F7 (Coagulation factor VII) variants and mutations
F7 (also known as Coagulation factor VII) is a human protein-coding gene encoding a coagulation factor VII protein. It binds tissue factor at sites of vascular injury and initiates coagulation by activating factors IX and X. Biallelic deficiency causes a rare bleeding disorder with highly variable severity, while recombinant activated factor VII is used therapeutically in selected bleeding conditions. This analysis covers 522 F7 variants and mutations. Of these, 78% have computational variant effect predictions. Disease context includes factor VII deficiency, congenital factor VII deficiency, and hemophilia B. Example F7 variants include M1T, V2F, and V2I.
Variant analysis overview
- Gene: F7
- Protein: Coagulation factor VII
- UniProt accession: P08709
- Organism: Homo sapiens
- Variants analyzed: 522
- Variant scope: all variants
- Completed: 2026-08-21
Variant and mutation evidence
- Variant composition: 224 unspecified-consequence records; 204 missense variants; 55 synonymous variants; 14 stop-gained variants; 12 frameshift variants; 1 in-frame insertions; 4 splice-region variants; 2 in-frame deletions; 5 substitution
- Prediction scores: 407 variants have prediction scores (78% of the analyzed set).
Clinical, disease, and population context
- Disease context: 25 disease associations are represented. Top associations: factor VII deficiency, congenital factor VII deficiency, hemophilia B, hemophilia A, blood coagulation disease, Abnormality of coagulation, Abnormal bleeding, Glanzmann thrombasthenia, coagulation protein disease, intracerebral hemorrhage, open-angle glaucoma, glaucoma.
Protein structure and variant hotspots
- Protein features: 4 domains; 1 binding sites; 16 post-translational modification sites.
- Structural context: 267 variants have structural context.
- PTM context: 23 variants overlap post-translational modification sites.
Data sources
Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, ClinGen, MaveDB, LitVar.
Notable F7 variants
Examples include M1T, V2F, V2I, V2V, S3P, S3Y, S3S, Q4K. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.
- M1T (p.Met1Thr), rs766294997, ClinGen CA7059799, ClinVar RCV003482110, MetaLR 0.63, MetaSVM -0.11, Pathogenic
- V2F (p.Val2Phe), gnomAD 13-113105845-G-T, REVEL 0.17, MetaLR 0.58
- V2I (p.Val2Ile), rs751247590, gnomAD 13-113105845-G-A, REVEL 0.07, MetaLR 0.54
- V2V (p.Val2Val), rs2035942635, gnomAD 13-113105847-C-A, CADD 0.42
- S3P (p.Ser3Pro), gnomAD 13-113105848-T-C, REVEL 0.16, MetaLR 0.51
- S3Y (p.Ser3Tyr), gnomAD 13-113105849-C-A, REVEL 0.22, MetaLR 0.69
- S3S (p.Ser3Ser), gnomAD 13-113105850-C-A, CADD 3.00
- Q4K (p.Gln4Lys), gnomAD 13-113105851-C-A, REVEL 0.13, MetaLR 0.49
