ABCA1 (O95477) variants and mutations
ABCA1 (also known as O95477) is a human protein-coding gene encoding a phospholipid-transporting ATPase protein. It transfers cellular cholesterol and phospholipids to lipid-poor apolipoproteins, especially ApoA-I, initiating HDL formation and reverse cholesterol transport. Severe loss of function causes Tangier disease, while partial impairment can markedly lower HDL cholesterol. This analysis covers 2,727 ABCA1 variants and mutations. Of these, 90% have computational variant effect predictions. Disease context includes Tangier disease, hypoalphalipoproteinemia, primary, 1, and Decreased HDL cholesterol concentration. Example ABCA1 variants include A2T, A2V, and C3F.
Variant analysis overview
- Gene: ABCA1
- Protein: O95477
- UniProt accession: O95477
- Organism: Homo sapiens
- Variants analyzed: 2727
- Variant scope: all variants
- Completed: 2026-08-19
Variant and mutation evidence
- Variant composition: 2,465 unspecified-consequence records; 106 synonymous variants; 120 missense variants; 19 frameshift variants; 5 stop-gained variants; 1 in-frame insertions; 6 splice-region variants; 2 in-frame deletions; 3 substitution
- Prediction scores: 2,443 variants have prediction scores (90% of the analyzed set).
Clinical, disease, and population context
- Disease context: 25 disease associations are represented. Top associations: Tangier disease, hypoalphalipoproteinemia, primary, 1, Decreased HDL cholesterol concentration, metabolic syndrome, Hypercholesterolemia, metabolic disease, open-angle glaucoma, glaucoma, coronary artery disorder, alcohol drinking, hyperlipidemia, Abnormality of the cardiovascular system.
Protein structure and variant hotspots
- Protein features: 15 transmembrane segments; 2 domains; 2 binding sites; 24 post-translational modification sites.
- Structural context: 872 variants have structural context.
- PTM context: 28 variants overlap post-translational modification sites.
Data sources
Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, MaveDB, LitVar.
Notable ABCA1 variants
Examples include A2T, A2V, C3F, C3S, C3Y, W4C, P5H, Q6*. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.
- A2T (p.Ala2Thr), TOPMed rs1212858633, REVEL 0.42, CADD 22.40
- A2V (p.Ala2Val), TOPMed rs1840851606, REVEL 0.53, CADD 24.20
- C3F (p.Cys3Phe), rs149491765, ClinGen CA5169519, ClinVar RCV004304559, ESP rs149491765, REVEL 0.23, CADD 3.71, Uncertain significance, Cardiovascular phenotype
- C3S (p.Cys3Ser), ESP rs149491765, ExAC rs149491765, TOPMed rs149491765, gnomAD rs149491765, REVEL 0.10, CADD 8.67, Uncertain significance
- C3Y (p.Cys3Tyr), cosmic curated COSV10531, ESP rs149491765, ExAC rs149491765, TOPMed rs149491765, REVEL 0.18, CADD 8.76, Uncertain significance, Cardiovascular phenotype
- W4C (p.Trp4Cys), TOPMed rs1221387381, gnomAD rs1221387381, REVEL 0.45, CADD 22.90
- P5H (p.Pro5His), TOPMed rs1326879009, gnomAD rs1326879009, REVEL 0.32, CADD 24.00
- Q6* (p.Gln6Ter), rs1840850607, ClinGen CA374319069, ClinVar RCV001951210, TOPMed rs1840850607, CADD 40.00, Pathogenic
- Q6H (p.Gln6His), TOPMed rs1226778696, gnomAD rs1226778696, REVEL 0.75, CADD 24.60
- Q6P (p.Gln6Pro), rs2538409288, ClinGen CA374319067, ClinVar RCV002407862, Uncertain significance, Cardiovascular phenotype
- L7V (p.Leu7Val), TOPMed rs1840850202, REVEL 0.18, CADD 10.00
- R8K (p.Arg8Lys), ExAC rs748989873, gnomAD rs748989873, SIFT 1.00
- R8M (p.Arg8Met), ExAC rs748989873, gnomAD rs748989873, REVEL 0.08, CADD 20.90
- L9F (p.Leu9Phe), gnomAD rs1232298897, REVEL 0.64, CADD 23.40
- L11P (p.Leu11Pro), ExAC rs777372679, gnomAD rs777372679, REVEL 0.90, CADD 28.80
- N14K (p.Asn14Lys), Ensembl rs2118433191, SIFT 0.00
- L15F (p.Leu15Phe), gnomAD rs1394248066, REVEL 0.29, CADD 12.10
- T16S (p.Thr16Ser), gnomAD rs1466089023, REVEL 0.63, CADD 25.90
- F17C (p.Phe17Cys), gnomAD rs1171398601, REVEL 0.49, CADD 24.00
- F17Y (p.Phe17Tyr), gnomAD rs1171398601, REVEL 0.30, CADD 18.90
- R19I (p.Arg19Ile), NCI-TCGA TCGA novel, REVEL 0.59, CADD 25.20, Variant assessed as somatic; moderate impact.
