MAOB (P27338) variants and mutations
MAOB (also known as P27338) is a human protein-coding gene encoding an amine oxidase [flavin-containing] B protein. It oxidatively degrades dopamine and several trace amines, particularly in brain glial cells and other tissues. Pharmacologic inhibition increases brain dopamine availability and is used in Parkinson disease, while inherited severe deficiency is rare. This analysis covers 555 MAOB variants and mutations. Of these, 94% have computational variant effect predictions. Disease context includes Parkinson disease, major depressive disorder, and depressive disorder. Example MAOB variants include S2I, S2N, and K4I.
Variant analysis overview
- Gene: MAOB
- Protein: P27338
- UniProt accession: P27338
- Organism: Homo sapiens
- Variants analyzed: 555
- Variant scope: all variants
- Completed: 2026-08-19
Variant and mutation evidence
- Variant composition: 394 unspecified-consequence records; 1 stop retained variant; 74 missense variants; 65 synonymous variants; 7 frameshift variants; 2 in-frame deletions; 6 stop-gained variants; 4 splice-region variants; 2 substitution
- Prediction scores: 521 variants have prediction scores (94% of the analyzed set).
Clinical, disease, and population context
- Disease context: 25 disease associations are represented. Top associations: Parkinson disease, major depressive disorder, depressive disorder, hypertensive disorder, Hypertension, melancholia, neurodegenerative disease, cocaine dependence, neuropathic pain, Borderline personality disorder, progressive supranuclear palsy, internet addiction disorder.
Protein structure and variant hotspots
- Protein features: 1 transmembrane segments; 3 post-translational modification sites.
- Structural context: 43 variants have structural context.
- PTM context: 4 variants overlap post-translational modification sites.
Data sources
Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, MaveDB, LitVar.
Notable MAOB variants
Examples include S2I, S2N, K4I, D6E, G13D, G16=, M17T, A18V. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.
- S2I (p.Ser2Ile), NCI-TCGA TCGA novel, MetaLR 0.02, MetaSVM -1.03, Variant assessed as somatic; moderate impact.
- S2N (p.Ser2Asn), ExAC rs778172877, gnomAD rs778172877, REVEL 0.02, MetaLR 0.02
- K4I (p.Lys4Ile), Ensembl rs2035478417, MetaLR 0.02, MetaSVM -1.01
- D6E (p.Asp6Glu), gnomAD rs1217654270, REVEL 0.23, MetaLR 0.03
- G13D (p.Gly13Asp), Ensembl rs867906703, MetaLR 0.81, MetaSVM 0.85
- G16=, NCI-TCGA Cosmic COSV1009, Variant assessed as somatic; low impact.
- M17T (p.Met17Thr), gnomAD rs1332503515, REVEL 0.66, MetaLR 0.58
- A18V (p.Ala18Val), ExAC rs762962154, gnomAD rs762962154, REVEL 0.53, MetaLR 0.74
- A19G (p.Ala19Gly), ExAC rs773282941, gnomAD rs773282941, REVEL 0.57, MetaLR 0.29
- L22P (p.Leu22Pro), ExAC rs770202748, Uncertain significance, not specified
- L22R (p.Leu22Arg), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- L28R (p.Leu28Arg), NCI-TCGA Cosmic COSV1009, Variant assessed as somatic; moderate impact.
- N29D (p.Asn29Asp), TOPMed rs1028364289, REVEL 0.27, MetaLR 0.47
- V30A (p.Val30Ala), NCI-TCGA TCGA novel, REVEL 0.90, MetaLR 0.95, Variant assessed as somatic; moderate impact.
- V31I (p.Val31Ile), rs189979184, ClinGen CA10391365, ClinVar RCV004226697, 1000Genomes rs189979184, REVEL 0.05, MetaLR 0.02, Uncertain significance, not specified
- V32I (p.Val32Ile), ExAC rs747346258
- E34* (p.Glu34Ter), NCI-TCGA TCGA novel, Variant assessed as somatic; high impact.
