (p.Val14Met), gnomAD rs1474476400, REVEL 0.02, CADD 9.47
- V14A (p.Val14Ala), gnomAD 15-73699680-T-C, REVEL 0.02, CADD 8.18
- G15A (p.Gly15Ala), gnomAD rs1184694339, REVEL 0.05, CADD 3.60
- G15D (p.Gly15Asp), gnomAD rs1184694339, REVEL 0.12, CADD 8.69
- G15S (p.Gly15Ser), gnomAD 15-73699682-G-A, REVEL 0.03, CADD 13.30
- A16V (p.Ala16Val), ExAC rs754525593, gnomAD rs754525593, REVEL 0.06, CADD 16.10
- A16T (p.Ala16Thr), gnomAD 15-73699685-G-A, REVEL 0.03, CADD 0.12
- A17T (p.Ala17Thr), ExAC rs778534129, gnomAD rs778534129, REVEL 0.11, CADD 18.70
- A17V (p.Ala17Val), Ensembl rs1900302819, REVEL 0.17, CADD 5.55
- p.Ala17 Leu18del, rs1433529148, gnomAD 15-73699687-AGCCC, CADD 16.40
- L18P (p.Leu18Pro), gnomAD rs1683322181, REVEL 0.25, CADD 25.40
- G19E (p.Gly19Glu), gnomAD 15-73699692-TG-T, CADD 23.30
- G19A (p.Gly19Ala), gnomAD 15-73699695-G-C, REVEL 0.03, CADD 19.00
- G19G (p.Gly19Gly), rs752455322, gnomAD 15-73699696-A-G, CADD 9.35
- A20P (p.Ala20Pro), gnomAD rs1468931998, REVEL 0.06, CADD 10.20
- A20S (p.Ala20Ser), gnomAD 15-73699586-G-T, CADD 13.80
- A20E (p.Ala20Glu), gnomAD 15-73699587-C-A, CADD 8.87
- A20A (p.Ala20Ala), rs758002298, gnomAD 15-73699699-A-G, CADD 7.93
- L21L (p.Leu21Leu), gnomAD 15-73699700-C-T, CADD 10.40
- L21P (p.Leu21Pro), gnomAD 15-73699701-T-C, REVEL 0.27, CADD 25.00
- F23L (p.Phe23Leu), TOPMed rs1013184632, REVEL 0.04, CADD 18.70
- F23F (p.Phe23Phe), rs1203066266, gnomAD 15-73699600-C-T, CADD 8.50
- C24F (p.Cys24Phe), TOPMed rs1414351122, gnomAD rs1414351122, REVEL 0.09, CADD 22.00
- C24S (p.Cys24Ser), TOPMed rs921368722, gnomAD rs921368722, REVEL 0.10, CADD 22.40
- C24Y (p.Cys24Tyr), rs1293274615, gnomAD 15-73690772-G-A, CADD 1.91
- C24C (p.Cys24Cys), rs1390686574, gnomAD 15-73699621-T-C, CADD 13.60
- C24* (p.Cys24Ter), gnomAD 15-73699711-C-A, CADD 36.00
- L25F (p.Leu25Phe), gnomAD 15-73699712-C-T, REVEL 0.01, CADD 17.50
- L25V (p.Leu25Val), gnomAD 15-73699712-C-G, REVEL 0.03, CADD 12.30
- L25L (p.Leu25Leu), rs746815593, gnomAD 15-73699714-C-T, CADD 11.20
- T26A (p.Thr26Ala), Ensembl rs1360878390
- T26E (p.Thr26Glu), gnomAD 15-73699713-TCACA, CADD 33.00
- T26K (p.Thr26Lys), gnomAD 15-73699716-C-A, REVEL 0.06, CADD 22.60
- T26I (p.Thr26Ile), gnomAD 15-73699716-C-T, REVEL 0.06, CADD 27.50
- G27A (p.Gly27Ala), Ensembl rs1284432116
- G27R (p.Gly27Arg), TOPMed rs1900304438, gnomAD rs1900304438, REVEL 0.18, CADD 36.00