- R19K (p.Arg19Lys), TOPMed rs1840847436, REVEL 0.32, CADD 22.00
- Q21E (p.Gln21Glu), gnomAD rs1394871591, REVEL 0.56, CADD 23.60
- T22I (p.Thr22Ile), Ensembl rs1840846838
- T22R (p.Thr22Arg), NCI-TCGA TCGA novel, SIFT 0.00, Variant assessed as somatic; moderate impact.
- C23R (p.Cys23Arg), TOPMed rs1407526873, gnomAD rs1407526873, REVEL 0.35, CADD 25.40
- C23Y (p.Cys23Tyr), rs769337995, ClinGen CA5169499, ClinVar RCV001165521, ClinVar RCV001165522, REVEL 0.32, CADD 26.10, Uncertain significance, not provided; Tangier disease; Hypoalphalipoproteinemia, primary, 1
- L27R (p.Leu27Arg), Ensembl rs1588516100
- L27V (p.Leu27Val), TOPMed rs1839481537
- E28Q (p.Glu28Gln), rs755348141, ClinGen CA5169496, ClinVar RCV001904615, ClinVar RCV006634945, REVEL 0.38, CADD 27.50, Uncertain significance, Hypercholesterolemia, familial, 1; not provided
- V29G (p.Val29Gly), ExAC rs752155736, gnomAD rs752155736, REVEL 0.73, CADD 32.00
- A30V (p.Ala30Val), ExAC rs780741302, TOPMed rs780741302, gnomAD rs780741302, REVEL 0.12, CADD 22.30
- W31C (p.Trp31Cys), gnomAD rs1839480494, REVEL 0.89, CADD 29.90
- W31R (p.Trp31Arg), gnomAD rs1340795238, REVEL 0.92, CADD 30.00
- P32H (p.Pro32His), NCI-TCGA TCGA novel, SIFT 0.00, Variant assessed as somatic; moderate impact.
- F34L (p.Phe34Leu), cosmic curated COSV66058, TOPMed rs1839479648, SIFT 0.00
- I35V (p.Ile35Val), rs138992952, ClinGen CA5169491, ClinVar RCV001906801, ClinVar RCV005308583, REVEL 0.42, CADD 23.20, Conflicting interpretations, Cardiovascular phenotype; not provided
- I40L (p.Ile40Leu), TOPMed rs1839478202, SIFT 0.02
- V42A (p.Val42Ala), TOPMed rs1839477633, SIFT 0.00
- R43L (p.Arg43Leu), ExAC rs767261058, TOPMed rs767261058, gnomAD rs767261058, REVEL 0.95, CADD 28.80, Uncertain significance
- R43Q (p.Arg43Gln), rs767261058, ClinGen CA5169485, ClinVar RCV004201482, ExAC rs767261058, REVEL 0.89, CADD 29.50, Uncertain significance, Cardiovascular phenotype
- R43W (p.Arg43Trp), rs1458927804, NCI-TCGA Cosmic COSV6605, cosmic curated COSV66057, REVEL 0.89, CADD 32.00, Variant assessed as somatic; moderate impact.
