CARD9 (Q9H257) variants and mutations
CARD9 (also known as Q9H257) is a human protein-coding gene encoding a caspase recruitment domain-containing protein 9 protein. It couples fungal and other innate immune receptors to NF-kappaB and inflammatory signaling in myeloid cells. Biallelic loss-of-function variants cause profound susceptibility to invasive and mucocutaneous fungal infections. This analysis covers 953 CARD9 variants and mutations. Of these, 96% have computational variant effect predictions. Disease context includes Chronic mucocutaneous candidosis, inflammatory bowel disease, and Crohn disease. Example CARD9 variants include S2L, D3E, and Y4*.
Variant analysis overview
- Gene: CARD9
- Protein: Q9H257
- UniProt accession: Q9H257
- Organism: Homo sapiens
- Variants analyzed: 953
- Variant scope: all variants
- Completed: 2026-08-19
Variant and mutation evidence
- Variant composition: 743 unspecified-consequence records; 5 stop lost; 1 stop retained variant; 48 synonymous variants; 117 missense variants; 2 in-frame insertions; 4 splice-region variants; 11 frameshift variants; 13 stop-gained variants; 5 in-frame deletions; 3 substitution
- Prediction scores: 912 variants have prediction scores (96% of the analyzed set).
Clinical, disease, and population context
- Disease context: 25 disease associations are represented. Top associations: Chronic mucocutaneous candidosis, inflammatory bowel disease, Crohn disease, ulcerative colitis, IgA glomerulonephritis, deep seated dermatophytosis, dermatophytosis, dermatomycosis, immunodeficiency disease, ankylosing spondylitis, psoriasis, sclerosing cholangitis.
Protein structure and variant hotspots
- Protein features: 1 domains; 3 binding sites; 12 post-translational modification sites.
- Structural context: 109 variants have structural context.
- PTM context: 26 variants overlap post-translational modification sites.
Data sources
Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, MaveDB, LitVar.
Notable CARD9 variants
Examples include S2L, D3E, Y4*, Y4D, Y4H, E5K, D7N, D8E. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.
- S2L (p.Ser2Leu), rs995161906, ClinGen CA201615901, ClinVar RCV002795045, TOPMed rs995161906, REVEL 0.05, CADD 22.00, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- D3E (p.Asp3Glu), ESP rs375098569, ExAC rs375098569, TOPMed rs375098569, gnomAD rs375098569, REVEL 0.06, CADD 19.20, Uncertain significance, Inborn genetic diseases
- Y4* (p.Tyr4Ter), 1000Genomes rs35051231, ESP rs35051231, ExAC rs35051231, TOPMed rs35051231, CADD 32.00, Likely benign
- Y4D (p.Tyr4Asp), ExAC rs775128842, gnomAD rs775128842, REVEL 0.10, CADD 22.30, Uncertain significance
- Y4H (p.Tyr4His), rs775128842, ClinGen CA5333275, ClinVar RCV001035607, ClinVar RCV004963000, REVEL 0.10, CADD 23.40, Uncertain significance, Inborn genetic diseases; Predisposition to invasive fungal disease due to CARD9
- E5K (p.Glu5Lys), rs371061371, ClinGen CA5333272, cosmic curated COSV53730, ClinVar RCV001326189, REVEL 0.13, CADD 25.40, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- D7N (p.Asp7Asn), rs374091388, ClinGen CA5333270, ClinVar RCV000311218, ESP rs374091388, REVEL 0.17, CADD 24.30, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- D8E (p.Asp8Glu), 1000Genomes rs148523221, ESP rs148523221, ExAC rs148523221, TOPMed rs148523221, REVEL 0.04, CADD 0.00, Benign
