BCL10 (B-cell lymphoma/leukemia 10) variants and mutations

BCL10 (also known as B-cell lymphoma/leukemia 10) is a human protein-coding gene encoding a b-cell lymphoma/leukemia 10 protein. It forms part of the CARD11-BCL10-MALT1 signaling complex that couples antigen-receptor activation to NF-kappaB signaling in lymphocytes. Biallelic loss can cause combined immunodeficiency, while dysregulated signaling contributes to certain lymphomas. This analysis covers 478 BCL10 variants and mutations. Of these, 79% have computational variant effect predictions. Disease context includes immunodeficiency 37, MALT lymphoma, and testicular germ cell tumor. Example BCL10 variants include M1L, E2D, and E2E.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, MaveDB, LitVar.

Notable BCL10 variants

Examples include M1L, E2D, E2E, P3P, T4S, T4T, T4A, A5G. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.