PRKCB (Protein kinase C beta type) variants and mutations
PRKCB (also known as Protein kinase C beta type) is a human protein-coding gene encoding a protein kinase C beta type protein. Its annotated function is calcium-activated, phospholipid- and diacylglycerol (DAG)-dependent serine/threonine-protein kinase involved in various cellular processes such as regulation of the B-cell receptor (BCR) signalosome, oxidative stress-induced apoptosis…. It is annotated at the cytoplasm. This analysis covers 1,025 PRKCB variants and mutations. Of these, 54% have computational variant effect predictions. Disease context includes acute myeloid leukemia, mast cell leukemia, and systemic mastocytosis. Example PRKCB variants include A2V, A2T, and A2P.
Variant analysis overview
- Gene: PRKCB
- Protein: Protein kinase C beta type
- UniProt accession: P05771
- Organism: Homo sapiens
- Variants analyzed: 1025
- Variant scope: all variants
- Completed: 2026-08-28
Variant and mutation evidence
- Variant composition: 842 unspecified-consequence records; 92 missense variants; 79 synonymous variants; 6 frameshift variants; 1 in-frame deletions; 2 stop-gained variants; 3 splice-region variants
- Prediction scores: 550 variants have prediction scores (54% of the analyzed set).
Clinical, disease, and population context
- Disease context: 25 disease associations are represented. Top associations: acute myeloid leukemia, mast cell leukemia, systemic mastocytosis, mastocytosis, ulcerative colitis, neoplasm, inflammatory bowel disease, acute myeloid leukemia by FAB classification, diffuse large B-cell lymphoma, peripheral neuropathy, psoriasis, Crohn disease.
Protein structure and variant hotspots
- Protein features: 3 domains; 16 binding sites; 17 post-translational modification sites.
- Structural context: 569 variants have structural context.
- PTM context: 33 variants overlap post-translational modification sites.
Data sources
Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, MaveDB, LitVar.
Notable PRKCB variants
Examples include A2V, A2T, A2P, A2S, A2G, D3E, D3Y, D3N. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.
- A2V (p.Ala2Val), cosmic curated COSV10732, CADD 23.80, PolyPhen-2 0.00
- A2T (p.Ala2Thr), gnomAD 16-23836179-G-A, CADD 24.80, PolyPhen-2 0.01
- A2P (p.Ala2Pro), gnomAD 16-23836179-G-C, CADD 24.90, PolyPhen-2 0.09
- A2S (p.Ala2Ser), gnomAD 16-23836179-G-T, CADD 23.10, PolyPhen-2 0.00
- A2G (p.Ala2Gly), gnomAD 16-23836180-C-G, CADD 23.80, PolyPhen-2 0.01
- D3E (p.Asp3Glu), gnomAD rs1290205152, CADD 23.90, PolyPhen-2 0.89
- D3Y (p.Asp3Tyr), gnomAD 16-23836182-G-T, CADD 31.00, PolyPhen-2 0.99
- D3N (p.Asp3Asn), gnomAD 16-23836182-G-A, CADD 31.00, PolyPhen-2 0.93
- D3D (p.Asp3Asp), gnomAD 16-23836184-C-T, CADD 15.60