- A35T (p.Ala35Thr), Ensembl rs2035168018
- R36Q (p.Arg36Gln), ExAC rs756887426, TOPMed rs756887426, gnomAD rs756887426, REVEL 0.65, MetaLR 0.85
- R36W (p.Arg36Trp), rs778570953, ExAC rs778570953, TOPMed rs778570953, gnomAD rs778570953, REVEL 0.86, MetaLR 0.93, Uncertain significance, not specified
- D37E (p.Asp37Glu), TOPMed rs1171549806, gnomAD rs1171549806, REVEL 0.54, MetaLR 0.84
- R38C (p.Arg38Cys), ExAC rs778871584, TOPMed rs778871584, gnomAD rs778871584, REVEL 0.91, MetaLR 0.94
- R38H (p.Arg38His), ExAC rs17856663, TOPMed rs17856663, gnomAD rs17856663, REVEL 0.89, MetaLR 0.95
- G40R (p.Gly40Arg), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- G41S (p.Gly41Ser), rs2519259197, ClinGen CA413010637, ClinVar RCV004351700, REVEL 0.92, MetaLR 0.80, Uncertain significance, not specified
- N48D (p.Asn48Asp), ExAC rs747397495, gnomAD rs747397495, REVEL 0.53, MetaLR 0.65
- Q49E (p.Gln49Glu), ExAC rs775868592, gnomAD rs775868592, REVEL 0.05, MetaLR 0.01
- K50N (p.Lys50Asn), TOPMed rs2035101907, gnomAD rs2035101907, REVEL 0.04, MetaLR 0.01, Uncertain significance, not specified
- K50T (p.Lys50Thr), Ensembl rs1712107050, MetaLR 0.01, MetaSVM -0.93
- D55V (p.Asp55Val), NCI-TCGA Cosmic COSV1009, MetaLR 0.22, MetaSVM -0.41, Variant assessed as somatic; moderate impact.
- G58R (p.Gly58Arg), NCI-TCGA TCGA novel, NCI-TCGA Cosmic COSV1009, REVEL 0.97, MetaLR 0.92, Variant assessed as somatic; high impact.
- S59A (p.Ser59Ala), rs201981141, ClinGen CA10391338, ClinVar RCV004082148, ESP rs201981141, REVEL 0.26, MetaLR 0.37, Uncertain significance, not specified
- Y60C (p.Tyr60Cys), ESP rs370820554, TOPMed rs370820554, gnomAD rs370820554, REVEL 0.94, MetaLR 0.89
- V61L (p.Val61Leu), NCI-TCGA Cosmic COSV1009, NCI-TCGA Cosmic COSV6520, Variant assessed as somatic; moderate impact.
- P63S (p.Pro63Ser), TOPMed rs1298437740, gnomAD rs1298437740, REVEL 0.80, MetaLR 0.87
- Q65R (p.Gln65Arg), TOPMed rs2035101570, gnomAD rs2035101570, REVEL 0.50, MetaLR 0.15
- R67C (p.Arg67Cys), rs777268698, NCI-TCGA Cosmic COSV1009, NCI-TCGA Cosmic COSV6520, ExAC rs777268698, REVEL 0.58, MetaLR 0.82, Variant assessed as somatic; moderate impact.
- R67H (p.Arg67His), rs755689863, NCI-TCGA Cosmic COSV6520, ExAC rs755689863, TOPMed rs755689863, REVEL 0.39, MetaLR 0.68, Variant assessed as somatic; moderate impact.
- R67S (p.Arg67Ser), ExAC rs777268698, TOPMed rs777268698, gnomAD rs777268698, REVEL 0.77, MetaLR 0.88
- I68V (p.Ile68Val), Ensembl rs2035101370, REVEL 0.32, MetaLR 0.59
- L69F (p.Leu69Phe), NCI-TCGA Cosmic COSV6520, Uncertain significance, not specified
- L69W (p.Leu69Trp), Ensembl rs2035101263, REVEL 0.90, MetaLR 0.90
- A72D (p.Ala72Asp), NCI-TCGA Cosmic COSV6520, Variant assessed as somatic; moderate impact.