- Q4* (p.Gln4Ter), gnomAD 13-113105851-C-T, CADD 33.00
- Q4P (p.Gln4Pro), gnomAD 13-113105852-A-C, REVEL 0.37, MetaLR 0.58
- Q4R (p.Gln4Arg), gnomAD 13-113105852-A-G, REVEL 0.24, MetaLR 0.45
- Q4L (p.Gln4Leu), gnomAD 13-113105852-A-T, REVEL 0.24, MetaLR 0.49
- Q4Q (p.Gln4Gln), gnomAD 13-113105853-G-A, CADD 0.81
- Q4H (p.Gln4His), gnomAD 13-113105853-G-T, REVEL 0.27, MetaLR 0.56
- A5T (p.Ala5Thr), gnomAD 13-113105854-G-A, REVEL 0.12, MetaLR 0.54
- A5S (p.Ala5Ser), gnomAD 13-113105854-G-T, REVEL 0.12, MetaLR 0.49
- A5V (p.Ala5Val), rs755010915, gnomAD 13-113105855-C-T, REVEL 0.11, MetaLR 0.58
- A5D (p.Ala5Asp), rs755010915, gnomAD 13-113105855-C-A, REVEL 0.15, MetaLR 0.64
- A5A (p.Ala5Ala), rs150465470, gnomAD 13-113105856-C-T, CADD 2.04
- L6Q (p.Leu6Gln), gnomAD 13-113105854-GCC-, CADD 13.90
- L6F (p.Leu6Phe), gnomAD 13-113105857-C-T, REVEL 0.13, MetaLR 0.44
- L6I (p.Leu6Ile), gnomAD 13-113105857-C-A, REVEL 0.17, MetaLR 0.47
- L6H (p.Leu6His), gnomAD 13-113105858-T-A, REVEL 0.24, MetaLR 0.50
- L6P (p.Leu6Pro), gnomAD 13-113105858-T-C, REVEL 0.22, MetaLR 0.47
- L6L (p.Leu6Leu), gnomAD 13-113105859-C-T, CADD 2.31
- R7W (p.Arg7Trp), gnomAD 13-113105860-A-T, REVEL 0.29, MetaLR 0.60
- R7G (p.Arg7Gly), gnomAD 13-113105860-A-G, REVEL 0.27, MetaLR 0.52
- R7M (p.Arg7Met), gnomAD 13-113105861-G-T, REVEL 0.22, MetaLR 0.56
- R7T (p.Arg7Thr), rs1301327017, gnomAD 13-113105861-G-C, REVEL 0.18, MetaLR 0.52
- R7S (p.Arg7Ser), gnomAD 13-113105862-G-C, REVEL 0.26, MetaLR 0.55
- R7R (p.Arg7Arg), gnomAD 13-113105862-G-A, CADD 4.61
- L8I (p.Leu8Ile), gnomAD 13-113105863-C-A, REVEL 0.17, MetaLR 0.59
- L8P (p.Leu8Pro), gnomAD 13-113105864-T-C, REVEL 0.25, MetaLR 0.60
- L8R (p.Leu8Arg), gnomAD 13-113105864-T-G, REVEL 0.34, MetaLR 0.72
- L8L (p.Leu8Leu), gnomAD 13-113105865-C-T, CADD 3.01
- L9I (p.Leu9Ile), NCI-TCGA TCGA novel, TOPMed rs963545410, REVEL 0.26, MetaLR 0.67, Variant assessed as somatic; moderate impact.
- p.Leu9dup, gnomAD 13-113105862-G-GC, CADD 8.64
- L9F (p.Leu9Phe), rs963545410, gnomAD 13-113105866-C-T, REVEL 0.21, MetaLR 0.54
- L9P (p.Leu9Pro), rs1398906712, gnomAD 13-113105867-T-C, REVEL 0.53, MetaLR 0.81
- L9L (p.Leu9Leu), rs1391817628, gnomAD 13-113105868-C-A, CADD 7.20
- C10R (p.Cys10Arg), rs756153946, gnomAD 13-113105869-T-C, REVEL 0.35, MetaLR 0.68
- C10Y (p.Cys10Tyr), rs777789240, gnomAD 13-113105870-G-A, REVEL 0.32, MetaLR 0.72
- C10F (p.Cys10Phe), gnomAD 13-113105870-G-T, REVEL 0.29, MetaLR 0.66
- C10* (p.Cys10Ter), rs2142195925, gnomAD 13-113105871-C-A, CADD 36.00
- C10C (p.Cys10Cys), gnomAD 13-113105871-C-T, CADD 12.00
- L11F (p.Leu11Phe), gnomAD 13-113105872-C-T, REVEL 0.10, MetaLR 0.43