- E9D (p.Glu9Asp), TOPMed rs1034840190, gnomAD rs1034840190, SIFT 0.14
- E9K (p.Glu9Lys), rs369865691, ClinGen CA5333268, ClinVar RCV000824334, ESP rs369865691, REVEL 0.05, CADD 9.84, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- E9V (p.Glu9Val), ExAC rs754129074, TOPMed rs754129074, gnomAD rs754129074, REVEL 0.03, CADD 13.20, Uncertain significance, Inborn genetic diseases
- S12I (p.Ser12Ile), 1000Genomes rs4077515, ESP rs4077515, ExAC rs4077515, TOPMed rs4077515, REVEL 0.03, CADD 6.80, Benign
- S12N (p.Ser12Asn), rs4077515, ClinGen CA5333266, cosmic curated COSV53731, ClinVar RCV000408113, REVEL 0.01, CADD 1.43, Likely benign, not specified; Predisposition to invasive fungal disease due to CARD9 deficiency
- V13A (p.Val13Ala), Ensembl rs2131445679, SIFT 0.88
- V13I (p.Val13Ile), rs377431254, ClinGen CA5333264, cosmic curated COSV53738, ClinVar RCV001987528, REVEL 0.06, CADD 0.31, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- V13L (p.Val13Leu), cosmic curated COSV53738, ESP rs377431254, ExAC rs377431254, TOPMed rs377431254, REVEL 0.06, CADD 0.35, Uncertain significance
- E15D (p.Glu15Asp), TOPMed rs971785161, gnomAD rs971785161, REVEL 0.23, CADD 22.90
- G16D (p.Gly16Asp), rs1833289004, ClinGen CA375546516, cosmic curated COSV53733, ClinVar RCV002954827, REVEL 0.09, CADD 14.90, Uncertain significance, Inborn genetic diseases
- G16S (p.Gly16Ser), cosmic curated COSV10459, ESP rs144081957, ExAC rs144081957, gnomAD rs144081957, REVEL 0.03, CADD 7.95
- F17S (p.Phe17Ser), rs1833288953, ClinGen CA375546509, ClinVar RCV001059439, Ensembl rs1833288953, REVEL 0.17, CADD 23.90, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- R18L (p.Arg18Leu), ESP rs372586424, TOPMed rs372586424, REVEL 0.64, CADD 25.00
- R18Q (p.Arg18Gln), ESP rs372586424, TOPMed rs372586424, REVEL 0.52, CADD 25.60, Uncertain significance, not provided
- R18W (p.Arg18Trp), rs1159160299, UniProt VAR 084630, gnomAD rs1159160299, REVEL 0.86, CADD 26.40, Pathogenic, in IMD103
- V19E (p.Val19Glu), ExAC rs773760350, gnomAD rs773760350, REVEL 0.27, CADD 23.10
- T20M (p.Thr20Met), rs763713013, ClinGen CA5333260, cosmic curated COSV53732, ClinVar RCV001350890, REVEL 0.08, CADD 12.00, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- T22P (p.Thr22Pro), Ensembl rs1588726560
- S23* (p.Ser23Ter), rs775267971, ClinGen CA375546475, ClinVar RCV002271345, ExAC rs775267971, AlphaMissense 0.14, MetaLR 0.06, Uncertain significance
- S23L (p.Ser23Leu), rs775267971, ClinGen CA5333258, NCI-TCGA Cosmic COSV5373, cosmic curated COSV53733, REVEL 0.22, AlphaMissense 0.14, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- S23S (p.Ser23Ser), rs891969889, []
- I25M (p.Ile25Met), rs139436668, ClinGen CA375546462, ClinVar RCV002008931, ESP rs139436668, AlphaMissense 0.20, MetaLR 0.15, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- D26N (p.Asp26Asn), cosmic curated COSV53737, ESP rs368845667, ExAC rs368845667, TOPMed rs368845667, REVEL 0.16, CADD 22.50
- P27L (p.Pro27Leu), rs2538671919, ClinGen CA375546449, ClinVar RCV002903980, REVEL 0.47, CADD 26.20, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- R29C (p.Arg29Cys), rs776666302, ClinGen CA5333255, ClinVar RCV002780927, ExAC rs776666302, REVEL 0.38, CADD 27.90, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- R29H (p.Arg29His), rs201587695, ClinGen CA5333253, cosmic curated COSV53731, ClinVar RCV001216268, REVEL 0.25, CADD 25.90, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency; not provided
