TUBB2B (Tubulin beta-2B chain) variants and mutations

TUBB2B (also known as Tubulin beta-2B chain) is a human protein-coding gene encoding a tubulin beta-2B chain protein. It contributes to neuronal microtubules needed for progenitor division, neuronal migration, axon development, and cortical organization. Heterozygous pathogenic variants cause tubulinopathy with polymicrogyria, cortical dysplasia, developmental delay, and sometimes epilepsy. This analysis covers 669 TUBB2B variants and mutations. Of these, 82% have computational variant effect predictions. Disease context includes complex cortical dysplasia with other brain malformations 7, Polymicrogyria due to TUBB2B mutation, and breast cancer. Example TUBB2B variants include M1?, M1I, and R2H.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, MaveDB, LitVar.

Notable TUBB2B variants

Examples include M1?, M1I, R2H, R2S, V5M, I7F, Q8*, A9E. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.