- P4A (p.Pro4Ala), TOPMed rs1012485614, CADD 19.90, PolyPhen-2 0.00
- P4L (p.Pro4Leu), 1000Genomes rs757085223, ExAC rs757085223, gnomAD rs757085223, CADD 22.70, PolyPhen-2 0.00
- P4R (p.Pro4Arg), cosmic curated COSV57792, 1000Genomes rs757085223, ExAC rs757085223, gnomAD rs757085223, CADD 23.60, PolyPhen-2 0.00
- P4T (p.Pro4Thr), gnomAD 16-23836185-C-A, CADD 21.40, PolyPhen-2 0.00
- P4Q (p.Pro4Gln), gnomAD 16-23836186-C-A, CADD 23.50, PolyPhen-2 0.01
- P4P (p.Pro4Pro), rs1962150407, gnomAD 16-23836187-G-A, CADD 16.00
- A5D (p.Ala5Asp), 1000Genomes rs201366670, ExAC rs201366670, gnomAD rs201366670, CADD 22.60, PolyPhen-2 0.00
- A5V (p.Ala5Val), 1000Genomes rs201366670, ExAC rs201366670, gnomAD rs201366670, CADD 22.50, PolyPhen-2 0.00
- A5T (p.Ala5Thr), gnomAD 16-23836188-G-A, CADD 22.70, PolyPhen-2 0.00
- A5P (p.Ala5Pro), gnomAD 16-23836188-G-C, CADD 22.90, PolyPhen-2 0.01
- A5G (p.Ala5Gly), gnomAD 16-23836189-C-G, CADD 22.50, PolyPhen-2 0.00
- A6E (p.Ala6Glu), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- A6T (p.Ala6Thr), rs2506948286, ClinGen CA395267085, ClinVar RCV004210563, CADD 23.60, PolyPhen-2 0.01, Uncertain significance, not specified
- A6V (p.Ala6Val), gnomAD rs1269979183, CADD 24.00, PolyPhen-2 0.01, Uncertain significance, not specified
- A6S (p.Ala6Ser), gnomAD 16-23836191-G-T, CADD 21.30, PolyPhen-2 0.01
- A6A (p.Ala6Ala), rs768549392, gnomAD 16-23836193-G-A, CADD 16.50
- G7A (p.Gly7Ala), Ensembl rs1962150664
- G7E (p.Gly7Glu), Ensembl rs1962150664, CADD 22.90, PolyPhen-2 0.09, Uncertain significance, not specified
- G7R (p.Gly7Arg), gnomAD 16-23836194-G-A, CADD 23.20, PolyPhen-2 0.30
- G7G (p.Gly7Gly), gnomAD 16-23836196-G-A, CADD 15.40
- P8Q (p.Pro8Gln), ExAC rs781362818, gnomAD rs781362818, CADD 21.80, PolyPhen-2 0.00
- P8R (p.Pro8Arg), gnomAD 16-23836192-CG-C, CADD 29.60
- P8S (p.Pro8Ser), gnomAD 16-23836197-C-T, CADD 19.80, PolyPhen-2 0.00
- P8T (p.Pro8Thr), gnomAD 16-23836197-C-A, CADD 20.90, PolyPhen-2 0.00
- P8L (p.Pro8Leu), gnomAD 16-23836198-C-T, CADD 22.50, PolyPhen-2 0.00
- P8P (p.Pro8Pro), rs1364388947, gnomAD 16-23836199-G-A, CADD 15.70
- P9Q (p.Pro9Gln), ESP rs368093414, ExAC rs368093414, TOPMed rs368093414, gnomAD rs368093414, CADD 18.00, PolyPhen-2 0.00
- P9S (p.Pro9Ser), 1000Genomes rs575795787, ExAC rs575795787, gnomAD rs575795787, CADD 13.20, PolyPhen-2 0.00
- P9R (p.Pro9Arg), gnomAD 16-23836201-C-G, CADD 18.60, PolyPhen-2 0.00
- P9L (p.Pro9Leu), gnomAD 16-23836201-C-T, CADD 19.40, PolyPhen-2 0.00
- P9P (p.Pro9Pro), gnomAD 16-23836202-G-A, CADD 15.30
- P10L (p.Pro10Leu), gnomAD rs1425263935, CADD 23.10, PolyPhen-2 0.13
- P10S (p.Pro10Ser), gnomAD rs1384528118
- P10T (p.Pro10Thr), NCI-TCGA Cosmic COSV5778, cosmic curated COSV57782, Variant assessed as somatic; moderate impact.