- Y46C (p.Tyr46Cys), ExAC rs774092046, gnomAD rs774092046, REVEL 0.78, CADD 29.50
- Y46H (p.Tyr46His), TOPMed rs1024109695, gnomAD rs1024109695
- P47A (p.Pro47Ala), Ensembl rs1839475726
- P47L (p.Pro47Leu), TOPMed rs1839475530, gnomAD rs1839475530, REVEL 0.74, CADD 28.80, Uncertain significance, Cardiovascular phenotype
- P48L (p.Pro48Leu), gnomAD rs1195606986, REVEL 0.55, CADD 23.20
- P48R (p.Pro48Arg), gnomAD rs1195606986, REVEL 0.75, CADD 25.60
- E50Q (p.Glu50Gln), gnomAD rs1445439340, REVEL 0.25, CADD 22.60
- Q51* (p.Gln51Ter), gnomAD rs1260852374, CADD 46.00
- H52Q (p.His52Gln), TOPMed rs1839474289, SIFT 0.00
- H52R (p.His52Arg), gnomAD rs1210208195, REVEL 0.50, CADD 25.50
- E53A (p.Glu53Ala), TOPMed rs1051504651, REVEL 0.86, CADD 33.00
- E53G (p.Glu53Gly), TOPMed rs1051504651, REVEL 0.90, CADD 33.00, Uncertain significance, Cardiovascular phenotype
- C54G (p.Cys54Gly), Ensembl rs1564254351, REVEL 0.97, CADD 28.70
- C54S (p.Cys54Ser), NCI-TCGA Cosmic COSV6605, cosmic curated COSV66057, Variant assessed as somatic; moderate impact.
- H55R (p.His55Arg), ExAC rs754046194, gnomAD rs754046194, REVEL 0.92, CADD 26.30
- N58D (p.Asn58Asp), gnomAD rs1274571289, REVEL 0.78, CADD 29.00
- M61I (p.Met61Ile), ExAC rs764408074, gnomAD rs764408074, MetaLR 0.60, MetaSVM -0.15
- P62L (p.Pro62Leu), cosmic curated COSV10442, TOPMed rs907671851, gnomAD rs907671851, REVEL 0.93, MetaLR 0.95
- S63C (p.Ser63Cys), Ensembl rs1838980179, REVEL 0.89, MetaLR 0.98
- A64E (p.Ala64Glu), TOPMed rs1838979948, gnomAD rs1838979948, REVEL 0.89, MetaLR 0.98
- G65R (p.Gly65Arg), NCI-TCGA Cosmic COSV1010, cosmic curated COSV10103, NCI-TCGA Cosmic COSV6606, Variant assessed as somatic; moderate impact.
- L67P (p.Leu67Pro), gnomAD rs1235996098
- P68S (p.Pro68Ser), cosmic curated COSV10531, Ensembl rs928929671, REVEL 0.83, MetaLR 0.99
- W69G (p.Trp69Gly), ExAC rs756278529, gnomAD rs756278529, REVEL 0.95, MetaLR 0.99
- V70G (p.Val70Gly), NCI-TCGA TCGA novel, MetaLR 0.96, MetaSVM 1.11, Variant assessed as somatic; moderate impact.
- V70D (p.Val70Asp), rs964035613, []
- Q71H (p.Gln71His), gnomAD rs1301632435, REVEL 0.88, MetaLR 0.99
- G72W (p.Gly72Trp), gnomAD rs1440897035, REVEL 0.88, MetaLR 1.00
- I73V (p.Ile73Val), NCI-TCGA TCGA novel, MetaLR 0.94, MetaSVM 0.99, Variant assessed as somatic; moderate impact.
- I74V (p.Ile74Val), TOPMed rs1588502130, REVEL 0.49, MetaLR 0.89
- C75F (p.Cys75Phe), NCI-TCGA TCGA novel, MetaLR 0.99, MetaSVM 0.94, Variant assessed as somatic; moderate impact.
