SOS1 (Son of sevenless homolog 1) variants and mutations

SOS1 (also known as Son of sevenless homolog 1) is a human protein-coding gene encoding a son of sevenless homolog 1 protein. It activates RAS by exchanging GDP for GTP downstream of receptor tyrosine kinases. Germline activating variants are a common cause of Noonan syndrome, while excessive SOS1-RAS signaling can contribute to cancer. This analysis covers 2,058 SOS1 variants and mutations. Of these, 70% have computational variant effect predictions. Disease context includes Noonan syndrome, hereditary gingival fibromatosis, and RASopathy. Example SOS1 variants include Q2*, Q2E, and Q2H.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, ClinGen, MaveDB, LitVar.

Notable SOS1 variants

Examples include Q2*, Q2E, Q2H, Q2K, Q2L, Q2P, A3S, A3V. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.