RBM10 (RNA-binding protein 10) variants and mutations
RBM10 (also known as RNA-binding protein 10) is a human protein-coding gene encoding a RNA-binding protein 10 protein. It regulates alternative pre-mRNA splicing and influences expression of proteins controlling cell growth, apoptosis, and differentiation. Loss-of-function variants cause TARP syndrome, while somatic inactivation is recurrent in lung adenocarcinoma and other cancers. This analysis covers 3,837 RBM10 variants and mutations. Of these, 21% have computational variant effect predictions. Disease context includes TARP syndrome, lung adenocarcinoma, and neurodegenerative disease. Example RBM10 variants include M1?, E2D, and E2G.
Variant analysis overview
- Gene: RBM10
- Protein: RNA-binding protein 10
- UniProt accession: P98175
- Organism: Homo sapiens
- Variants analyzed: 3837
- Variant scope: all variants
- Completed: 2026-08-22
Variant and mutation evidence
- Variant composition: 3,686 unspecified-consequence records; 76 synonymous variants; 52 missense variants; 12 in-frame deletions; 3 frameshift variants; 2 stop-gained variants; 2 splice-region variants; 3 in-frame insertions; 1 substitution
- Prediction scores: 799 variants have prediction scores (21% of the analyzed set).
Clinical, disease, and population context
- Disease context: 25 disease associations are represented. Top associations: TARP syndrome, lung adenocarcinoma, neurodegenerative disease, pancreatic adenocarcinoma, non-small cell lung carcinoma, colorectal adenocarcinoma, hereditary disease, urinary bladder cancer, bladder transitional cell carcinoma, cleft palate, gastric carcinoma, dengue disease.
Protein structure and variant hotspots
- Protein features: 3 domains; 14 post-translational modification sites.
- Structural context: 734 variants have structural context.
- PTM context: 59 variants overlap post-translational modification sites.
- Experimental data: 28 protein positions have experimental scores. Source: RBM10 Zinc finger, RanBP2-type domain domainome 1.0.
Data sources
Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, MaveDB, LitVar.
Notable RBM10 variants
Examples include M1?, E2D, E2G, E2K, E2Q, E2V, Y3*, Y3C. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.
- M1?, cosmic curated COSV52102, NCI-TCGA Cosmic COSV9933, cosmic curated COSV99333, cosmic curated COSV10941, Variant assessed as somatic; high impact.
- E2D (p.Glu2Asp), Ensembl rs2147065807
- E2G (p.Glu2Gly), NCI-TCGA Cosmic COSV9933, cosmic curated COSV99333, Ensembl rs2147065783, Variant assessed as somatic; moderate impact.
- E2K (p.Glu2Lys), cosmic curated COSV52102, Ensembl rs2147065765
- E2Q (p.Glu2Gln), Ensembl rs2147065765
- E2V (p.Glu2Val), Ensembl rs2147065783
- Y3* (p.Tyr3Ter), Ensembl rs2147065857
- Y3C (p.Tyr3Cys), rs1877750604, ClinGen CA412784297, ClinVar RCV002922667, TOPMed rs1877750604, REVEL 0.18, CADD 27.80, Uncertain significance, not provided
- Y3D (p.Tyr3Asp), Ensembl rs2147065821
- Y3N (p.Tyr3Asn), Ensembl rs2147065821
- Y3Y (p.Tyr3Tyr), gnomAD X-47147490-T-C, CADD 13.40
- E4G (p.Glu4Gly), Ensembl rs2147065869
- E4K (p.Glu4Lys), cosmic curated COSV52102, gnomAD rs1556762490, REVEL 0.14, CADD 28.20
- E4V (p.Glu4Val), Ensembl rs2147065869
- E4A (p.Glu4Ala), rs1481063725, gnomAD X-47145481-A-C, CADD 23.40
- R5* (p.Arg5Ter), cosmic curated COSV52102
- R5=, NCI-TCGA Cosmic COSV5210, Variant assessed as somatic; low impact.
