GATA6 (Transcription factor GATA-6) variants and mutations

GATA6 (also known as Transcription factor GATA-6) is a human protein-coding gene encoding a transcription factor GATA-6 protein. It regulates developmental programs in the pancreas, heart, gut, and other endoderm-derived tissues. Haploinsufficiency is a major cause of pancreatic agenesis and neonatal diabetes and can also produce congenital heart disease and other developmental abnormalities. This analysis covers 1,385 GATA6 variants and mutations. Of these, 85% have computational variant effect predictions. Disease context includes pancreatic hypoplasia-diabetes-congenital heart disease syndrome, Pancreatic hypoplasia - diabetes - congenital heart disease, and atrioventricular septal defect 5. Example GATA6 variants include M1?, M1K, and A2V.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, AlphaFold DB, gnomAD constraint, Open Targets, ClinGen, MaveDB, LitVar.

Notable GATA6 variants

Examples include M1?, M1K, A2V, A2T, A2S, A2A, p.Leu3 Thr4delinsSer, L3M. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.