- A72T (p.Ala72Thr), ESP rs148575315, TOPMed rs148575315
- E74D (p.Glu74Asp), rs2035101147, ClinGen CA413009991, ClinVar RCV004416014, TOPMed rs2035101147, REVEL 0.14, MetaLR 0.03, Uncertain significance, not specified
- G76R (p.Gly76Arg), Ensembl rs2035101065, REVEL 0.58, MetaLR 0.22
- Y80C (p.Tyr80Cys), gnomAD rs1280271793, REVEL 0.87, MetaLR 0.87
- E84D (p.Glu84Asp), ExAC rs781299154, TOPMed rs781299154, gnomAD rs781299154, REVEL 0.36, MetaLR 0.44
- E86K (p.Glu86Lys), NCI-TCGA Cosmic COSV6520, TOPMed rs2035100724, Variant assessed as somatic; moderate impact.
- R87C (p.Arg87Cys), rs776880004, NCI-TCGA Cosmic COSV1009, 1000Genomes rs776880004, TOPMed rs776880004, REVEL 0.29, MetaLR 0.61, Variant assessed as somatic; moderate impact.
- R87G (p.Arg87Gly), 1000Genomes rs776880004, TOPMed rs776880004, gnomAD rs776880004, REVEL 0.40, MetaLR 0.70
- R87H (p.Arg87His), 1000Genomes rs192154106, ExAC rs192154106, TOPMed rs192154106, gnomAD rs192154106, REVEL 0.32, MetaLR 0.61
- H90Y (p.His90Tyr), NCI-TCGA Cosmic COSV6520, Variant assessed as somatic; moderate impact.
- H91D (p.His91Asp), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- H91Y (p.His91Tyr), Ensembl rs2035100429
- K93N (p.Lys93Asn), NCI-TCGA Cosmic COSV6520, REVEL 0.07, MetaLR 0.02, Variant assessed as somatic; moderate impact.
- G94=, NCI-TCGA TCGA novel, Variant assessed as somatic; low impact.
- G94D (p.Gly94Asp), rs1423670702, NCI-TCGA Cosmic COSV6520, gnomAD rs1423670702, REVEL 0.32, MetaLR 0.13, Variant assessed as somatic; moderate impact.
- S96L (p.Ser96Leu), NCI-TCGA Cosmic COSV1009, MetaLR 0.59, MetaSVM -0.17, Variant assessed as somatic; moderate impact.
- Y97H (p.Tyr97His), TOPMed rs1215586148, gnomAD rs1215586148, REVEL 0.31, MetaLR 0.56
- P98L (p.Pro98Leu), NCI-TCGA TCGA novel, MetaLR 0.02, MetaSVM -0.99, Variant assessed as somatic; moderate impact.
- P98S (p.Pro98Ser), rs1426305009, NCI-TCGA Cosmic COSV1009, gnomAD rs1426305009, REVEL 0.08, MetaLR 0.02, Variant assessed as somatic; moderate impact.
- R100S (p.Arg100Ser), ExAC rs767870404, gnomAD rs767870404, NCI-TCGA TCGA novel, REVEL 0.24, MetaLR 0.42, Uncertain significance, not specified
- G101R (p.Gly101Arg), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- G101V (p.Gly101Val), TOPMed rs2034621596, MetaLR 0.90, MetaSVM 0.90
- F103S (p.Phe103Ser), TOPMed rs1601986947, MetaLR 0.07, MetaSVM -1.03, Uncertain significance, not specified
- P104S (p.Pro104Ser), gnomAD rs1489790682, REVEL 0.77, MetaLR 0.78
- P104T (p.Pro104Thr), gnomAD rs1489790682, REVEL 0.78, MetaLR 0.89
- V106A (p.Val106Ala), TOPMed rs1393975465, REVEL 0.20, MetaLR 0.48
- V106I (p.Val106Ile), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- W107* (p.Trp107Ter), NCI-TCGA Cosmic COSV6520, Variant assessed as somatic; high impact.