- R5K (p.Arg5Lys), Ensembl rs2147065906
- R5S (p.Arg5Ser), Ensembl rs2147065922
- R5T (p.Arg5Thr), Ensembl rs2147065906
- R6C (p.Arg6Cys), NCI-TCGA Cosmic COSV5210, cosmic curated COSV52102, Ensembl rs2147065948, Variant assessed as somatic; moderate impact.
- R6G (p.Arg6Gly), Ensembl rs2147065948
- R6H (p.Arg6His), NCI-TCGA Cosmic COSV5210, cosmic curated COSV52101, Ensembl rs2147065970, Variant assessed as somatic; moderate impact.
- R6L (p.Arg6Leu), NCI-TCGA Cosmic COSV5210, Variant assessed as somatic; moderate impact.
- R6P (p.Arg6Pro), Ensembl rs2147065970, REVEL 0.12, CADD 34.00
- R6S (p.Arg6Ser), Ensembl rs2147065948
- G7A (p.Gly7Ala), Ensembl rs1934464276
- G7D (p.Gly7Asp), Ensembl rs1934464276
- G7S (p.Gly7Ser), Ensembl rs2147127432
- G7V (p.Gly7Val), Ensembl rs1934464276
- G7E (p.Gly7Glu), rs1432006293, gnomAD X-47145454-G-A, CADD 23.80
- G7G (p.Gly7Gly), gnomAD X-47145455-G-A, CADD 14.90
- G8A (p.Gly8Ala), Ensembl rs2147127478
- G8D (p.Gly8Asp), Ensembl rs2147127478
- G8S (p.Gly8Ser), Ensembl rs2147127467
- G8V (p.Gly8Val), cosmic curated COSV61313
- R9C (p.Arg9Cys), Ensembl rs2147127508
- R9G (p.Arg9Gly), Ensembl rs2147127508
- R9H (p.Arg9His), cosmic curated COSV61312, Ensembl rs2147127515, REVEL 0.16, CADD 29.80
- R9P (p.Arg9Pro), Ensembl rs2147127515
- R9W (p.Arg9Trp), rs1266887422, gnomAD X-47145474-C-T, CADD 24.20
- R9L (p.Arg9Leu), gnomAD X-47145475-G-T, CADD 23.40
- R9R (p.Arg9Arg), rs1556761631, gnomAD X-47145476-G-A, CADD 15.00
- G10A (p.Gly10Ala), Ensembl rs2147127550
- G10C (p.Gly10Cys), Ensembl rs2147127528
- G10R (p.Gly10Arg), Ensembl rs2147127528
- G10S (p.Gly10Ser), Ensembl rs2147127528
- G10G (p.Gly10Gly), gnomAD X-47169327-T-C, CADD 12.40
- D11E (p.Asp11Glu), Ensembl rs2147127602
- D11N (p.Asp11Asn), NCI-TCGA Cosmic COSV1002, cosmic curated COSV10023, Ensembl rs2147127574, Variant assessed as somatic; moderate impact.
- D11V (p.Asp11Val), Ensembl rs2147127594
- D11Y (p.Asp11Tyr), Ensembl rs2147127574
- R12G (p.Arg12Gly), Ensembl rs2147127613
- R12K (p.Arg12Lys), Ensembl rs2147127629
- R12S (p.Arg12Ser), Ensembl rs2147127638
- R12T (p.Arg12Thr), Ensembl rs2147127629
- R12W (p.Arg12Trp), Ensembl rs2147127613
- T13A (p.Thr13Ala), gnomAD rs1556770558
- T13P (p.Thr13Pro), gnomAD rs1556770558
- T13S (p.Thr13Ser), gnomAD rs1556770558
- G14A (p.Gly14Ala), Ensembl rs2147127711
- G14D (p.Gly14Asp), Ensembl rs2147127711
- G14S (p.Gly14Ser), cosmic curated COSV10520, Ensembl rs2147127700
- G14V (p.Gly14Val), Ensembl rs2147127711
- R15A (p.Arg15Ala), NCI-TCGA Cosmic COSV6131, Variant assessed as somatic; high impact.
