MYL3 (Myosin light chain 3) variants and mutations

MYL3 (also known as Myosin light chain 3) is a human protein-coding gene encoding a myosin light chain 3 protein. It provides an essential light chain for cardiac ventricular myosin and modulates actin-myosin force generation within the sarcomere. Pathogenic variants can cause hypertrophic or restrictive cardiomyopathy and disturb ventricular contractile mechanics. This analysis covers 502 MYL3 variants and mutations. Of these, 80% have computational variant effect predictions. Disease context includes hypertrophic cardiomyopathy, Rare familial disorder with hypertrophic cardiomyopathy, and Abnormality of the cardiovascular system. Example MYL3 variants include M1K, M1V, and A2D.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, ClinGen, MaveDB, LitVar.

Notable MYL3 variants

Examples include M1K, M1V, A2D, A2P, A2S, A2A, A2T, P3H. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.