- C75S (p.Cys75Ser), TOPMed rs750478782, gnomAD rs750478782, REVEL 0.94, MetaLR 0.99
- A77G (p.Ala77Gly), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- A77V (p.Ala77Val), TOPMed rs1479726300, MetaLR 0.92, MetaSVM 0.78
- N78H (p.Asn78His), Ensembl rs981555662
- P80R (p.Pro80Arg), TOPMed rs983387544, gnomAD rs983387544, REVEL 0.86, MetaLR 0.97
- F82Y (p.Phe82Tyr), Ensembl rs951906188, Uncertain significance, Cardiovascular phenotype
- R83C (p.Arg83Cys), cosmic curated COSV10531, TOPMed rs1408254842, gnomAD rs1408254842, REVEL 0.89, MetaLR 0.96, Uncertain significance, Cardiovascular phenotype
- R83H (p.Arg83His), rs751367482, NCI-TCGA Cosmic COSV6605, cosmic curated COSV66057, ExAC rs751367482, REVEL 0.73, MetaLR 0.95, Conflicting interpretations, not provided
- R83S (p.Arg83Ser), TOPMed rs1408254842, gnomAD rs1408254842, REVEL 0.77, MetaLR 0.94, Uncertain significance, Cardiovascular phenotype
- Y84H (p.Tyr84His), ExAC rs766158859, gnomAD rs766158859, REVEL 0.38, MetaLR 0.83
- P85L (p.Pro85Leu), rs145183203, ClinGen CA5169461, cosmic curated COSV66059, ClinVar RCV000288931, REVEL 0.84, MetaLR 0.99, Conflicting interpretations, not provided; Hypoalphalipoproteinemia, primary, 1; Cardiovascular phenotype
- P85S (p.Pro85Ser), rs2119176197, ClinGen CA374316311, ClinVar RCV002261874, Ensembl rs2119176197, AlphaMissense 0.11, MetaLR 0.99, Uncertain significance, not provided
- T86A (p.Thr86Ala), Ensembl rs1023108666
- P87A (p.Pro87Ala), gnomAD rs1838974381, REVEL 0.63, MetaLR 0.96
- G88R (p.Gly88Arg), Ensembl rs2119176173, REVEL 0.89, MetaLR 1.00
- E89K (p.Glu89Lys), NCI-TCGA Cosmic COSV6605, cosmic curated COSV66057, Variant assessed as somatic; moderate impact.
- A90T (p.Ala90Thr), ExAC rs761420922, gnomAD rs761420922
- P91S (p.Pro91Ser), rs1436757527, NCI-TCGA Cosmic COSV6605, cosmic curated COSV66058, gnomAD rs1436757527, REVEL 0.89, MetaLR 1.00, Variant assessed as somatic; moderate impact.
- G92E (p.Gly92Glu), NCI-TCGA Cosmic COSV6605, cosmic curated COSV66059, Variant assessed as somatic; moderate impact.
- G92R (p.Gly92Arg), rs1212597294, TOPMed rs1212597294, gnomAD rs1212597294, REVEL 0.91, MetaLR 1.00, Variant assessed as somatic; moderate impact.
- V93D (p.Val93Asp), TOPMed rs964035613, Uncertain significance, Cardiovascular phenotype
- V93F (p.Val93Phe), NCI-TCGA Cosmic COSV6606, cosmic curated COSV66060, REVEL 0.57, MetaLR 0.93, Variant assessed as somatic; moderate impact.
- V93G (p.Val93Gly), NCI-TCGA TCGA novel, MetaLR 0.96, MetaSVM 1.10, Variant assessed as somatic; moderate impact.
- V93I (p.Val93Ile), TOPMed rs1450935000, gnomAD rs1450935000, REVEL 0.31, MetaLR 0.83, Conflicting interpretations, not provided; Cardiovascular phenotype
- G95* (p.Gly95Ter), TOPMed rs1838972114
- G95V (p.Gly95Val), TOPMed rs1838971909
- G95R (p.Gly95Arg), rs976402066, []
- F97C (p.Phe97Cys), ExAC rs768439631, gnomAD rs768439631, REVEL 0.92, MetaLR 0.83
- N98S (p.Asn98Ser), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- K99E (p.Lys99Glu), gnomAD rs1233984022
- K99R (p.Lys99Arg), Ensembl rs1588501795, MetaLR 0.51, MetaSVM -0.02
- S100C (p.Ser100Cys), TOPMed rs868563297, gnomAD rs868563297, REVEL 0.66, MetaLR 0.42
- S100F (p.Ser100Phe), cosmic curated COSV10468, TOPMed rs868563297, gnomAD rs868563297
- S100T (p.Ser100Thr), Ensembl rs1026309041
- I101T (p.Ile101Thr), ExAC rs746595809, gnomAD rs746595809, REVEL 0.61, MetaLR 0.26
- V102M (p.Val102Met), gnomAD rs1431676132
- A103S (p.Ala103Ser), Ensembl rs2119172738, MetaLR 0.12, MetaSVM -0.95
- R104C (p.Arg104Cys), rs141348278, cosmic curated COSV66058, ESP rs141348278, TOPMed rs141348278, REVEL 0.94, MetaLR 0.94, Variant assessed as somatic; moderate impact.