- P10R (p.Pro10Arg), gnomAD 16-23836204-C-G, CADD 21.70, PolyPhen-2 0.33
- P10P (p.Pro10Pro), gnomAD 16-23836205-G-A, CADD 15.70
- S11G (p.Ser11Gly), gnomAD 16-23836206-A-G, CADD 17.70, PolyPhen-2 0.00
- S11N (p.Ser11Asn), gnomAD 16-23836207-G-A, CADD 15.80, PolyPhen-2 0.00
- S11R (p.Ser11Arg), gnomAD 16-23836208-C-A, CADD 15.90, PolyPhen-2 0.00
- S11S (p.Ser11Ser), rs1962151180, gnomAD 16-23836208-C-T, CADD 14.20
- E12D (p.Glu12Asp), cosmic curated COSV10033, CADD 22.60, PolyPhen-2 0.00
- E12V (p.Glu12Val), ESP rs370984906, ExAC rs370984906, TOPMed rs370984906, gnomAD rs370984906, CADD 24.70, PolyPhen-2 0.00
- E12E (p.Glu12Glu), rs1394092955, gnomAD 16-23836211-G-A, CADD 15.10
- G13D (p.Gly13Asp), ExAC rs749669754, gnomAD rs749669754, CADD 23.00, PolyPhen-2 0.08
- G13R (p.Gly13Arg), gnomAD 16-23836212-G-C, CADD 24.10, PolyPhen-2 0.01
- G13C (p.Gly13Cys), gnomAD 16-23836212-G-T, CADD 24.80, PolyPhen-2 0.43
- G13S (p.Gly13Ser), gnomAD 16-23836212-G-A, CADD 22.10, PolyPhen-2 0.00
- G13G (p.Gly13Gly), gnomAD 16-23836214-C-T, CADD 14.90
- E14G (p.Glu14Gly), gnomAD rs1243136292, AlphaMissense 0.06, MetaLR 0.19
- E14K (p.Glu14Lys), rs771388864, ExAC rs771388864, gnomAD rs771388864, CADD 23.00, PolyPhen-2 0.00, Variant assessed as somatic; moderate impact.
- E14V (p.Glu14Val), rs1243136292, ClinGen CA395267135, ClinVar RCV004077074, AlphaMissense 0.06, MetaLR 0.19, Uncertain significance, not specified
- E14Q (p.Glu14Gln), gnomAD 16-23836215-G-C, CADD 22.60, PolyPhen-2 0.03
- E14* (p.Glu14Ter), gnomAD 16-23836215-G-T, CADD 40.00
- E14E (p.Glu14Glu), gnomAD 16-23836217-G-A, CADD 14.10
- E15K (p.Glu15Lys), TOPMed rs1313793731, gnomAD rs1313793731, CADD 24.30, PolyPhen-2 0.55, Uncertain significance, not specified
- E15del (p.Glu15del), rs1329149162, gnomAD 16-23836214-CGAG-, CADD 21.80
- S16I (p.Ser16Ile), TOPMed rs1359470631, gnomAD rs1359470631, CADD 23.00
- S16N (p.Ser16Asn), gnomAD 16-23836222-G-A, CADD 21.90, PolyPhen-2 0.02
- S16S (p.Ser16Ser), gnomAD 16-23836223-C-T, CADD 16.10
- T17I (p.Thr17Ile), ExAC rs773819749, gnomAD rs773819749, CADD 22.50, PolyPhen-2 0.21
- T17A (p.Thr17Ala), gnomAD 16-23836224-A-G, CADD 19.10, PolyPhen-2 0.00
- T17T (p.Thr17Thr), gnomAD 16-23836226-C-G, CADD 8.37
- V18M (p.Val18Met), NCI-TCGA Cosmic COSV5776, cosmic curated COSV57763, CADD 22.80, PolyPhen-2 0.01, Variant assessed as somatic; moderate impact.
- V18L (p.Val18Leu), gnomAD 16-23836227-G-C, CADD 21.10, PolyPhen-2 0.00
- R19C (p.Arg19Cys), NCI-TCGA Cosmic COSV5776, cosmic curated COSV57769, CADD 32.00, PolyPhen-2 0.97, Variant assessed as somatic; moderate impact.
- R19H (p.Arg19His), ExAC rs759234204, gnomAD rs759234204, CADD 28.90, PolyPhen-2 0.95
- R19L (p.Arg19Leu), cosmic curated COSV57780, CADD 28.60, PolyPhen-2 0.88
- R19P (p.Arg19Pro), ExAC rs759234204, gnomAD rs759234204
- R19S (p.Arg19Ser), gnomAD 16-23836230-C-A, CADD 25.20, PolyPhen-2 0.88
- F20L (p.Phe20Leu), ExAC rs766899029, gnomAD rs766899029, CADD 25.80, PolyPhen-2 0.48
- F20S (p.Phe20Ser), NCI-TCGA Cosmic COSV1003, cosmic curated COSV10033, Variant assessed as somatic; moderate impact.