- L11I (p.Leu11Ile), gnomAD 13-113105872-C-A, REVEL 0.10, MetaLR 0.47
- L11L (p.Leu11Leu), gnomAD 13-113105874-T-C, CADD 7.96
- L12M (p.Leu12Met), gnomAD 13-113105875-C-A, REVEL 0.20, MetaLR 0.64
- L12L (p.Leu12Leu), gnomAD 13-113105875-C-T, CADD 12.80
- L13P (p.Leu13Pro), rs387906507, ClinGen CA121846, ClinVar RCV000012856, UniProt VAR 014391, REVEL 0.54, MetaLR 0.57, Pathogenic, in FA7D
- L13I (p.Leu13Ile), gnomAD 13-113105878-C-A, REVEL 0.19, MetaLR 0.56
- L13F (p.Leu13Phe), gnomAD 13-113105878-C-T, REVEL 0.11, MetaLR 0.48
- L13H (p.Leu13His), rs387906507, gnomAD 13-113105879-T-A, REVEL 0.38, MetaLR 0.71
- L13L (p.Leu13Leu), gnomAD 13-113105880-T-C, CADD 5.92
- G14W (p.Gly14Trp), gnomAD 13-113105881-G-T, REVEL 0.29, MetaLR 0.60
- G14V (p.Gly14Val), gnomAD 13-113105882-G-T, REVEL 0.28, MetaLR 0.57
- G14E (p.Gly14Glu), gnomAD 13-113105882-G-A, REVEL 0.27, MetaLR 0.59
- G14G (p.Gly14Gly), rs2035943310, gnomAD 13-113105883-G-T, CADD 7.24
- L15I (p.Leu15Ile), gnomAD 13-113105884-C-A, REVEL 0.15, MetaLR 0.51
- L15F (p.Leu15Phe), gnomAD 13-113105884-C-T, REVEL 0.07, MetaLR 0.63
- L15P (p.Leu15Pro), gnomAD 13-113105885-T-C, REVEL 0.48, MetaLR 0.64
- L15L (p.Leu15Leu), rs2035943364, gnomAD 13-113105886-T-C, CADD 7.08
- Q16* (p.Gln16Ter), gnomAD 13-113105887-C-T, CADD 38.00
- Q16K (p.Gln16Lys), gnomAD 13-113105887-C-A, REVEL 0.15, MetaLR 0.53
- Q16P (p.Gln16Pro), rs1303999134, gnomAD 13-113105888-A-C, REVEL 0.23, MetaLR 0.53
- Q16R (p.Gln16Arg), gnomAD 13-113105888-A-G, REVEL 0.14, MetaLR 0.46
- Q16H (p.Gln16His), gnomAD 13-113105889-G-T, REVEL 0.21, MetaLR 0.55
- Q16Q (p.Gln16Gln), gnomAD 13-113105889-G-A, CADD 7.13
- Q16L (p.Gln16Leu), rs1191650983, gnomAD 13-113110702-A-T, REVEL 0.24, MetaLR 0.73
- G17S (p.Gly17Ser), gnomAD 13-113105890-G-A, REVEL 0.28, MetaLR 0.50
- G17C (p.Gly17Cys), gnomAD 13-113105890-G-T, REVEL 0.27, MetaLR 0.63
- G17R (p.Gly17Arg), gnomAD 13-113105890-G-C, REVEL 0.34, MetaLR 0.52
- G17D (p.Gly17Asp), gnomAD 13-113105891-G-A, REVEL 0.33, MetaLR 0.60
- G17V (p.Gly17Val), rs1231244636, gnomAD 13-113105891-G-T, REVEL 0.23, MetaLR 0.55
- G17G (p.Gly17Gly), gnomAD 13-113105892-C-T, CADD 4.22
- C18Y (p.Cys18Tyr), rs370843454, gnomAD 13-113105894-G-A, REVEL 0.21, MetaLR 0.50
- C18F (p.Cys18Phe), gnomAD 13-113105894-G-T, REVEL 0.17, MetaLR 0.50
- C18C (p.Cys18Cys), rs771079279, gnomAD 13-113105895-C-T, CADD 4.82
- L19V (p.Leu19Val), gnomAD 13-113105896-C-G, REVEL 0.25, MetaLR 0.66
- L19L (p.Leu19Leu), gnomAD 13-113105896-C-T, CADD 9.88
- L19M (p.Leu19Met), gnomAD 13-113105896-C-A, REVEL 0.23, MetaLR 0.78
- L19P (p.Leu19Pro), rs779250171, gnomAD 13-113105897-T-C, REVEL 0.59, MetaLR 0.69
- A20S (p.Ala20Ser), gnomAD 13-113105899-G-T, REVEL 0.15, MetaLR 0.49