- R104H (p.Arg104His), ExAC rs772601794, TOPMed rs772601794, gnomAD rs772601794, REVEL 0.92, MetaLR 0.94
- R104P (p.Arg104Pro), cosmic curated COSV10748, ExAC rs772601794, TOPMed rs772601794, gnomAD rs772601794, REVEL 0.91, MetaLR 0.92
- L105P (p.Leu105Pro), ExAC rs746275015, gnomAD rs746275015, REVEL 0.98, MetaLR 0.95
- F106I (p.Phe106Ile), ExAC rs774529961, gnomAD rs774529961, REVEL 0.72, MetaLR 0.92
- F106L (p.Phe106Leu), ExAC rs774529961, gnomAD rs774529961, REVEL 0.56, MetaLR 0.72
- S107A (p.Ser107Ala), rs376321182, ClinGen CA5169427, ClinVar RCV002900528, ESP rs376321182, REVEL 0.20, MetaLR 0.74, Conflicting interpretations, not provided
- D108G (p.Asp108Gly), rs2538345868, ClinGen CA374316091, ClinVar RCV004370314, REVEL 0.91, MetaLR 0.93, Uncertain significance, Cardiovascular phenotype
- A109T (p.Ala109Thr), rs1387348591, ClinGen CA374316087, ClinVar RCV002716036, TOPMed rs1387348591, AlphaMissense 0.09, MetaLR 0.26, Uncertain significance, not provided
- R110Q (p.Arg110Gln), ExAC rs748409694, TOPMed rs748409694, gnomAD rs748409694, REVEL 0.12, MetaLR 0.06
- R110W (p.Arg110Trp), rs769844472, ClinGen CA5169425, cosmic curated COSV10654, ClinVar RCV002626904, REVEL 0.15, MetaLR 0.21, Likely benign, not provided
- R111S (p.Arg111Ser), 1000Genomes rs543312335, ExAC rs543312335, TOPMed rs543312335, gnomAD rs543312335, REVEL 0.47, MetaLR 0.80, Uncertain significance, not provided
- L113P (p.Leu113Pro), 1000Genomes rs2119172669, REVEL 0.85, MetaLR 0.39
- S116N (p.Ser116Asn), Ensembl rs201992557, REVEL 0.42, MetaLR 0.92
- Q117K (p.Gln117Lys), TOPMed rs1838833004
- Q117R (p.Gln117Arg), Ensembl rs935915046
- K118E (p.Lys118Glu), rs753703009, ClinGen CA5169418, cosmic curated COSV66057, ClinVar RCV000285655, REVEL 0.29, MetaLR 0.50, Uncertain significance, Hypoalphalipoproteinemia, primary, 1; Tangier disease
- D119E (p.Asp119Glu), rs763744498, ClinGen CA374316018, ClinVar RCV002021548, ClinVar RCV003331275, REVEL 0.55, MetaLR 0.80, Conflicting interpretations, not provided; not specified
- D119Y (p.Asp119Tyr), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- T120I (p.Thr120Ile), TOPMed rs1391677880, gnomAD rs1391677880, REVEL 0.43, MetaLR 0.86, Uncertain significance, Cardiovascular phenotype
- S121T (p.Ser121Thr), rs1564241066, ClinGen CA374316008, ClinVar RCV002452351, TOPMed rs1564241066, REVEL 0.32, MetaLR 0.83, Uncertain significance, Cardiovascular phenotype
- M122I (p.Met122Ile), TOPMed rs1380061540, REVEL 0.25, MetaLR 0.66
- M122L (p.Met122Leu), rs948927879, ClinGen CA197381924, ClinVar RCV004521440, TOPMed rs948927879, REVEL 0.20, MetaLR 0.41, Uncertain significance, Cardiovascular phenotype
- K123R (p.Lys123Arg), gnomAD rs1292688118, REVEL 0.23, MetaLR 0.64
- D124G (p.Asp124Gly), NCI-TCGA Cosmic COSV1010, cosmic curated COSV10103, REVEL 0.47, MetaLR 0.61, Variant assessed as somatic; moderate impact.