- R29L (p.Arg29Leu), 1000Genomes rs201587695, ESP rs201587695, ExAC rs201587695, TOPMed rs201587695, REVEL 0.36, CADD 25.60, Uncertain significance
- T31I (p.Thr31Ile), Ensembl rs1833287648, SIFT 0.06
- P32L (p.Pro32Leu), gnomAD rs1247747413, REVEL 0.73, CADD 26.70
- P32S (p.Pro32Ser), ExAC rs778826719, gnomAD rs778826719, REVEL 0.54, CADD 25.80
- Y33* (p.Tyr33Ter), TOPMed rs1833287477, CADD 40.00
- Y33F (p.Tyr33Phe), Ensembl rs2131445607, SIFT 0.02
- L34M (p.Leu34Met), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- R35Q (p.Arg35Gln), rs1454037218, UniProt VAR 084632, TOPMed rs1454037218, gnomAD rs1454037218, REVEL 0.38, CADD 26.80, Pathogenic, in IMD103
- Q36* (p.Gln36Ter), rs768845190, ClinGen CA5333251, ClinVar RCV002816643, ExAC rs768845190, CADD 41.00, Pathogenic
- C37G (p.Cys37Gly), ExAC rs200980160, gnomAD rs200980160
- C37W (p.Cys37Trp), Ensembl rs2131445586, SIFT 0.00
- K38Q (p.Lys38Gln), TOPMed rs903633185, SIFT 0.01
- N41K (p.Asn41Lys), ExAC rs750817144, gnomAD rs750817144, REVEL 0.10, CADD 24.10
- P42L (p.Pro42Leu), rs2538671781, ClinGen CA2739265245, ClinVar RCV003607143, REVEL 0.03, CADD 22.50, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- D43N (p.Asp43Asn), gnomAD rs1359993470, REVEL 0.14, CADD 27.00
- D44E (p.Asp44Glu), TOPMed rs931686923, gnomAD rs931686923, REVEL 0.44, CADD 14.20
- D44N (p.Asp44Asn), Ensembl rs1564370286, REVEL 0.47, CADD 27.20
- E45K (p.Glu45Lys), NCI-TCGA Cosmic COSV5373, cosmic curated COSV53736, Variant assessed as somatic; moderate impact.
- E46K (p.Glu46Lys), gnomAD rs1407323914, REVEL 0.37, CADD 31.00
- V48G (p.Val48Gly), Ensembl rs1588726463, SIFT 0.00
- S50N (p.Ser50Asn), gnomAD rs1414848495, REVEL 0.11, CADD 17.20
- S50R (p.Ser50Arg), ESP rs149255047, ExAC rs149255047, TOPMed rs149255047, gnomAD rs149255047, REVEL 0.21, CADD 19.00, Likely benign
- S50T (p.Ser50Thr), gnomAD rs1414848495, SIFT 0.02
- D51A (p.Asp51Ala), Ensembl rs867997087
- D51E (p.Asp51Glu), TOPMed rs1833285586, gnomAD rs1833285586, REVEL 0.19, CADD 24.80
- D51G (p.Asp51Gly), Ensembl rs867997087, SIFT 0.00
- D51N (p.Asp51Asn), cosmic curated COSV10004, TOPMed rs922901788, gnomAD rs922901788, REVEL 0.23, CADD 26.50
- P52L (p.Pro52Leu), NCI-TCGA Cosmic COSV1000, cosmic curated COSV10004, SIFT 0.01, Variant assessed as somatic; moderate impact.
- P52S (p.Pro52Ser), gnomAD rs1265712771, REVEL 0.34, CADD 24.30
- N53K (p.Asn53Lys), ExAC rs762536086, gnomAD rs762536086, REVEL 0.05, CADD 17.20
- N53S (p.Asn53Ser), rs377708969, ClinGen CA201615741, ClinVar RCV002025599, gnomAD rs377708969, REVEL 0.02, CADD 0.42, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- N53T (p.Asn53Thr), gnomAD rs377708969, SIFT 0.64, Uncertain significance
- V55I (p.Val55Ile), ExAC rs752221728, gnomAD rs752221728, REVEL 0.20, CADD 23.40, Uncertain significance, Inborn genetic diseases
- R57C (p.Arg57Cys), TOPMed rs1040324141, gnomAD rs1040324141, REVEL 0.59, CADD 31.00
- R57G (p.Arg57Gly), TOPMed rs1040324141, gnomAD rs1040324141, REVEL 0.61, CADD 27.80
- R57H (p.Arg57His), rs940550122, ClinGen CA201615723, cosmic curated COSV53733, ClinVar RCV001064701, REVEL 0.56, CADD 28.00, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- K58E (p.Lys58Glu), NCI-TCGA Cosmic COSV5373, cosmic curated COSV53738, Variant assessed as somatic; moderate impact.
