TERT (Telomerase reverse transcriptase) variants and mutations

TERT (also known as Telomerase reverse transcriptase) is a human protein-coding gene encoding a telomerase reverse transcriptase protein. It extends telomeric DNA using an internal RNA template and helps counter progressive chromosome-end shortening in stem and proliferative cells. Loss-of-function variants cause telomere-biology disorders, while promoter activation and increased activity support unlimited proliferation in many cancers. This analysis covers 2,142 TERT variants and mutations. Of these, 85% have computational variant effect predictions. Disease context includes dyskeratosis congenita, autosomal dominant 2, pulmonary fibrosis and/or bone marrow failure, Telomere-related, 1, and dyskeratosis congenita. Example TERT variants include P2A, P2L, and P2R.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, ClinGen, MaveDB, LitVar.

Notable TERT variants

Examples include P2A, P2L, P2R, P2T, R3C, R3H, R3P, A4P. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.