- W107C (p.Trp107Cys), rs769571980, ClinGen CA10391301, ClinVar RCV004416015, ExAC rs769571980, REVEL 0.74, MetaLR 0.78, Uncertain significance, not specified
- W107R (p.Trp107Arg), ExAC rs774521579, TOPMed rs774521579, gnomAD rs774521579, REVEL 0.56, MetaLR 0.64
- P109L (p.Pro109Leu), 1000Genomes rs149395667, ESP rs149395667, ExAC rs149395667, TOPMed rs149395667, REVEL 0.84, MetaLR 0.82
- I110V (p.Ile110Val), TOPMed rs1307131428, gnomAD rs1307131428, REVEL 0.29, MetaLR 0.55
- T111A (p.Thr111Ala), Ensembl rs952603149, REVEL 0.21, MetaLR 0.26
- T111N (p.Thr111Asn), gnomAD rs1294657930, MetaLR 0.51, MetaSVM -0.53
- Y112C (p.Tyr112Cys), gnomAD rs1219565046, REVEL 0.11, MetaLR 0.06
- Y112N (p.Tyr112Asn), TOPMed rs2034620392
- H115R (p.His115Arg), ExAC rs776406971, TOPMed rs776406971, gnomAD rs776406971, REVEL 0.06, MetaLR 0.02, Uncertain significance, not specified
- N116K (p.Asn116Lys), gnomAD rs1440009738, REVEL 0.68, MetaLR 0.83
- N117T (p.Asn117Thr), NCI-TCGA Cosmic COSV6520, MetaLR 0.06, MetaSVM -1.07, Variant assessed as somatic; moderate impact.
- F118Y (p.Phe118Tyr), Ensembl rs994140054, MetaLR 0.04, MetaSVM -1.10
- W119* (p.Trp119Ter), NCI-TCGA Cosmic COSV6520, Variant assessed as somatic; high impact.
- W119R (p.Trp119Arg), Ensembl rs2034619895, MetaLR 0.78, MetaSVM 0.47
- R120K (p.Arg120Lys), ExAC rs768327519, gnomAD rs768327519, REVEL 0.67, MetaLR 0.75
- M122I (p.Met122Ile), TOPMed rs2034619742, REVEL 0.26, MetaLR 0.46
- M122V (p.Met122Val), TOPMed rs2034619785, REVEL 0.29, MetaLR 0.61
- D123Y (p.Asp123Tyr), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- D124A (p.Asp124Ala), ExAC rs780074639, TOPMed rs780074639, gnomAD rs780074639, REVEL 0.27, MetaLR 0.46, Uncertain significance, not specified
- D124G (p.Asp124Gly), ExAC rs780074639, TOPMed rs780074639, gnomAD rs780074639, REVEL 0.30, MetaLR 0.55
- R127L (p.Arg127Leu), ESP rs372591640, ExAC rs372591640, TOPMed rs372591640, gnomAD rs372591640, REVEL 0.05, MetaLR 0.03
- R127Q (p.Arg127Gln), ESP rs372591640, ExAC rs372591640, TOPMed rs372591640, gnomAD rs372591640, REVEL 0.07, MetaLR 0.02
- P130L (p.Pro130Leu), rs17852046, TOPMed rs17852046, gnomAD rs17852046, REVEL 0.48, MetaLR 0.12, Variant assessed as somatic; moderate impact.
- P130Q (p.Pro130Gln), TOPMed rs17852046, gnomAD rs17852046, REVEL 0.49, MetaLR 0.15
- S131R (p.Ser131Arg), rs766904222, ClinGen CA10391283, ClinVar RCV004416016, ExAC rs766904222, AlphaMissense 0.18, MetaLR 0.54, Uncertain significance, not specified
- A133T (p.Ala133Thr), ExAC rs763385013, TOPMed rs763385013, gnomAD rs763385013, REVEL 0.77, MetaLR 0.79
- A133D (p.Ala133Asp), rs780074639, []
- W135* (p.Trp135Ter), NCI-TCGA Cosmic COSV1009, CADD 39.00, Variant assessed as somatic; high impact.