- R59Q (p.Arg59Gln), cosmic curated COSV53738, TOPMed rs979849048, gnomAD rs979849048, REVEL 0.25, CADD 29.00
- R59W (p.Arg59Trp), rs907791516, NCI-TCGA Cosmic COSV5373, cosmic curated COSV53732, TOPMed rs907791516, REVEL 0.36, CADD 25.90, Variant assessed as somatic; moderate impact.
- K60I (p.Lys60Ile), NCI-TCGA Cosmic COSV1000, cosmic curated COSV10004, SIFT 0.00, Variant assessed as somatic; moderate impact.
- V61=, NCI-TCGA TCGA novel, Variant assessed as somatic; low impact.
- V61L (p.Val61Leu), ExAC rs765010252, gnomAD rs765010252, REVEL 0.19, CADD 22.80
- V61A (p.Val61Ala), rs779545462, []
- G62R (p.Gly62Arg), gnomAD rs1278536786, REVEL 0.43, CADD 35.00
- V63M (p.Val63Met), ESP rs138379141, gnomAD rs138379141, REVEL 0.10, CADD 15.90
- L65P (p.Leu65Pro), gnomAD rs1276381998, REVEL 0.64, CADD 25.80
- L68M (p.Leu68Met), NCI-TCGA Cosmic COSV5373, cosmic curated COSV53732, REVEL 0.45, CADD 25.10, Variant assessed as somatic; moderate impact.
- Q69* (p.Gln69Ter), rs1310355874, ClinGen CA375546179, ClinVar RCV003607635, gnomAD rs1310355874, CADD 37.00, Pathogenic
- Q69H (p.Gln69His), rs1045323623, TOPMed rs1045323623, gnomAD rs1045323623, REVEL 0.20, CADD 19.00, Variant assessed as somatic; moderate impact.
- R70L (p.Arg70Leu), ESP rs376793464, ExAC rs376793464, TOPMed rs376793464, gnomAD rs376793464, REVEL 0.34, CADD 23.80, Uncertain significance, in IMD103
- R70Q (p.Arg70Gln), rs376793464, ClinGen CA5333214, ClinVar RCV001352219, ESP rs376793464, REVEL 0.29, CADD 23.80, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- R70W (p.Arg70Trp), rs767522068, UniProt VAR 084634, ExAC rs767522068, TOPMed rs767522068, REVEL 0.32, CADD 25.10, Pathogenic, in IMD103
- T71N (p.Thr71Asn), ExAC rs746089018, TOPMed rs746089018, gnomAD rs746089018, REVEL 0.28, CADD 23.00
- T71S (p.Thr71Ser), ExAC rs769905929, TOPMed rs769905929, gnomAD rs769905929, REVEL 0.18, CADD 23.50
- G72C (p.Gly72Cys), rs398122362, ClinGen CA375546167, ClinVar RCV000700097, TOPMed rs398122362, AlphaMissense 0.48, MetaLR 0.33, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- G72D (p.Gly72Asp), cosmic curated COSV53730, Ensembl rs865827438, REVEL 0.71, CADD 24.90, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- G72S (p.Gly72Ser), rs398122362, ClinGen CA145368, ClinVar RCV000074438, UniProt VAR 070828, REVEL 0.73, AlphaMissense 0.48, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- H73P (p.His73Pro), TOPMed rs1383238223, gnomAD rs1383238223, REVEL 0.15, CADD 22.90
- H73Q (p.His73Gln), gnomAD rs1380371712, REVEL 0.11, CADD 22.30
- H73R (p.His73Arg), TOPMed rs1383238223, gnomAD rs1383238223, REVEL 0.06, CADD 16.80
- H73Y (p.His73Tyr), TOPMed rs1449809662, gnomAD rs1449809662, REVEL 0.10, CADD 24.80
- K74R (p.Lys74Arg), gnomAD rs1177629322, REVEL 0.08, CADD 16.90
- G75S (p.Gly75Ser), rs1437385436, ClinGen CA375546148, ClinVar RCV000807082, TOPMed rs1437385436, REVEL 0.65, CADD 26.20, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- Y76C (p.Tyr76Cys), Ensembl rs2131444790, SIFT 0.19
- A78V (p.Ala78Val), cosmic curated COSV53731, gnomAD rs1182277747, REVEL 0.34, CADD 24.80
- L80V (p.Leu80Val), TOPMed rs1833269956
- E81* (p.Glu81Ter), ExAC rs748704811, TOPMed rs748704811, gnomAD rs748704811, CADD 39.00
- E81K (p.Glu81Lys), ExAC rs748704811, TOPMed rs748704811, gnomAD rs748704811, REVEL 0.59, CADD 26.10
- S82N (p.Ser82Asn), ExAC rs778562065, TOPMed rs778562065, gnomAD rs778562065, REVEL 0.50, CADD 24.40
- L83V (p.Leu83Val), TOPMed rs1293607739, gnomAD rs1293607739, REVEL 0.48, CADD 23.10
- E84G (p.Glu84Gly), NCI-TCGA TCGA novel, SIFT 0.04, Variant assessed as somatic; moderate impact.