- R15C (p.Arg15Cys), NCI-TCGA Cosmic COSV6131, cosmic curated COSV61310, Ensembl rs2147127747, REVEL 0.17, CADD 27.40, Variant assessed as somatic; moderate impact.
- R15G (p.Arg15Gly), Ensembl rs2147127747
- R15H (p.Arg15His), NCI-TCGA TCGA novel, Ensembl rs2147127759, Variant assessed as somatic; moderate impact.
- R15L (p.Arg15Leu), cosmic curated COSV10520
- R15P (p.Arg15Pro), Ensembl rs2147127759
- Y16* (p.Tyr16Ter), NCI-TCGA TCGA novel, Ensembl rs2147127831, Variant assessed as somatic; high impact.
- Y16C (p.Tyr16Cys), rs2147127817, ClinGen CA412788073, cosmic curated COSV61310, ClinVar RCV001764111, AlphaMissense 0.96, MetaLR 0.08, Uncertain significance, not provided
- Y16F (p.Tyr16Phe), Ensembl rs2147127817, Uncertain significance
- Y16H (p.Tyr16His), Ensembl rs2147127794
- Y16N (p.Tyr16Asn), Ensembl rs2147127794
- G17* (p.Gly17Ter), Ensembl rs2147127840
- G17R (p.Gly17Arg), Ensembl rs2147127840
- G17W (p.Gly17Trp), NCI-TCGA TCGA novel, Variant assessed as somatic; high impact.
- G17S (p.Gly17Ser), gnomAD X-47145501-G-A, CADD 23.20
- G17C (p.Gly17Cys), gnomAD X-47145501-G-T, CADD 24.90
- G17V (p.Gly17Val), rs1932035675, gnomAD X-47145502-G-T, CADD 21.60
- G17G (p.Gly17Gly), gnomAD X-47145509-G-T, CADD 16.10
- A18G (p.Ala18Gly), Ensembl rs2147127864, REVEL 0.05, CADD 23.10
- A18V (p.Ala18Val), Ensembl rs2147127864
- A18D (p.Ala18Asp), gnomAD X-47145472-C-A, CADD 22.70
- A18A (p.Ala18Ala), gnomAD X-47145473-C-T, CADD 16.00
- A18S (p.Ala18Ser), rs1251032975, gnomAD X-47145498-G-T, CADD 17.30
- A18T (p.Ala18Thr), rs1251032975, gnomAD X-47145498-G-A, CADD 22.20
- A18E (p.Ala18Glu), rs781937346, gnomAD X-47147387-C-A, CADD 22.70
- T19S (p.Thr19Ser), TOPMed rs1420226129, gnomAD rs1420226129, REVEL 0.09, CADD 16.10
- D20A (p.Asp20Ala), Ensembl rs2147127933
- D20E (p.Asp20Glu), Ensembl rs2147127948
- D20G (p.Asp20Gly), Ensembl rs2147127933
- D20H (p.Asp20His), Ensembl rs2147127913
- D20N (p.Asp20Asn), cosmic curated COSV61312, Ensembl rs2147127913
- D20V (p.Asp20Val), Ensembl rs2147127933
- D20Y (p.Asp20Tyr), Ensembl rs2147127913
- R21C (p.Arg21Cys), cosmic curated COSV10966, ExAC rs782165166, TOPMed rs782165166, gnomAD rs782165166, REVEL 0.14, CADD 27.70, Uncertain significance, not provided
- R21G (p.Arg21Gly), ExAC rs782165166, TOPMed rs782165166, gnomAD rs782165166
- R21H (p.Arg21His), NCI-TCGA Cosmic COSV6131, cosmic curated COSV61312, gnomAD rs1934465408, REVEL 0.12, CADD 25.10, Variant assessed as somatic; moderate impact.