- G27W (p.Gly27Trp), rs201009986, gnomAD 15-73699607-G-T, CADD 1.89
- G27G (p.Gly27Gly), gnomAD 15-73699609-G-C, CADD 12.80
- G27V (p.Gly27Val), gnomAD 15-73702255-G-T, REVEL 0.23, CADD 33.00
- G27E (p.Gly27Glu), gnomAD 15-73702255-G-A, REVEL 0.23, CADD 26.20
- A28D (p.Ala28Asp), ExAC rs780114636, gnomAD rs780114636, REVEL 0.21, CADD 23.70
- A28S (p.Ala28Ser), rs769865072, ClinGen CA393095574, ClinVar RCV004271973, ExAC rs769865072, REVEL 0.15, CADD 23.30, Uncertain significance, not specified
- A28T (p.Ala28Thr), ExAC rs769865072, TOPMed rs769865072, gnomAD rs769865072, REVEL 0.16, CADD 23.80, Uncertain significance
- A28V (p.Ala28Val), gnomAD 15-73699596-C-T, CADD 14.30
- A28A (p.Ala28Ala), gnomAD 15-73702259-C-T, CADD 0.22
- L29R (p.Leu29Arg), rs1365553366, gnomAD 15-73702260-CT-C, CADD 24.50
- L29V (p.Leu29Val), gnomAD 15-73702260-C-G, REVEL 0.04, CADD 0.02
- L29L (p.Leu29Leu), gnomAD 15-73702260-C-T, CADD 0.58
- L29P (p.Leu29Pro), gnomAD 15-73702261-T-C, REVEL 0.27, CADD 23.30
- E30Q (p.Glu30Gln), ExAC rs749357618, TOPMed rs749357618, gnomAD rs749357618, REVEL 0.10, CADD 22.50
- E30* (p.Glu30Ter), gnomAD 15-73690774-G-T, CADD 7.80
- E30E (p.Glu30Glu), rs960162918, gnomAD 15-73690776-G-A, CADD 8.58
- E30D (p.Glu30Asp), gnomAD 15-73690776-G-T, CADD 9.54
- E30G (p.Glu30Gly), gnomAD 15-73702263-GA-G, CADD 25.40
- E30K (p.Glu30Lys), gnomAD 15-73702263-G-A, REVEL 0.18, CADD 20.20
- p.Glu30 Val31insGlyAsp, gnomAD 15-73702265-G-GGG, CADD 11.80
- V31F (p.Val31Phe), gnomAD rs766904389, REVEL 0.45, CADD 21.90, Uncertain significance
- V31I (p.Val31Ile), rs766904389, ClinGen CA272664020, ClinVar RCV004433379, gnomAD rs766904389, REVEL 0.10, CADD 9.08, Uncertain significance, not specified
- Q32H (p.Gln32His), rs1316005699, gnomAD 15-73690764-G-T, CADD 1.30
- Q32* (p.Gln32Ter), rs771883161, gnomAD 15-73690765-C-T, CADD 4.64
- Q32Q (p.Gln32Gln), rs1400247571, gnomAD 15-73690767-A-G, CADD 2.45
- Q32P (p.Gln32Pro), gnomAD 15-73699623-A-C, CADD 13.20
- Q32T (p.Gln32Thr), gnomAD 15-73702267-T-TGA, CADD 25.50
- Q32K (p.Gln32Lys), gnomAD 15-73702269-C-A, REVEL 0.14, CADD 14.40
- V33I (p.Val33Ile), gnomAD rs1441665542
- P34R (p.Pro34Arg), TOPMed rs1900423635
- P34S (p.Pro34Ser), rs1022188310, ClinGen CA272664021, ClinVar RCV004315165, TOPMed rs1022188310, REVEL 0.13, CADD 15.80, Uncertain significance, not specified
- P34H (p.Pro34His), gnomAD 15-73699614-C-A, CADD 13.70