- L85F (p.Leu85Phe), rs1239721232, ClinGen CA375546039, ClinVar RCV003266785, TOPMed rs1239721232, REVEL 0.22, CADD 22.40, Uncertain significance, Inborn genetic diseases
- Y86C (p.Tyr86Cys), rs1049019466, ClinGen CA201615195, ClinVar RCV001299098, Ensembl rs1049019466, REVEL 0.50, CADD 26.20, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- P88L (p.Pro88Leu), rs141691778, NCI-TCGA Cosmic COSV5373, ESP rs141691778, ExAC rs141691778, REVEL 0.60, CADD 25.40, Variant assessed as somatic; moderate impact.
- Y91* (p.Tyr91Ter), rs766061901, ClinGen CA375545960, ClinVar RCV002834586, CADD 36.00, Pathogenic, in IMD103
- Y91H (p.Tyr91His), rs921151054, ClinGen CA201615185, ClinVar RCV000788931, ClinVar RCV001067651, REVEL 0.78, CADD 26.10, Conflicting interpretations, not provided; Predisposition to invasive fungal disease due to CARD9 deficiency
- K92E (p.Lys92Glu), Ensembl rs1833268870, REVEL 0.08, CADD 23.10
- V94I (p.Val94Ile), ExAC rs755827252, TOPMed rs755827252, gnomAD rs755827252, REVEL 0.13, CADD 13.50
- G96D (p.Gly96Asp), ExAC rs767265193, gnomAD rs767265193, REVEL 0.54, CADD 24.90
- K97N (p.Lys97Asn), rs532497257, ClinGen CA375545885, ClinVar RCV002829337, REVEL 0.12, CADD 23.10, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- K97R (p.Lys97Arg), cosmic curated COSV53732, ExAC rs774343383, TOPMed rs774343383, gnomAD rs774343383, REVEL 0.08, CADD 24.10
- E98G (p.Glu98Gly), gnomAD rs1833268163, REVEL 0.23, CADD 28.60
- E98K (p.Glu98Lys), gnomAD rs1253739630, REVEL 0.21, CADD 25.80
- P99L (p.Pro99Leu), rs200248442, ClinGen CA5333193, ClinVar RCV002642489, ClinVar RCV005535378, REVEL 0.50, CADD 27.00, Uncertain significance, Inborn genetic diseases; Predisposition to invasive fungal disease due to CARD9
- P99R (p.Pro99Arg), 1000Genomes rs200248442, ExAC rs200248442, gnomAD rs200248442, REVEL 0.56, CADD 26.90, Uncertain significance
- P99T (p.Pro99Thr), rs1488546054, ClinGen CA375545870, ClinVar RCV001338491, gnomAD rs1488546054, REVEL 0.61, CADD 25.60, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- A100D (p.Ala100Asp), Ensembl rs867858918, SIFT 0.29
- R101C (p.Arg101Cys), rs398122364, ClinGen CA145375, cosmic curated COSV10513, ClinVar RCV000074441, REVEL 0.75, CADD 26.60, risk factor, Predisposition to invasive fungal disease due to CARD9 deficiency
- R101H (p.Arg101His), rs988002931, ClinGen CA201615119, ClinVar RCV003110399, TOPMed rs988002931, REVEL 0.32, CADD 25.30, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- R101L (p.Arg101Leu), UniProt VAR 084636, REVEL 0.46, CADD 25.20, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- V102A (p.Val102Ala), gnomAD rs1245788237, SIFT 0.17
- V102I (p.Val102Ile), TOPMed rs1490862744, gnomAD rs1490862744, REVEL 0.08, CADD 22.70
- M105T (p.Met105Thr), gnomAD rs1291757290
- M105V (p.Met105Val), rs374308759, ClinGen CA5333189, ClinVar RCV001035608, ESP rs374308759, AlphaMissense 0.06, MetaLR 0.04, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- D108N (p.Asp108Asn), ExAC rs761129740, TOPMed rs761129740, gnomAD rs761129740, REVEL 0.27, CADD 32.00
- D108Y (p.Asp108Tyr), ExAC rs761129740, TOPMed rs761129740, gnomAD rs761129740, REVEL 0.40, CADD 33.00