- R21L (p.Arg21Leu), gnomAD rs1934465408, REVEL 0.15, CADD 25.10
- R21P (p.Arg21Pro), gnomAD rs1934465408
- R21S (p.Arg21Ser), rs782756726, gnomAD X-47145502-G-GT, CADD 23.80
- R21R (p.Arg21Arg), rs1224947130, gnomAD X-47145506-T-G, CADD 18.40
- S22* (p.Ser22Ter), ExAC rs782373421, gnomAD rs782373421
- S22L (p.Ser22Leu), cosmic curated COSV10885, ExAC rs782373421, gnomAD rs782373421, REVEL 0.06, CADD 19.70
- S22P (p.Ser22Pro), Ensembl rs2147128005, REVEL 0.04, CADD 21.90
- S22T (p.Ser22Thr), Ensembl rs2147128005
- S22W (p.Ser22Trp), ExAC rs782373421, gnomAD rs782373421
- S22S (p.Ser22Ser), gnomAD X-47145452-T-C, CADD 13.00
- S22R (p.Ser22Arg), rs1932026711, gnomAD X-47145458-C-A, CADD 21.70
- S6del (p.Ser6del), gnomAD X-47145461-TTCC-T, CADD 20.70
- S22A (p.Ser22Ala), gnomAD X-47147359-T-G, CADD 17.60
- S22Y (p.Ser22Tyr), rs2147064198, gnomAD X-47147360-C-A, CADD 21.00
- S22F (p.Ser22Phe), rs2147064198, gnomAD X-47147360-C-T, CADD 18.40
- Q23* (p.Gln23Ter), NCI-TCGA TCGA novel, TOPMed rs1934466298, Variant assessed as somatic; high impact.
- Q23E (p.Gln23Glu), TOPMed rs1934466298
- Q23H (p.Gln23His), Ensembl rs2147128102
- Q23K (p.Gln23Lys), TOPMed rs1934466298
- Q23R (p.Gln23Arg), gnomAD X-47169365-A-G, REVEL 0.05, CADD 22.80
- D24H (p.Asp24His), Ensembl rs2147128124
- D24N (p.Asp24Asn), Ensembl rs2147128124, Uncertain significance, Inborn genetic diseases
- D25G (p.Asp25Gly), NCI-TCGA Cosmic COSV1002, cosmic curated COSV10023, Ensembl rs2147128171, REVEL 0.10, CADD 23.70, Variant assessed as somatic; moderate impact.
- D25H (p.Asp25His), Ensembl rs2147128159
- D25N (p.Asp25Asn), Ensembl rs2147128159
- D25V (p.Asp25Val), Ensembl rs2147128171
- D25Y (p.Asp25Tyr), Ensembl rs2147128159
- D25D (p.Asp25Asp), rs200766225, gnomAD X-47169372-T-C, CADD 6.70
- G26A (p.Gly26Ala), Ensembl rs2147128198
- G26C (p.Gly26Cys), Ensembl rs2147128188
- G26V (p.Gly26Val), Ensembl rs2147128198
- G26R (p.Gly26Arg), gnomAD X-47145506-T-TG, CADD 32.00
- G26D (p.Gly26Asp), gnomAD X-47145511-G-A, CADD 19.50
- G26G (p.Gly26Gly), gnomAD X-47145512-C-T, CADD 16.30
- G26E (p.Gly26Glu), gnomAD X-47145514-G-A, CADD 23.70
- G27A (p.Gly27Ala), Ensembl rs2147128231
- G27E (p.Gly27Glu), Ensembl rs2147128231
- G27R (p.Gly27Arg), Ensembl rs2147128218
- G27V (p.Gly27Val), Ensembl rs2147128231
- G27S (p.Gly27Ser), rs2147064658, gnomAD X-47147395-G-A, CADD 23.70
- E28D (p.Glu28Asp), Ensembl rs2147128284
- E28G (p.Glu28Gly), Ensembl rs2147128272
- E28K (p.Glu28Lys), Ensembl rs2147128256
- E28Q (p.Glu28Gln), Ensembl rs2147128256
- N29D (p.Asn29Asp), Ensembl rs2147128301
- N29I (p.Asn29Ile), Ensembl rs2147128314
- N29K (p.Asn29Lys), Ensembl rs2147128335
- N29S (p.Asn29Ser), Ensembl rs2147128314
- N29T (p.Asn29Thr), Ensembl rs2147128314
- N29Y (p.Asn29Tyr), Ensembl rs2147128301
- N29N (p.Asn29Asn), rs2147128335, gnomAD X-47169384-C-T, CADD 9.79
- R30C (p.Arg30Cys), rs782008653, ExAC rs782008653, TOPMed rs782008653, gnomAD rs782008653, REVEL 0.16, CADD 25.80, Variant assessed as somatic; moderate impact.
