HCN4 (Q9Y3Q4) variants and mutations

HCN4 (also known as Q9Y3Q4) is a human protein-coding gene encoding a potassium/sodium hyperpolarization-activated cyclic nucleotide-gated channel 4 protein. Its hyperpolarization-activated current contributes substantially to spontaneous diastolic depolarization in sinoatrial-node pacemaker cells. Pathogenic variants can cause sinus bradycardia, conduction abnormalities, and in some families left-ventricular noncompaction. This analysis covers 2,147 HCN4 variants and mutations. Of these, 84% have computational variant effect predictions. Disease context includes sick sinus syndrome 2, autosomal dominant, atrial fibrillation, and heart failure. Example HCN4 variants include M1V, D2E, and D2V.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, ClinGen, MaveDB, LitVar.

Notable HCN4 variants

Examples include M1V, D2E, D2V, D2Y, K3M, K3N, K3R, K3T. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.