- A21D (p.Ala21Asp), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- A21P (p.Ala21Pro), NCI-TCGA Cosmic COSV5777, Variant assessed as somatic; moderate impact.
- A21T (p.Ala21Thr), rs1195385839, NCI-TCGA Cosmic COSV5777, cosmic curated COSV57778, TOPMed rs1195385839, CADD 23.00, PolyPhen-2 0.39, Variant assessed as somatic; moderate impact.
- A21V (p.Ala21Val), gnomAD 16-23836237-C-T, CADD 22.70, PolyPhen-2 0.05
- A21A (p.Ala21Ala), gnomAD 16-23836238-C-A, CADD 16.40
- R22G (p.Arg22Gly), NCI-TCGA Cosmic COSV5779, cosmic curated COSV57798, Variant assessed as somatic; moderate impact.
- R22H (p.Arg22His), cosmic curated COSV10732, 1000Genomes rs200442462, CADD 32.00, PolyPhen-2 1.00
- R22S (p.Arg22Ser), gnomAD 16-23836239-C-A, CADD 27.80, PolyPhen-2 1.00
- R22L (p.Arg22Leu), gnomAD 16-23836240-G-T, CADD 32.00, PolyPhen-2 1.00
- R22R (p.Arg22Arg), rs775089575, gnomAD 16-23836241-C-T, CADD 16.90
- K23Q (p.Lys23Gln), gnomAD 16-23836242-A-C, CADD 22.30, PolyPhen-2 0.05
- K23R (p.Lys23Arg), gnomAD 16-23836243-A-G, CADD 22.30, PolyPhen-2 0.02
- K23K (p.Lys23Lys), gnomAD 16-23836244-A-G, CADD 16.60
- G24D (p.Gly24Asp), cosmic curated COSV57795, CADD 29.70, PolyPhen-2 1.00
- G24R (p.Gly24Arg), ExAC rs760228327, gnomAD rs760228327, CADD 32.00, PolyPhen-2 1.00
- G24V (p.Gly24Val), cosmic curated COSV57783
- G24A (p.Gly24Ala), gnomAD 16-23836241-CA-C, CADD 29.00
- G24C (p.Gly24Cys), gnomAD 16-23836245-G-T, CADD 32.00, PolyPhen-2 1.00
- G24G (p.Gly24Gly), rs763989321, gnomAD 16-23836247-C-T, CADD 16.00
- A25T (p.Ala25Thr), gnomAD 16-23836248-G-A, CADD 30.00, PolyPhen-2 1.00
- A25A (p.Ala25Ala), gnomAD 16-23836250-C-T, CADD 15.10
- L26I (p.Leu26Ile), gnomAD 16-23836251-C-A, CADD 22.30, PolyPhen-2 0.40
- L26F (p.Leu26Phe), gnomAD 16-23836251-C-T, CADD 25.70, PolyPhen-2 0.97
- L26L (p.Leu26Leu), gnomAD 16-23836253-C-T, CADD 14.80
- R27P (p.Arg27Pro), TOPMed rs1378724342, gnomAD rs1378724342
- R27Q (p.Arg27Gln), rs1378724342, TOPMed rs1378724342, gnomAD rs1378724342, CADD 32.00, PolyPhen-2 0.95, Variant assessed as somatic; moderate impact.