- A20T (p.Ala20Thr), gnomAD 13-113105899-G-A, REVEL 0.09, MetaLR 0.60
- A20P (p.Ala20Pro), gnomAD 13-113105899-G-C, REVEL 0.19, MetaLR 0.58
- A20D (p.Ala20Asp), gnomAD 13-113105900-C-A, REVEL 0.24, MetaLR 0.68
- A20A (p.Ala20Ala), rs746210982, gnomAD 13-113105901-T-C, CADD 9.16
- A21T (p.Ala21Thr), rs1237989279, gnomAD 13-113105902-G-A, REVEL 0.08, MetaLR 0.47
- A21S (p.Ala21Ser), gnomAD 13-113105902-G-T, REVEL 0.07, MetaLR 0.41
- A21E (p.Ala21Glu), gnomAD 13-113105903-C-A, REVEL 0.25, MetaLR 0.75
- A21V (p.Ala21Val), gnomAD 13-113105903-C-T, REVEL 0.18, MetaLR 0.62
- A21A (p.Ala21Ala), gnomAD 13-113105904-A-G, CADD 23.10
- G22D (p.Gly22Asp), rs747488180, gnomAD 13-113106845-G-A, CADD 17.70, SIFT 0.23
- G22G (p.Gly22Gly), gnomAD 13-113106846-C-A, CADD 2.38
- G23R (p.Gly23Arg), rs138470706, gnomAD 13-113106847-G-A, CADD 14.10, SIFT 0.10
- G23E (p.Gly23Glu), rs1235588257, gnomAD 13-113106848-G-A, CADD 10.30, SIFT 0.11
- G23G (p.Gly23Gly), rs770757843, gnomAD 13-113106849-G-A, CADD 2.92
- V24F (p.Val24Phe), gnomAD 13-113105905-G-T, REVEL 0.63, MetaLR 0.71
- V24I (p.Val24Ile), rs376168927, gnomAD 13-113105905-G-A, REVEL 0.28, MetaLR 0.51
- V24S (p.Val24Ser), rs1566904599, gnomAD 13-113106846-CG-C, CADD 15.00
- V24A (p.Val24Ala), gnomAD 13-113106851-T-C, CADD 2.46, SIFT 0.73
- V24V (p.Val24Val), gnomAD 13-113106852-C-G, CADD 2.41
- V24L (p.Val24Leu), gnomAD 13-113110695-G-C, REVEL 0.23, MetaLR 0.21
- A25P (p.Ala25Pro), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- A25T (p.Ala25Thr), gnomAD 13-113106853-G-A, CADD 3.73, SIFT 0.45
- A25S (p.Ala25Ser), gnomAD 13-113106853-G-T, CADD 1.86, SIFT 0.60
- A27T (p.Ala27Thr), rs1262951606, gnomAD 13-113106859-G-A, CADD 6.21, SIFT 0.44
- A27P (p.Ala27Pro), rs1262951606, gnomAD 13-113106859-G-C, CADD 12.50, SIFT 0.35
- A27D (p.Ala27Asp), gnomAD 13-113106860-C-A, CADD 4.31, SIFT 0.11
- A27A (p.Ala27Ala), gnomAD 13-113106861-C-T, CADD 2.39
- A27S (p.Ala27Ser), gnomAD 13-113110710-G-T, REVEL 0.55, MetaLR 0.79
- A27V (p.Ala27Val), gnomAD 13-113110711-C-T, REVEL 0.72, MetaLR 0.86
- S28P (p.Ser28Pro), gnomAD 13-113106862-T-C, CADD 8.76, SIFT 0.26
- S28* (p.Ser28Ter), gnomAD 13-113106863-C-A, CADD 32.00
- S28L (p.Ser28Leu), gnomAD 13-113106863-C-T, CADD 8.89, SIFT 0.18
- S28S (p.Ser28Ser), gnomAD 13-113106864-A-T, CADD 2.31
- G29R (p.Gly29Arg), rs371824980, gnomAD 13-113106865-G-A, CADD 13.20, SIFT 0.89
- G29V (p.Gly29Val), gnomAD 13-113106866-G-T, CADD 10.00, SIFT 0.21
- G29A (p.Gly29Ala), gnomAD 13-113106866-G-C, CADD 0.84, SIFT 0.73
- G29G (p.Gly29Gly), gnomAD 13-113106867-A-G, CADD 10.10
- G30R (p.Gly30Arg), rs775296543, NCI-TCGA Cosmic COSV6064, ExAC rs775296543, gnomAD rs775296543, CADD 4.60, SIFT 0.19, Variant assessed as somatic; moderate impact.
