IFNGR1 (Interferon gamma receptor 1) variants and mutations

IFNGR1 (also known as Interferon gamma receptor 1) is a human protein-coding gene encoding an interferon gamma receptor 1 protein. It binds interferon-gamma and initiates STAT1-dependent antimicrobial and immune-activating programs. Complete or partial loss-of-function variants cause Mendelian susceptibility to mycobacterial disease with severity related to residual signaling. This analysis covers 1,018 IFNGR1 variants and mutations. Of these, 70% have computational variant effect predictions. Disease context includes disseminated atypical mycobacterial infection, chronic granulomatous disease, and idiopathic pulmonary fibrosis. Example IFNGR1 variants include M1K, M1V, and A2D.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, MaveDB, LitVar.

Notable IFNGR1 variants

Examples include M1K, M1V, A2D, A2G, A2T, A2V, L3F, L3V. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.