- D124N (p.Asp124Asn), gnomAD rs865982523, REVEL 0.38, MetaLR 0.76
- M125L (p.Met125Leu), TOPMed rs1364351263, gnomAD rs1364351263, MetaLR 0.43, MetaSVM -0.60, Uncertain significance, Cardiovascular phenotype
- M125V (p.Met125Val), TOPMed rs1364351263, gnomAD rs1364351263, REVEL 0.36, MetaLR 0.57
- R126C (p.Arg126Cys), rs1286945641, ClinGen CA374315969, ClinVar RCV001167635, ClinVar RCV001167636, REVEL 0.26, MetaLR 0.80, Uncertain significance, not provided; Hypoalphalipoproteinemia, primary, 1; Tangier disease
- R126G (p.Arg126Gly), TOPMed rs1286945641, gnomAD rs1286945641, REVEL 0.28, MetaLR 0.75, Uncertain significance
- R126H (p.Arg126His), rs138438101, NCI-TCGA Cosmic COSV6605, cosmic curated COSV66057, ESP rs138438101, REVEL 0.25, MetaLR 0.60, Likely benign, Cardiovascular phenotype
- R126L (p.Arg126Leu), ESP rs138438101, ExAC rs138438101, TOPMed rs138438101, gnomAD rs138438101, REVEL 0.23, MetaLR 0.66
- K127R (p.Lys127Arg), rs1394881972, NCI-TCGA Cosmic COSV6605, TOPMed rs1394881972, gnomAD rs1394881972, REVEL 0.27, MetaLR 0.75, Likely benign, not provided
- K127T (p.Lys127Thr), NCI-TCGA Cosmic COSV6605, cosmic curated COSV66058, MetaLR 0.75, MetaSVM 0.23, Variant assessed as somatic; moderate impact.
- R130G (p.Arg130Gly), ExAC rs759052376, gnomAD rs759052376, REVEL 0.17, MetaLR 0.73, Likely benign
- R130I (p.Arg130Ile), NCI-TCGA Cosmic COSV6605, cosmic curated COSV66057, MetaLR 0.71, MetaSVM 0.01, Variant assessed as somatic; moderate impact.
- T131A (p.Thr131Ala), NCI-TCGA Cosmic COSV6605, cosmic curated COSV66059, NCI-TCGA Cosmic COSV6606, Variant assessed as somatic; moderate impact.
- T131S (p.Thr131Ser), NCI-TCGA Cosmic COSV6605, NCI-TCGA Cosmic COSV6606, cosmic curated COSV66060, MetaLR 0.76, MetaSVM 0.15, Variant assessed as somatic; moderate impact.
- Q133* (p.Gln133Ter), ExAC rs774782707, TOPMed rs774782707, gnomAD rs774782707, CADD 35.00
- Q133P (p.Gln133Pro), rs771194181, ClinGen CA5169411, ClinVar RCV002700564, ExAC rs771194181, REVEL 0.42, MetaLR 0.82, Uncertain significance, not provided
- Q133R (p.Gln133Arg), ExAC rs771194181, TOPMed rs771194181, gnomAD rs771194181, REVEL 0.23, MetaLR 0.74, Uncertain significance
- Q134E (p.Gln134Glu), ExAC rs763565713, TOPMed rs763565713, gnomAD rs763565713, REVEL 0.12, MetaLR 0.74
- I135M (p.Ile135Met), ExAC rs773677698
- I135N (p.Ile135Asn), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- I135V (p.Ile135Val), TOPMed rs1838827223, MetaLR 0.60, MetaSVM -0.26, Uncertain significance, Cardiovascular phenotype
- K136N (p.Lys136Asn), NCI-TCGA Cosmic COSV6605, cosmic curated COSV66058, MetaLR 0.63, MetaSVM -0.34, Variant assessed as somatic; moderate impact.