- R27W (p.Arg27Trp), gnomAD 16-23836254-C-T, CADD 27.30, PolyPhen-2 1.00
- R27R (p.Arg27Arg), rs75964872, gnomAD 16-23836254-C-A, CADD 15.50
- Q28E (p.Gln28Glu), Ensembl rs1962153164
- Q28R (p.Gln28Arg), gnomAD 16-23836258-A-G, CADD 22.60, PolyPhen-2 0.10
- K29* (p.Lys29Ter), cosmic curated COSV10732
- K29E (p.Lys29Glu), gnomAD rs1461287415, CADD 29.50, PolyPhen-2 0.99
- K29M (p.Lys29Met), Ensembl rs2141070534
- K29N (p.Lys29Asn), cosmic curated COSV10033, cosmic curated COSV10732
- K29K (p.Lys29Lys), rs146177740, gnomAD 16-23836262-G-A, CADD 14.20
- N30H (p.Asn30His), Ensembl rs2141070543
- N30K (p.Asn30Lys), cosmic curated COSV10033, CADD 20.20, PolyPhen-2 0.23
- V31M (p.Val31Met), cosmic curated COSV57782, gnomAD rs1962153490, CADD 28.50, PolyPhen-2 0.98
- V31A (p.Val31Ala), gnomAD 16-23836267-T-C, CADD 28.80, PolyPhen-2 0.91
- V31V (p.Val31Val), gnomAD 16-23836268-G-C, CADD 14.40
- H32L (p.His32Leu), rs2506948603, ClinGen CA395267253, ClinVar RCV004327593, Uncertain significance, not specified
- H32Q (p.His32Gln), TOPMed rs1401988911, gnomAD rs1401988911, CADD 23.40, PolyPhen-2 0.89
- H32N (p.His32Asn), gnomAD 16-23836269-C-A, CADD 25.90, PolyPhen-2 0.84
- H32Y (p.His32Tyr), gnomAD 16-23836269-C-T, CADD 22.60, PolyPhen-2 0.02
- H32H (p.His32His), rs1401988911, gnomAD 16-23836271-T-C, CADD 14.60
- E33G (p.Glu33Gly), gnomAD 16-23836273-A-G, CADD 32.00, PolyPhen-2 0.74
- E33E (p.Glu33Glu), rs751689932, gnomAD 16-23836274-G-A, CADD 14.90
- V34I (p.Val34Ile), gnomAD 16-23836275-G-A, CADD 23.00, PolyPhen-2 0.15
- V34A (p.Val34Ala), gnomAD 16-23836276-T-C, CADD 29.70, PolyPhen-2 0.83
- V34V (p.Val34Val), rs1597201117, gnomAD 16-23836277-C-G, CADD 14.30
- K35R (p.Lys35Arg), TOPMed rs1962153958, CADD 23.50, PolyPhen-2 0.39
- K35K (p.Lys35Lys), gnomAD 16-23836280-G-A, CADD 15.30
- N36S (p.Asn36Ser), gnomAD rs1335436295, CADD 22.60, PolyPhen-2 0.00
- N36T (p.Asn36Thr), cosmic curated COSV57794
- H37Y (p.His37Tyr), cosmic curated COSV10961, CADD 27.10, PolyPhen-2 1.00
- H37N (p.His37Asn), gnomAD 16-23836284-C-A, CADD 27.20, PolyPhen-2 1.00
- H37H (p.His37His), gnomAD 16-23836286-C-T, CADD 15.40
- K38R (p.Lys38Arg), Ensembl rs2141070561, CADD 23.10, PolyPhen-2 0.07
- K38T (p.Lys38Thr), gnomAD 16-23836288-A-C, CADD 27.10, PolyPhen-2 0.71
- K38K (p.Lys38Lys), rs755247718, gnomAD 16-23836289-A-G, CADD 15.40
- F39L (p.Phe39Leu), gnomAD 16-23836290-T-C, CADD 32.00, PolyPhen-2 1.00
- F39F (p.Phe39Phe), gnomAD 16-23836292-C-T, CADD 15.70
- T40A (p.Thr40Ala), cosmic curated COSV57804, CADD 23.20, PolyPhen-2 0.01
- T40I (p.Thr40Ile), cosmic curated COSV57766
- T40S (p.Thr40Ser), gnomAD 16-23836294-C-G, CADD 21.30, PolyPhen-2 0.01
- T40T (p.Thr40Thr), rs1487689045, gnomAD 16-23836295-C-T, CADD 14.50
- A41S (p.Ala41Ser), Ensembl rs2141070572, CADD 27.00
- A41T (p.Ala41Thr), NCI-TCGA Cosmic COSV1003, cosmic curated COSV10033, CADD 28.40, PolyPhen-2 0.95, Variant assessed as somatic; moderate impact.
