V161G (p.Val161Gly) variant of SETX (Helicase senataxin)

V161G (p.Val161Gly) in SETX (Helicase senataxin) is a missense change. Clinical records from ClinVar, EBI, and UniProt describe it as likely pathogenic in the context of Spastic ataxia. The available variant effect predictions contribute to a CATVariant prioritization score of 0.66 / 1. The record also includes population frequency data and structural context.

V161G (p.Val161Gly) variant details