- P138R (p.Pro138Arg), TOPMed rs2034603615, REVEL 0.88, MetaLR 0.83
- P138S (p.Pro138Ser), gnomAD rs1440909955, REVEL 0.87, MetaLR 0.89
- L139F (p.Leu139Phe), Ensembl rs944307703
- A140T (p.Ala140Thr), Ensembl rs890050856, REVEL 0.83, MetaLR 0.91
- A140V (p.Ala140Val), TOPMed rs1378086580, REVEL 0.85, MetaLR 0.90
- E141K (p.Glu141Lys), NCI-TCGA Cosmic COSV1009, Variant assessed as somatic; moderate impact.
- E142K (p.Glu142Lys), ESP rs147281288, ExAC rs147281288, TOPMed rs147281288, gnomAD rs147281288, REVEL 0.33, MetaLR 0.65
- W143* (p.Trp143Ter), NCI-TCGA Cosmic COSV6520, CADD 36.00, Variant assessed as somatic; high impact.
- N145D (p.Asn145Asp), rs2519220513, ClinGen CA413007977, ClinVar RCV004416017, Uncertain significance, not specified
- N145K (p.Asn145Lys), NCI-TCGA Cosmic COSV1009, MetaLR 0.47, MetaSVM -0.51, Variant assessed as somatic; moderate impact.
- M148V (p.Met148Val), gnomAD rs1179798721, REVEL 0.28, MetaLR 0.01
- E150K (p.Glu150Lys), gnomAD rs1418610469
- D153E (p.Asp153Glu), rs2519220465, ClinGen CA413007775, ClinVar RCV004312225, Uncertain significance, not specified
- D153N (p.Asp153Asn), Ensembl rs2034602930, MetaLR 0.02, MetaSVM -1.02
- K154N (p.Lys154Asn), ExAC rs774808110, TOPMed rs774808110, gnomAD rs774808110, REVEL 0.13, MetaLR 0.03
- L155F (p.Leu155Phe), rs201889071, ClinGen CA10391277, ClinVar RCV004291306, 1000Genomes rs201889071, REVEL 0.22, MetaLR 0.49, Uncertain significance, not specified
- E159D (p.Glu159Asp), ExAC rs766994984, TOPMed rs766994984, gnomAD rs766994984, REVEL 0.18, MetaLR 0.50
- E159K (p.Glu159Lys), ExAC rs745859820, gnomAD rs745859820, REVEL 0.24, MetaLR 0.33
- S160C (p.Ser160Cys), rs371973652, NCI-TCGA Cosmic COSV1009, TOPMed rs371973652, gnomAD rs371973652, REVEL 0.43, MetaLR 0.73, Variant assessed as somatic; moderate impact.
- S160Y (p.Ser160Tyr), TOPMed rs371973652, gnomAD rs371973652, REVEL 0.43, MetaLR 0.66
- A161S (p.Ala161Ser), rs143909840, ClinGen CA10391258, ClinVar RCV004231426, ClinVar RCV004696262, REVEL 0.34, MetaLR 0.74, Uncertain significance, not provided; not specified
- Q163K (p.Gln163Lys), TOPMed rs1269258923, REVEL 0.22, MetaLR 0.36
- Q163R (p.Gln163Arg), TOPMed rs2034540260, gnomAD rs2034540260, REVEL 0.20, MetaLR 0.34
- T166A (p.Thr166Ala), ESP rs138342360, ExAC rs138342360, TOPMed rs138342360, gnomAD rs138342360, REVEL 0.34, MetaLR 0.58, Uncertain significance, not specified
- L167V (p.Leu167Val), TOPMed rs1316591298, gnomAD rs1316591298, REVEL 0.43, MetaLR 0.61, Uncertain significance, not specified
- F168L (p.Phe168Leu), NCI-TCGA Cosmic COSV6520, REVEL 0.75, MetaLR 0.63, Variant assessed as somatic; moderate impact.
- N170K (p.Asn170Lys), NCI-TCGA Cosmic COSV6520, MetaLR 0.79, MetaSVM 0.53, Variant assessed as somatic; moderate impact.