- G30E (p.Gly30Glu), gnomAD 13-113106867-AG-A, CADD 14.70
- G30G (p.Gly30Gly), gnomAD 13-113106870-A-G, CADD 10.60
- G30S (p.Gly30Ser), rs1330001431, gnomAD 13-113110716-G-A, REVEL 0.14, MetaLR 0.35
- G30C (p.Gly30Cys), rs1330001431, gnomAD 13-113110716-G-T, REVEL 0.34, MetaLR 0.64
- G30D (p.Gly30Asp), rs1440487911, gnomAD 13-113110717-G-A, REVEL 0.18, MetaLR 0.44
- G30V (p.Gly30Val), gnomAD 13-113110717-G-T, REVEL 0.20, MetaLR 0.48
- E31K (p.Glu31Lys), rs868540201, gnomAD 13-113106871-G-A, CADD 4.28, SIFT 1.00
- E31D (p.Glu31Asp), rs1458165308, gnomAD 13-113106873-A-C, CADD 0.61, SIFT 0.60
- E31* (p.Glu31Ter), gnomAD 13-113110704-G-T, CADD 41.00, SIFT 0.36
- E31A (p.Glu31Ala), gnomAD 13-113110705-A-C, REVEL 0.31, MetaLR 0.70
- E31E (p.Glu31Glu), rs1238005931, gnomAD 13-113110706-G-A, CADD 9.12, SIFT 0.25
- T32A (p.Thr32Ala), rs2036074155, gnomAD 13-113110698-A-G, REVEL 0.10, MetaLR 0.46
- R33W (p.Arg33Trp), rs764010176, gnomAD 13-113106877-C-T, CADD 10.50, SIFT 0.10
- R33L (p.Arg33Leu), rs753973045, gnomAD 13-113106878-G-T, CADD 0.45, SIFT 1.00
- R33P (p.Arg33Pro), rs753973045, gnomAD 13-113106878-G-C, CADD 0.95, SIFT 0.25
- R33Q (p.Arg33Gln), rs753973045, gnomAD 13-113106878-G-A, CADD 0.21, SIFT 0.42
- R33R (p.Arg33Arg), rs1421774369, gnomAD 13-113106879-G-A, CADD 3.72
- p.Arg36 Phe42delinsLeu, gnomAD 13-113110731-CGCC, CADD 20.40
- D34T (p.Asp34Thr), NCI-TCGA Cosmic COSV6064, Variant assessed as somatic; high impact.