- K137E (p.Lys137Glu), rs770247341, ClinGen CA5169408, ClinVar RCV003067121, ExAC rs770247341, REVEL 0.21, MetaLR 0.77, Uncertain significance, not provided
- S138P (p.Ser138Pro), rs1416907998, ClinGen CA374315894, ClinVar RCV002333057, TOPMed rs1416907998, REVEL 0.19, MetaLR 0.65, Uncertain significance, Cardiovascular phenotype
- S139G (p.Ser139Gly), ESP rs369383278, TOPMed rs369383278, MetaLR 0.75, MetaSVM -0.15
- N141D (p.Asn141Asp), ExAC rs748252360, gnomAD rs748252360, REVEL 0.16, MetaLR 0.55
- N141S (p.Asn141Ser), gnomAD rs1178234418, REVEL 0.22, MetaLR 0.56
- K143N (p.Lys143Asn), NCI-TCGA TCGA novel, MetaLR 0.87, MetaSVM 0.88, Variant assessed as somatic; moderate impact.
- K143T (p.Lys143Thr), gnomAD rs1836414141, REVEL 0.42, MetaLR 0.82
- L144P (p.Leu144Pro), ExAC rs751151447, gnomAD rs751151447, REVEL 0.74, MetaLR 0.94
- Q145L (p.Gln145Leu), TOPMed rs1348849954, gnomAD rs1348849954, REVEL 0.39, MetaLR 0.78
- Q145P (p.Gln145Pro), TOPMed rs1348849954, gnomAD rs1348849954, REVEL 0.65, MetaLR 0.80
- D146N (p.Asp146Asn), NCI-TCGA TCGA novel, MetaLR 0.91, MetaSVM 0.85, Variant assessed as somatic; moderate impact.
- L148Q (p.Leu148Gln), TOPMed rs1836413064, MetaLR 0.95, MetaSVM 1.09
- V149G (p.Val149Gly), rs2119105512, ClinGen CA374313245, ClinVar RCV001509364, Ensembl rs2119105512, REVEL 0.49, MetaLR 0.76, Uncertain significance, not provided
- D150N (p.Asp150Asn), ExAC rs766806821, TOPMed rs766806821, gnomAD rs766806821, REVEL 0.55, MetaLR 0.90
- N151S (p.Asn151Ser), TOPMed rs920799784, REVEL 0.37, MetaLR 0.84
- E152* (p.Glu152Ter), gnomAD rs1231762813, CADD 42.00
- E152A (p.Glu152Ala), NCI-TCGA TCGA novel, REVEL 0.85, MetaLR 0.95, Variant assessed as somatic; moderate impact.
- E152G (p.Glu152Gly), gnomAD rs1330498826, REVEL 0.88, MetaLR 0.94
- T153N (p.Thr153Asn), rs1836411504, ClinGen CA374313194, ClinVar RCV001978415, TOPMed rs1836411504, REVEL 0.63, MetaLR 0.91, Uncertain significance, not provided
- F154V (p.Phe154Val), gnomAD rs1307642956, REVEL 0.56, MetaLR 0.82
- S155C (p.Ser155Cys), rs1406953660, ClinGen CA374313168, ClinVar RCV004141247, AlphaMissense 0.62, MetaLR 0.95, Uncertain significance, Cardiovascular phenotype
- S155F (p.Ser155Phe), TOPMed rs1406953660, REVEL 0.80, AlphaMissense 0.62
- G156E (p.Gly156Glu), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- G156V (p.Gly156Val), rs369793332, ClinGen CA5169383, ClinVar RCV003118574, ESP rs369793332, REVEL 0.58, MetaLR 0.77, Likely benign, not provided
Public ABCA1 analysis runs
- ABCA1 analysis run — ABCA1 (2,727 variants) — completed 2026-08-19