JAK1 (Tyrosine-protein kinase JAK1) variants and mutations

JAK1 (also known as Tyrosine-protein kinase JAK1) is a human protein-coding gene encoding a tyrosine-protein kinase protein. It couples many cytokine receptors to STAT transcription factors and is essential for interferon, interleukin, and growth-factor signaling. Loss-of-function can cause immunodeficiency, whereas activating alterations contribute to inflammatory disease and some malignancies. This analysis covers 2,282 JAK1 variants and mutations. Of these, 40% have computational variant effect predictions. Disease context includes rheumatoid arthritis, autoinflammation, immune dysregulation, and eosinophilia, and atopic eczema. Example JAK1 variants include M1T, Q2*, and L4V.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, MaveDB, LitVar.

Notable JAK1 variants

Examples include M1T, Q2*, L4V, N5S, I6T, K7R, E8*, E8G. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.