- D34N (p.Asp34Asn), rs1161208094, gnomAD 13-113106880-G-A, CADD 5.93, SIFT 0.48
- D34D (p.Asp34Asp), gnomAD 13-113106882-C-T, CADD 1.21
- M35V (p.Met35Val), gnomAD 13-113106883-A-G, CADD 0.00, SIFT 0.51
- M35I (p.Met35Ile), rs558158814, gnomAD 13-113106885-G-T, CADD 1.98, SIFT 0.50
- P36S (p.Pro36Ser), gnomAD 13-113106886-C-T, CADD 1.52, SIFT 0.51
- P36Q (p.Pro36Gln), rs765322703, gnomAD 13-113106887-C-A, CADD 3.72, SIFT 0.36
- P36L (p.Pro36Leu), rs765322703, gnomAD 13-113106887-C-T, CADD 3.05, SIFT 0.79
- P36P (p.Pro36Pro), rs3093238, gnomAD 13-113106888-G-A, CADD 3.36
- p.Trp37 Pro39del, rs1046118629, gnomAD 13-113106884-TGCC, CADD 6.52
- W37S (p.Trp37Ser), rs2035971492, gnomAD 13-113106890-G-C, CADD 9.71, SIFT 0.23
- W37* (p.Trp37Ter), gnomAD 13-113106890-G-A, CADD 33.00
- W37L (p.Trp37Leu), gnomAD 13-113106890-G-T, CADD 3.25, SIFT 0.37
- K38T (p.Lys38Thr), rs1415055510, gnomAD 13-113106893-A-C, CADD 2.63, SIFT 0.42
- K38K (p.Lys38Lys), gnomAD 13-113106894-G-A, CADD 3.00
- K38E (p.Lys38Glu), gnomAD 13-113110791-A-G, REVEL 0.36, CADD 16.80
- K38R (p.Lys38Arg), gnomAD 13-113110792-A-G, REVEL 0.38, CADD 11.00
- K38N (p.Lys38Asn), gnomAD 13-113110793-G-T, REVEL 0.37, CADD 18.10
- P39S (p.Pro39Ser), gnomAD 13-113106895-C-T, CADD 12.00, SIFT 0.84
- P39R (p.Pro39Arg), gnomAD 13-113106896-C-G, CADD 12.10, SIFT 0.58
- P39L (p.Pro39Leu), rs758592235, gnomAD 13-113106896-C-T, CADD 11.70, SIFT 0.47
- P39P (p.Pro39Pro), gnomAD 13-113106897-G-T, CADD 1.42
- G40W (p.Gly40Trp), gnomAD 13-113106898-G-T, CADD 14.80, SIFT 0.16
- G40V (p.Gly40Val), gnomAD 13-113106899-G-T, CADD 11.60, SIFT 0.24
- G40G (p.Gly40Gly), rs1226891250, gnomAD 13-113106900-G-T, CADD 1.67
- P41A (p.Pro41Ala), gnomAD 13-113106894-G-GC, CADD 19.60
- P41L (p.Pro41Leu), gnomAD 13-113106896-CG-C, CADD 3.41
- P41T (p.Pro41Thr), gnomAD 13-113106901-C-A, CADD 1.65, SIFT 0.96
- P41H (p.Pro41His), gnomAD 13-113106902-C-A, CADD 1.58, SIFT 0.14
- P41P (p.Pro41Pro), rs977782454, gnomAD 13-113106903-T-C, CADD 4.85
- P41S (p.Pro41Ser), rs373376565, gnomAD 13-113110767-C-T, REVEL 0.26, CADD 1.39
- P41Q (p.Pro41Gln), rs748949222, gnomAD 13-113110768-C-A, REVEL 0.26, CADD 11.70
- H42N (p.His42Asn), gnomAD 13-113106904-C-A, CADD 1.79, SIFT 0.35
- H42R (p.His42Arg), rs2035971875, gnomAD 13-113106905-A-G, CADD 1.17, SIFT 0.38
- H42Q (p.His42Gln), rs747374204, gnomAD 13-113106906-C-G, CADD 0.01, SIFT 0.34
- H42T (p.His42Thr), gnomAD 13-113110710-GC-G, CADD 26.00
- H42Y (p.His42Tyr), rs376971927, gnomAD 13-113110713-C-T, REVEL 0.26, MetaLR 0.74
- H42P (p.His42Pro), rs1446422994, gnomAD 13-113110714-A-C, REVEL 0.27, MetaLR 0.65
- H42H (p.His42His), rs2036074535, gnomAD 13-113110715-C-T, CADD 4.94, SIFT 0.11
- R43I (p.Arg43Ile), gnomAD 13-113106908-G-T, CADD 13.80, SIFT 0.08
Public F7 analysis runs
- F7 analysis run — F7 (522 variants) — completed 2026-08-21