- P34L (p.Pro34Leu), rs372744864, gnomAD 15-73699626-C-T, CADD 8.63
- P34P (p.Pro34Pro), rs138043841, gnomAD 15-73699627-G-A, CADD 14.20
- E35G (p.Glu35Gly), TOPMed rs1900423911, gnomAD rs1900423911, REVEL 0.20, CADD 23.90
- E35K (p.Glu35Lys), ExAC rs768902183, TOPMed rs768902183, REVEL 0.20, CADD 24.00
- E35E (p.Glu35Glu), rs1285020294, gnomAD 15-73702280-A-G, CADD 7.36
- D36A (p.Asp36Ala), Ensembl rs12902977
- D36V (p.Asp36Val), gnomAD 15-73702282-A-T, REVEL 0.29, CADD 22.00
- D36D (p.Asp36Asp), rs144769751, gnomAD 15-73702283-C-T, CADD 7.78
- P37L (p.Pro37Leu), gnomAD rs1289461498, REVEL 0.47, CADD 25.60
- P37S (p.Pro37Ser), gnomAD rs1243951843, REVEL 0.41, CADD 24.80
- P37T (p.Pro37Thr), gnomAD rs1243951843, REVEL 0.45, CADD 24.50
- P37A (p.Pro37Ala), gnomAD 15-73702284-C-G, REVEL 0.45, CADD 24.20
- P37R (p.Pro37Arg), gnomAD 15-73702285-C-G, REVEL 0.52, CADD 24.80
- P37P (p.Pro37Pro), gnomAD 15-73702286-A-T, CADD 2.69
- V38L (p.Val38Leu), ExAC rs774478067, TOPMed rs774478067, gnomAD rs774478067, REVEL 0.15, CADD 23.50
- V38M (p.Val38Met), ExAC rs774478067, TOPMed rs774478067, gnomAD rs774478067, REVEL 0.20, CADD 25.50
- V39M (p.Val39Met), gnomAD 15-73702290-G-A, REVEL 0.25, CADD 25.80
- V39L (p.Val39Leu), gnomAD 15-73702290-G-T, REVEL 0.20, CADD 25.20
- A40S (p.Ala40Ser), gnomAD rs1274807341
- A40T (p.Ala40Thr), gnomAD 15-73702293-G-A, REVEL 0.31, CADD 23.80
- A40V (p.Ala40Val), gnomAD 15-73702294-C-T, REVEL 0.12, CADD 23.20
- A40A (p.Ala40Ala), rs1435870876, gnomAD 15-73702295-A-C, CADD 9.66
- L41L (p.Leu41Leu), rs1180632581, gnomAD 15-73702298-G-A, CADD 4.96
- V42L (p.Val42Leu), TOPMed rs1243448980, gnomAD rs1243448980, REVEL 0.07, CADD 16.60
- V42M (p.Val42Met), gnomAD 15-73702299-G-A, REVEL 0.18, CADD 22.90
- V42A (p.Val42Ala), gnomAD 15-73702300-T-C, REVEL 0.08, CADD 20.40
- G43V (p.Gly43Val), gnomAD rs1353096579, REVEL 0.62, CADD 24.20
- G43D (p.Gly43Asp), gnomAD 15-73702303-G-A, REVEL 0.44, CADD 20.10
- G43G (p.Gly43Gly), gnomAD 15-73702304-C-A, CADD 6.05
- T44N (p.Thr44Asn), ExAC rs773583503, gnomAD rs773583503, REVEL 0.03, CADD 7.91
- T44T (p.Thr44Thr), rs761105640, gnomAD 15-73702307-C-T, CADD 0.92
- D45G (p.Asp45Gly), TOPMed rs1900426724, REVEL 0.45, CADD 24.50
- D45N (p.Asp45Asn), rs541095307, NCI-TCGA Cosmic COSV5920, cosmic curated COSV59203, ExAC rs541095307, REVEL 0.20, CADD 23.20, Variant assessed as somatic; moderate impact.