- V173A (p.Val173Ala), Ensembl rs1159861627
- V173I (p.Val173Ile), TOPMed rs2034539828, SIFT 1.00
- T174I (p.Thr174Ile), NCI-TCGA TCGA novel, MetaLR 0.11, MetaSVM -0.93, Variant assessed as somatic; moderate impact.
- T174N (p.Thr174Asn), TOPMed rs1459914959, gnomAD rs1459914959, REVEL 0.29, MetaLR 0.11
- A175E (p.Ala175Glu), Ensembl rs2034539678
- E176K (p.Glu176Lys), NCI-TCGA TCGA novel, SIFT 0.00, Variant assessed as somatic; moderate impact.
- A182V (p.Ala182Val), rs748373348, ExAC rs748373348, TOPMed rs748373348, gnomAD rs748373348, REVEL 0.70, MetaLR 0.71, Variant assessed as somatic; moderate impact.
- L186M (p.Leu186Met), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- Y188F (p.Tyr188Phe), Ensembl rs1555959206, REVEL 0.79, MetaLR 0.86
- Q191E (p.Gln191Glu), TOPMed rs1428823353, gnomAD rs1428823353, REVEL 0.24, MetaLR 0.07
- T195I (p.Thr195Ile), NCI-TCGA TCGA novel, MetaLR 0.71, MetaSVM 0.17, Variant assessed as somatic; moderate impact.
- T196A (p.Thr196Ala), TOPMed rs988819611, gnomAD rs988819611, REVEL 0.20, MetaLR 0.47, Uncertain significance, not specified
- T196R (p.Thr196Arg), rs781450685, ClinGen CA10391252, ClinVar RCV004416018, ExAC rs781450685, REVEL 0.30, MetaLR 0.55, Uncertain significance, not specified
- R197K (p.Arg197Lys), Ensembl rs2034539060
- R197S (p.Arg197Ser), Ensembl rs12845783, REVEL 0.68, MetaLR 0.78
- R197T (p.Arg197Thr), NCI-TCGA TCGA novel, MetaLR 0.85, MetaSVM 0.73, Variant assessed as somatic; moderate impact.
- S200* (p.Ser200Ter), 1000Genomes rs12850496, ExAC rs12850496, TOPMed rs12850496, gnomAD rs12850496
- S200L (p.Ser200Leu), rs12850496, NCI-TCGA Cosmic COSV6520, 1000Genomes rs12850496, ExAC rs12850496, REVEL 0.82, MetaLR 0.85, Variant assessed as somatic; moderate impact.
- S200P (p.Ser200Pro), ExAC rs768655609, gnomAD rs768655609, REVEL 0.82, MetaLR 0.85
- T201A (p.Thr201Ala), gnomAD rs12845773, REVEL 0.65, MetaLR 0.72
- T201P (p.Thr201Pro), gnomAD rs12845773
- T202A (p.Thr202Ala), NCI-TCGA Cosmic COSV1009, Variant assessed as somatic; moderate impact.
- N203K (p.Asn203Lys), NCI-TCGA Cosmic COSV1009, MetaLR 0.78, MetaSVM 0.46, Variant assessed as somatic; moderate impact.
- N203S (p.Asn203Ser), ESP rs375609221, ExAC rs375609221, TOPMed rs375609221, gnomAD rs375609221, REVEL 0.42, MetaLR 0.79
- G204E (p.Gly204Glu), NCI-TCGA Cosmic COSV6520, Variant assessed as somatic; moderate impact.
- G204V (p.Gly204Val), NCI-TCGA Cosmic COSV6520, MetaLR 0.93, MetaSVM 1.08, Variant assessed as somatic; moderate impact.
- Q206* (p.Gln206Ter), NCI-TCGA Cosmic COSV6520, TOPMed rs2034538269, CADD 39.00, Variant assessed as somatic; high impact.
- Q206H (p.Gln206His), NCI-TCGA Cosmic COSV1009, Variant assessed as somatic; moderate impact.