- R30G (p.Arg30Gly), ExAC rs782008653, TOPMed rs782008653, gnomAD rs782008653
- R30H (p.Arg30His), NCI-TCGA Cosmic COSV1002, cosmic curated COSV10023, Ensembl rs2147128362, Variant assessed as somatic; moderate impact.
- R30L (p.Arg30Leu), Ensembl rs2147128362
- R30P (p.Arg30Pro), Ensembl rs2147128362
- R30R (p.Arg30Arg), gnomAD X-47169387-C-T, CADD 11.20
- S31I (p.Ser31Ile), Ensembl rs2147128394
- S31N (p.Ser31Asn), Ensembl rs2147128394
- S31R (p.Ser31Arg), Ensembl rs2147128409, REVEL 0.07, CADD 18.30
- S31T (p.Ser31Thr), Ensembl rs2147128394
- S31L (p.Ser31Leu), rs2147064417, gnomAD X-47147375-C-T, CADD 25.20
- R32* (p.Arg32Ter), NCI-TCGA Cosmic COSV6130, cosmic curated COSV61309, Ensembl rs2147128429, Variant assessed as somatic; high impact.
- R32G (p.Arg32Gly), Ensembl rs2147128429, CADD 25.00
- R32P (p.Arg32Pro), Ensembl rs1934467229
- R32Q (p.Arg32Gln), Ensembl rs1934467229
- R32W (p.Arg32Trp), rs782312811, gnomAD X-47147380-A-T, CADD 26.10
- R32S (p.Arg32Ser), rs1193846029, gnomAD X-47147380-AG-A, CADD 24.70
- R32R (p.Arg32Arg), rs2147064502, gnomAD X-47147382-G-A, CADD 11.90
- D33E (p.Asp33Glu), cosmic curated COSV10885, ESP rs368193449, ExAC rs368193449, gnomAD rs368193449
- D33H (p.Asp33His), ExAC rs782092488, gnomAD rs782092488, Uncertain significance
- D33N (p.Asp33Asn), rs782092488, ClinGen CA10395044, ClinVar RCV003716945, ExAC rs782092488, REVEL 0.15, CADD 25.40, Uncertain significance, not provided
- D33D (p.Asp33Asp), rs368193449, gnomAD X-47169396-C-T, CADD 13.10
- H34L (p.His34Leu), Ensembl rs2147128517
- H34N (p.His34Asn), Ensembl rs1934468199
- H34P (p.His34Pro), Ensembl rs2147128517
- H34Q (p.His34Gln), 1000Genomes rs200208681, ExAC rs200208681, TOPMed rs200208681, gnomAD rs200208681
- H34R (p.His34Arg), Ensembl rs2147128517
- H34Y (p.His34Tyr), Ensembl rs1934468199, REVEL 0.06, CADD 23.20
- H34H (p.His34His), rs1556762422, gnomAD X-47147394-T-C, CADD 13.40
Public RBM10 analysis runs
- RBM10 analysis run — RBM10 (3,837 variants) — completed 2026-08-22