PTPN11 (Q06124) variants and mutations

PTPN11 (also known as Q06124) is a human protein-coding gene encoding a tyrosine-protein phosphatase non-receptor type 11 protein. Its SHP2 phosphatase activity promotes RAS-MAPK signaling downstream of many receptor tyrosine kinases and cytokine receptors. Germline dysregulating variants cause Noonan-spectrum disorders, while somatic activating variants drive juvenile myelomonocytic leukemia and other cancers. This analysis covers 1,792 PTPN11 variants and mutations. Of these, 38% have computational variant effect predictions. Disease context includes Noonan syndrome, Noonan syndrome with multiple lentigines, and juvenile myelomonocytic leukemia. Example PTPN11 variants include T2A, T2I, and T2K.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, ClinGen, MaveDB, LitVar.

Notable PTPN11 variants

Examples include T2A, T2I, T2K, T2T, S3L, S3W, S3*, S3S. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.