POLD1 (P28340) variants and mutations

POLD1 (also known as P28340) is a human protein-coding gene encoding a DNA polymerase delta catalytic subunit protein. It performs much of lagging-strand DNA synthesis and proofreads newly replicated DNA through its exonuclease activity. Germline proofreading-domain variants cause polymerase-proofreading-associated polyposis and cancer predisposition, while other variants can produce developmental progeroid syndromes. This analysis covers 3,864 POLD1 variants and mutations. Of these, 66% have computational variant effect predictions. Disease context includes mandibular hypoplasia-deafness-progeroid syndrome, non-small cell lung carcinoma, and acute lymphoblastic leukemia. Example POLD1 variants include M1K, M1L, and M1T.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, ClinGen, MaveDB, LitVar.

Notable POLD1 variants

Examples include M1K, M1L, M1T, M1V, D2E, D2G, D2H, D2Y. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.