- A109T (p.Ala109Thr), ExAC rs766469254, TOPMed rs766469254, gnomAD rs766469254, REVEL 0.10, CADD 13.60, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- A109V (p.Ala109Val), rs760681802, ClinGen CA5333156, ClinVar RCV000701249, ClinVar RCV006327127, REVEL 0.14, CADD 18.90, Uncertain significance, Inborn genetic diseases; Predisposition to invasive fungal disease due to CARD9
- G111E (p.Gly111Glu), rs371695061, ClinGen CA201614872, ClinVar RCV001360838, ESP rs371695061, REVEL 0.34, CADD 23.80, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- G111R (p.Gly111Arg), rs769183409, NCI-TCGA Cosmic COSV5373, cosmic curated COSV53731, ExAC rs769183409, REVEL 0.40, CADD 24.50, Variant assessed as somatic; moderate impact.
- E112* (p.Glu112Ter), TOPMed rs1277687271
- E112G (p.Glu112Gly), Ensembl rs1833259560, REVEL 0.22, CADD 27.00
- E112K (p.Glu112Lys), TOPMed rs1277687271
- Q117* (p.Gln117Ter), gnomAD rs1375893670, CADD 38.00
- Q117H (p.Gln117His), ExAC rs775922619, gnomAD rs775922619, REVEL 0.27, CADD 22.70
- L119M (p.Leu119Met), gnomAD rs1402887021, REVEL 0.77, CADD 25.30
- L119P (p.Leu119Pro), rs1171915203, ClinGen CA375545645, ClinVar RCV002865538, gnomAD rs1171915203, REVEL 0.94, CADD 25.70, Uncertain significance, Inborn genetic diseases
- M120I (p.Met120Ile), Ensembl rs1833258944, REVEL 0.38, CADD 24.20
- T121S (p.Thr121Ser), gnomAD rs1434258703, REVEL 0.03, CADD 8.45
- E122D (p.Glu122Asp), gnomAD rs1180760730, REVEL 0.42, CADD 23.60
- V123I (p.Val123Ile), rs780846137, ClinGen CA5333146, ClinVar RCV001222034, ExAC rs780846137, REVEL 0.10, CADD 16.90, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- M124I (p.Met124Ile), rs926038111, ClinGen CA201614831, ClinVar RCV001220036, Ensembl rs926038111, AlphaMissense 0.30, MetaLR 0.12, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- M124T (p.Met124Thr), rs1274878660, ClinGen CA375545612, ClinVar RCV001218958, TOPMed rs1274878660, REVEL 0.08, CADD 8.71, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- M124V (p.Met124Val), rs2131444353, ClinGen CA375545613, ClinVar RCV001863722, Ensembl rs2131444353, AlphaMissense 0.09, MetaLR 0.14, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- Q127* (p.Gln127Ter), ExAC rs770545753, gnomAD rs770545753, CADD 37.00
- V130A (p.Val130Ala), Ensembl rs1833257824, REVEL 0.09, CADD 15.50
- Q131E (p.Gln131Glu), gnomAD rs1833257712, REVEL 0.05, CADD 22.60
- Q131R (p.Gln131Arg), ExAC rs752622733, gnomAD rs752622733, REVEL 0.05, CADD 24.30
- D132H (p.Asp132His), ESP rs367638485, TOPMed rs367638485, gnomAD rs367638485
- D132N (p.Asp132Asn), ESP rs367638485, TOPMed rs367638485, gnomAD rs367638485, REVEL 0.05, CADD 22.90
- L133P (p.Leu133Pro), gnomAD rs1833257523, REVEL 0.23, CADD 25.20
- A135T (p.Ala135Thr), ExAC rs778718632, gnomAD rs778718632, REVEL 0.04, CADD 9.89
- A135V (p.Ala135Val), rs756177404, ClinGen CA5333139, cosmic curated COSV10004, ClinVar RCV002575032, REVEL 0.01, CADD 8.44, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- L137P (p.Leu137Pro), 1000Genomes rs201183869, REVEL 0.31, CADD 24.70
- L137V (p.Leu137Val), TOPMed rs1333436987, gnomAD rs1333436987, REVEL 0.14, CADD 18.90
- S138N (p.Ser138Asn), NCI-TCGA TCGA novel, REVEL 0.03, CADD 10.20, Variant assessed as somatic; moderate impact.