- K209T (p.Lys209Thr), ExAC rs754192677, gnomAD rs754192677, MetaLR 0.11, MetaSVM -0.90
- F210L (p.Phe210Leu), Ensembl rs2147134418, MetaLR 0.03, MetaSVM -1.09
- V211A (p.Val211Ala), ESP rs148264689, TOPMed rs148264689, gnomAD rs148264689, REVEL 0.32, MetaLR 0.70
- G212D (p.Gly212Asp), ExAC rs780719254, gnomAD rs780719254, REVEL 0.94, MetaLR 0.94
- G212V (p.Gly212Val), NCI-TCGA TCGA novel, MetaLR 0.95, MetaSVM 1.10, Variant assessed as somatic; moderate impact.
- G213R (p.Gly213Arg), NCI-TCGA Cosmic COSV6520, REVEL 0.66, MetaLR 0.29, Variant assessed as somatic; moderate impact.
- V217M (p.Val217Met), ExAC rs765931652, TOPMed rs765931652, gnomAD rs765931652, REVEL 0.18, MetaLR 0.06
- S218T (p.Ser218Thr), 1000Genomes rs746209846, ExAC rs746209846, gnomAD rs746209846, REVEL 0.19, MetaLR 0.06
- E219K (p.Glu219Lys), ExAC rs750363747, gnomAD rs750363747, REVEL 0.29, MetaLR 0.04
- R220L (p.Arg220Leu), NCI-TCGA Cosmic COSV1009, MetaLR 0.64, MetaSVM -0.22, Variant assessed as somatic; moderate impact.
- R220Q (p.Arg220Gln), rs980435225, NCI-TCGA Cosmic COSV1009, TOPMed rs980435225, REVEL 0.34, MetaLR 0.61, Uncertain significance, not specified
- R220W (p.Arg220Trp), rs1470898078, NCI-TCGA Cosmic COSV6520, TOPMed rs1470898078, gnomAD rs1470898078, REVEL 0.54, MetaLR 0.85, Variant assessed as somatic; moderate impact.
- I221M (p.Ile221Met), ExAC rs761533542, gnomAD rs761533542, REVEL 0.10, MetaLR 0.01
- I221T (p.Ile221Thr), NCI-TCGA TCGA novel, MetaLR 0.10, MetaSVM -0.99, Variant assessed as somatic; moderate impact.
- L224I (p.Leu224Ile), NCI-TCGA Cosmic COSV6520, Variant assessed as somatic; moderate impact.
- L224P (p.Leu224Pro), NCI-TCGA Cosmic COSV6520, Variant assessed as somatic; moderate impact.
- G226* (p.Gly226Ter), Ensembl rs866352942
- G226E (p.Gly226Glu), NCI-TCGA TCGA novel, gnomAD rs2034520856, REVEL 0.21, MetaLR 0.09, Variant assessed as somatic; moderate impact.
- D227G (p.Asp227Gly), TOPMed rs2034520809, gnomAD rs2034520809, REVEL 0.32, MetaLR 0.50
- R228* (p.Arg228Ter), ExAC rs776431835
- R228Q (p.Arg228Gln), 1000Genomes rs143144504, ESP rs143144504, ExAC rs143144504, TOPMed rs143144504, REVEL 0.19, MetaLR 0.03
- R233K (p.Arg233Lys), Ensembl rs2034520553, REVEL 0.23, MetaLR 0.51
- R233S (p.Arg233Ser), TOPMed rs2034520491, REVEL 0.29, MetaLR 0.32
- P234L (p.Pro234Leu), Ensembl rs2147134344, REVEL 0.89, MetaLR 0.93
- P234S (p.Pro234Ser), Ensembl rs2034520438, REVEL 0.71, MetaLR 0.91
- V235A (p.Val235Ala), NCI-TCGA Cosmic COSV1009, MetaLR 0.96, MetaSVM 1.10, Variant assessed as somatic; moderate impact.
Public MAOB analysis runs
- MAOB analysis run — MAOB (555 variants) — completed 2026-08-19