- A46T (p.Ala46Thr), gnomAD 15-73702311-G-A, REVEL 0.12, CADD 8.43
- A46A (p.Ala46Ala), gnomAD 15-73702313-C-T, CADD 8.72
- T47P (p.Thr47Pro), gnomAD 15-73702314-A-C, REVEL 0.22, CADD 23.50
- T47T (p.Thr47Thr), rs775020007, gnomAD 15-73702316-C-A, CADD 5.88
- L48M (p.Leu48Met), NCI-TCGA Cosmic COSV5920, cosmic curated COSV59204, Variant assessed as somatic; moderate impact.
- L48P (p.Leu48Pro), Ensembl rs1596012895, REVEL 0.43, CADD 25.80
- L48V (p.Leu48Val), gnomAD 15-73702316-CCT-C, CADD 24.90
- L48L (p.Leu48Leu), rs762416447, gnomAD 15-73702317-C-T, CADD 7.90
- C49R (p.Cys49Arg), ExAC rs763766438, TOPMed rs763766438, gnomAD rs763766438, REVEL 0.17, CADD 12.00, Likely benign, not specified
- C49Y (p.Cys49Tyr), 1000Genomes rs556248715, ExAC rs556248715, TOPMed rs556248715, gnomAD rs556248715, REVEL 0.10, CADD 14.30
- C49S (p.Cys49Ser), gnomAD 15-73702321-G-C, REVEL 0.12, CADD 9.05
- C50F (p.Cys50Phe), Ensembl rs2141564045
- C50G (p.Cys50Gly), gnomAD 15-73702323-T-G, REVEL 0.42, CADD 25.50
- C50Y (p.Cys50Tyr), gnomAD 15-73702324-G-A, REVEL 0.53, CADD 25.90
- S51C (p.Ser51Cys), ESP rs370507291, ExAC rs370507291, TOPMed rs370507291, gnomAD rs370507291, REVEL 0.33, CADD 24.60, Uncertain significance
- S51F (p.Ser51Phe), rs370507291, ClinGen CA7650183, cosmic curated COSV59205, ClinVar RCV004433372, REVEL 0.28, CADD 24.90, Uncertain significance, not specified
- S51P (p.Ser51Pro), 1000Genomes rs199799869, ESP rs199799869, ExAC rs199799869, TOPMed rs199799869, REVEL 0.25, CADD 23.40
- S51G (p.Ser51Gly), gnomAD 15-73699616-A-G, CADD 14.90
- S51R (p.Ser51Arg), rs747908389, gnomAD 15-73699616-A-C, CADD 14.90
- S51I (p.Ser51Ile), gnomAD 15-73699617-G-T, CADD 13.20
- S51S (p.Ser51Ser), rs11574473, gnomAD 15-73699618-C-T, CADD 13.60
- F52L (p.Phe52Leu), Ensembl rs1900428175
- F52S (p.Phe52Ser), ExAC rs756075404, gnomAD rs756075404, REVEL 0.22, CADD 25.90
- S53C (p.Ser53Cys), TOPMed rs1428756754, gnomAD rs1428756754, REVEL 0.26, CADD 17.80
- S53F (p.Ser53Phe), gnomAD 15-73702333-C-T, REVEL 0.13, CADD 17.80
- S53S (p.Ser53Ser), gnomAD 15-73702334-C-G, CADD 0.64
- P54A (p.Pro54Ala), TOPMed rs1435172384, gnomAD rs1435172384, REVEL 0.07, CADD 8.55
- P54S (p.Pro54Ser), cosmic curated COSV59205, TOPMed rs1435172384, gnomAD rs1435172384, REVEL 0.04, CADD 7.22
- P54R (p.Pro54Arg), rs770961285, gnomAD 15-73702335-CCT-C, CADD 22.10
Public CD276 analysis runs
- CD276 analysis run — CD276 (913 variants) — completed 2026-08-21