- S138R (p.Ser138Arg), rs2131444271, ClinGen CA375545528, ClinVar RCV001370805, ClinVar RCV004601482, REVEL 0.04, CADD 14.70, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency; Inborn geneti
- S139F (p.Ser139Phe), rs2538669504, ClinGen CA375545515, ClinVar RCV002958908, REVEL 0.05, CADD 23.90, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- D141H (p.Asp141His), ESP rs375341696, ExAC rs375341696, TOPMed rs375341696, gnomAD rs375341696, REVEL 0.05, CADD 22.60, Uncertain significance, Inborn genetic diseases
- D141N (p.Asp141Asn), rs375341696, ClinGen CA5333137, ClinVar RCV001904105, ESP rs375341696, REVEL 0.06, CADD 21.10, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- D142E (p.Asp142Glu), ExAC rs757521454, gnomAD rs757521454, REVEL 0.06, CADD 13.70
- I144F (p.Ile144Phe), rs977007616, ClinGen CA375545484, ClinVar RCV002035954, TOPMed rs977007616, AlphaMissense 0.18, MetaLR 0.08, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- I144V (p.Ile144Val), rs977007616, ClinGen CA201614787, ClinVar RCV004427181, TOPMed rs977007616, REVEL 0.03, AlphaMissense 0.18, Uncertain significance, Inborn genetic diseases
- E146A (p.Glu146Ala), TOPMed rs1833256414, REVEL 0.15, CADD 24.90
- E146G (p.Glu146Gly), TOPMed rs1833256414, REVEL 0.19, CADD 26.30
- E146K (p.Glu146Lys), cosmic curated COSV10459, TOPMed rs1407588129, gnomAD rs1407588129, REVEL 0.08, CADD 22.80, Uncertain significance
- E146Q (p.Glu146Gln), rs1407588129, ClinGen CA375545470, ClinVar RCV001221746, TOPMed rs1407588129, REVEL 0.07, CADD 16.10, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- R148P (p.Arg148Pro), ExAC rs757627986, TOPMed rs757627986, gnomAD rs757627986, REVEL 0.14, CADD 23.90, Uncertain significance
- R148Q (p.Arg148Gln), rs757627986, ClinGen CA5333134, ClinVar RCV000823901, ExAC rs757627986, REVEL 0.02, CADD 18.40, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- R148W (p.Arg148Trp), rs149206311, ClinGen CA5333135, ClinVar RCV001910889, ClinVar RCV002553593, REVEL 0.03, CADD 17.90, Uncertain significance, Inborn genetic diseases; not provided; Predisposition to invasive fungal disease
- V149L (p.Val149Leu), gnomAD rs1187475967, REVEL 0.04, CADD 1.73
- K150* (p.Lys150Ter), ExAC rs776001547, gnomAD rs776001547
- D151N (p.Asp151Asn), rs760135155, ClinGen CA5333130, ClinVar RCV002908051, ExAC rs760135155, REVEL 0.08, CADD 19.20, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- S152N (p.Ser152Asn), rs539919395, ClinGen CA201614758, ClinVar RCV000809823, Ensembl rs539919395, AlphaMissense 0.13, MetaLR 0.06, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- R155C (p.Arg155Cys), rs199947855, ClinGen CA5333129, ClinVar RCV000545325, ExAC rs199947855, REVEL 0.12, CADD 24.20, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
- R155H (p.Arg155His), rs145198648, ClinGen CA5333128, ClinVar RCV001952047, 1000Genomes rs145198648, REVEL 0.09, CADD 18.80, Uncertain significance, Predisposition to invasive fungal disease due to CARD9 deficiency
Public CARD9 analysis runs
- CARD9 analysis run — CARD9 (953 variants) — completed 2026-08-19