VCL (Vinculin) variants and mutations

VCL (also known as Vinculin) is a human protein-coding gene encoding a vinculin protein. It links integrins and cadherins to the actin cytoskeleton at focal adhesions and adherens junctions, transmitting mechanical force between cells and matrix. Pathogenic variants can cause dilated or hypertrophic cardiomyopathy and, in some cases, skeletal myopathy. This analysis covers 1,415 VCL variants and mutations. Of these, 78% have computational variant effect predictions. Disease context includes dilated cardiomyopathy 1W, hypertrophic cardiomyopathy 15, and hypertrophic cardiomyopathy. Example VCL variants include P2A, P2L, and P2P.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, ClinGen, MaveDB, LitVar.

Notable VCL variants

Examples include P2A, P2L, P2P, V3A, F4L, H5P, H5H, T6K. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.