- A41A (p.Ala41Ala), gnomAD 16-23836298-C-T, CADD 15.90
- R42H (p.Arg42His), NCI-TCGA Cosmic COSV1003, cosmic curated COSV10033, CADD 32.00, PolyPhen-2 0.98, Variant assessed as somatic; moderate impact.
- R42S (p.Arg42Ser), cosmic curated COSV10605
- R42L (p.Arg42Leu), gnomAD 16-23836300-G-T, CADD 31.00, PolyPhen-2 0.78
- R42R (p.Arg42Arg), gnomAD 16-23836301-C-T, CADD 16.00
- F43F (p.Phe43Phe), rs781315165, gnomAD 16-23836304-C-T, CADD 16.70
- F44I (p.Phe44Ile), cosmic curated COSV57777
- K45E (p.Lys45Glu), gnomAD 16-23836308-A-G, CADD 29.70, PolyPhen-2 0.94
- K45N (p.Lys45Asn), gnomAD 16-23836310-G-T, CADD 26.40, PolyPhen-2 0.97
- K45K (p.Lys45Lys), gnomAD 16-23836310-G-A, CADD 14.50
- Q46K (p.Gln46Lys), cosmic curated COSV10588
- Q46Q (p.Gln46Gln), rs1031003748, gnomAD 16-23836313-G-A, CADD 14.20
- P47L (p.Pro47Leu), rs2506948750, ClinGen CA395267365, ClinVar RCV004515135, Uncertain significance, not specified
- P47S (p.Pro47Ser), gnomAD 16-23836314-C-T, CADD 27.80, PolyPhen-2 0.99
- P47H (p.Pro47His), gnomAD 16-23836315-C-A, CADD 26.70, PolyPhen-2 1.00
- T48P (p.Thr48Pro), gnomAD rs1315454019, CADD 29.30, PolyPhen-2 0.98
- C50F (p.Cys50Phe), NCI-TCGA Cosmic COSV5780, Variant assessed as somatic; moderate impact.
- C50S (p.Cys50Ser), cosmic curated COSV57804, gnomAD rs1325263692, CADD 29.60, PolyPhen-2 0.97
- C50Y (p.Cys50Tyr), NCI-TCGA Cosmic COSV5780, Variant assessed as somatic; moderate impact.
- C50R (p.Cys50Arg), gnomAD 16-23836323-T-C, CADD 32.00, PolyPhen-2 0.98
- C50C (p.Cys50Cys), gnomAD 16-23836325-C-T, CADD 16.70
- S51R (p.Ser51Arg), gnomAD rs1227144603, NCI-TCGA Cosmic COSV1003, cosmic curated COSV10033, Variant assessed as somatic; moderate impact.
- S51N (p.Ser51Asn), gnomAD 16-23836327-G-A, CADD 28.70, PolyPhen-2 0.97
- S51S (p.Ser51Ser), gnomAD 16-23836328-C-T, CADD 15.80
- H52R (p.His52Arg), gnomAD rs1259154481, CADD 27.00, PolyPhen-2 0.97
- H52N (p.His52Asn), gnomAD 16-23836329-C-A, CADD 26.70, PolyPhen-2 0.98
- H52P (p.His52Pro), gnomAD 16-23836330-A-C, CADD 29.30, PolyPhen-2 0.99
- H52H (p.His52His), gnomAD 16-23836331-C-T, CADD 14.70
- C53G (p.Cys53Gly), NCI-TCGA Cosmic COSV5778, cosmic curated COSV57789, Variant assessed as somatic; moderate impact.
- C53Y (p.Cys53Tyr), cosmic curated COSV57768, CADD 32.00, PolyPhen-2 1.00
- T54S (p.Thr54Ser), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- T54A (p.Thr54Ala), gnomAD 16-23836335-A-G, CADD 25.10, PolyPhen-2 0.56
Public PRKCB analysis runs
- PRKCB analysis run — PRKCB (1,025 variants) — completed 2026-08-28