BCL11B (B-cell lymphoma/leukemia 11B) variants and mutations

BCL11B (also known as B-cell lymphoma/leukemia 11B) is a human protein-coding gene encoding a b-cell lymphoma/leukemia 11B protein. It regulates transcriptional programs required for T-cell development, craniofacial development, and nervous-system maturation. Heterozygous pathogenic variants can cause a syndromic neurodevelopmental disorder with immunologic abnormalities and variable craniofacial features. This analysis covers 1,664 BCL11B variants and mutations. Of these, 84% have computational variant effect predictions. Disease context includes intellectual developmental disorder with speech delay, dysmorphic facies, and t, immunodeficiency 49, and hereditary disease. Example BCL11B variants include R4H, K5Q, and N8K.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, AlphaFold DB, gnomAD constraint, Open Targets, MaveDB, LitVar.

Notable BCL11B variants

Examples include R4H, K5Q, N8K, P9L, Q10R, Q14*, Q14R, R15M. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.