ETV5 (ETS translocation variant 5) variants and mutations
ETV5 (also known as ETS translocation variant 5) is a human protein-coding gene encoding an ETS translocation variant 5 protein. It regulates growth-factor-responsive transcription during development and contributes to germ-cell, neural, and epithelial differentiation. Dysregulated expression can promote oncogenic growth and invasion, although recurrent pathogenic germline associations are less established. This analysis covers 816 ETV5 variants and mutations. Of these, 64% have computational variant effect predictions. Disease context includes Abnormality of the skeletal system, obesity disorder, and obstructive sleep apnea syndrome. Example ETV5 variants include M1?, D2I, and G3E.
Variant analysis overview
- Gene: ETV5
- Protein: ETS translocation variant 5
- UniProt accession: P41161
- Organism: Homo sapiens
- Variants analyzed: 816
- Variant scope: all variants
- Completed: 2026-08-20
Variant and mutation evidence
- Variant composition: 643 unspecified-consequence records; 64 missense variants; 97 synonymous variants; 3 in-frame deletions; 5 frameshift variants; 2 splice-region variants; 1 stop-gained variants; 1 in-frame insertions
- Prediction scores: 526 variants have prediction scores (64% of the analyzed set).
Clinical, disease, and population context
- Disease context: 25 disease associations are represented. Top associations: Abnormality of the skeletal system, obesity disorder, obstructive sleep apnea syndrome, diabetes mellitus, overnutrition, sleep apnea syndrome, morbid obesity, smoking behavior, Merkel cell skin cancer, colorectal adenocarcinoma, gastric carcinoma, skin squamous cell carcinoma.
Protein structure and variant hotspots
- Protein features: 1 post-translational modification sites.
- PTM context: 1 variants overlap post-translational modification sites.
Data sources
Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, MaveDB, LitVar.
Notable ETV5 variants
Examples include M1?, D2I, G3E, G3R, G3W, F4I, F4S, D6H. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.
- M1?, cosmic curated COSV10011, NCI-TCGA Cosmic COSV1001, Variant assessed as somatic; high impact.
- D2I (p.Asp2Ile), NCI-TCGA TCGA novel, Variant assessed as somatic; high impact.
- G3E (p.Gly3Glu), NCI-TCGA Cosmic COSV6050, cosmic curated COSV60503, Variant assessed as somatic; moderate impact.
- G3R (p.Gly3Arg), ExAC rs771889712, TOPMed rs771889712, gnomAD rs771889712, REVEL 0.64, CADD 24.50
- G3W (p.Gly3Trp), cosmic curated COSV10011
- F4I (p.Phe4Ile), 1000Genomes rs138565774, ESP rs138565774, ExAC rs138565774, TOPMed rs138565774, REVEL 0.70, CADD 28.10
- F4S (p.Phe4Ser), ExAC rs774084292, gnomAD rs774084292
- D6H (p.Asp6His), NCI-TCGA Cosmic COSV6050, cosmic curated COSV60507, Variant assessed as somatic; moderate impact.
- D6N (p.Asp6Asn), cosmic curated COSV60506, TOPMed rs1410515294
- Q8R (p.Gln8Arg), cosmic curated COSV60501
- P10S (p.Pro10Ser), cosmic curated COSV10511, REVEL 0.77, CADD 28.10
- F11L (p.Phe11Leu), ExAC rs770722736, gnomAD rs770722736
- M12I (p.Met12Ile), rs2473962227, ClinGen CA355845539, ClinVar RCV004107453, NCI-TCGA TCGA novel, REVEL 0.13, CADD 23.00, Uncertain significance, not specified
- M12V (p.Met12Val), cosmic curated COSV60504, Ensembl rs1714574501
- M12Y (p.Met12Tyr), NCI-TCGA TCGA novel, Variant assessed as somatic; high impact.
- P14S (p.Pro14Ser), cosmic curated COSV10644, ExAC rs748760207, TOPMed rs748760207
- G15V (p.Gly15Val), ExAC rs777457522, TOPMed rs777457522, gnomAD rs777457522, REVEL 0.18, CADD 23.20, Uncertain significance, not specified
- G15W (p.Gly15Trp), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- K16N (p.Lys16Asn), ExAC rs767365092, TOPMed rs767365092, gnomAD rs767365092, REVEL 0.09, CADD 23.40
- S17F (p.Ser17Phe), TOPMed rs990808893, gnomAD rs990808893, REVEL 0.27, CADD 28.00
- S17P (p.Ser17Pro), TOPMed rs1350949096, gnomAD rs1350949096, REVEL 0.08, CADD 24.40
- R18G (p.Arg18Gly), Ensembl rs1189324290
- R18P (p.Arg18Pro), 1000Genomes rs547190842, ExAC rs547190842, TOPMed rs547190842, gnomAD rs547190842, REVEL 0.19, CADD 20.50
- R18Q (p.Arg18Gln), cosmic curated COSV60500, 1000Genomes rs547190842, ExAC rs547190842, TOPMed rs547190842, REVEL 0.05, CADD 18.80, Uncertain significance, not specified
- S19A (p.Ser19Ala), gnomAD rs1714570486, REVEL 0.02, CADD 16.70
- E21* (p.Glu21Ter), NCI-TCGA Cosmic COSV1001, cosmic curated COSV10011, Variant assessed as somatic; high impact.
- E21D (p.Glu21Asp), ExAC rs770669598, TOPMed rs770669598, gnomAD rs770669598, REVEL 0.02, CADD 15.90
- R25L (p.Arg25Leu), cosmic curated COSV60501, REVEL 0.42, CADD 28.30
- R25Q (p.Arg25Gln), ExAC rs763263094, TOPMed rs763263094, gnomAD rs763263094, REVEL 0.29, CADD 29.10, Uncertain significance, not specified
- R25W (p.Arg25Trp), rs112315086, ClinGen CA2742756, cosmic curated COSV60500, ClinVar RCV004166188, REVEL 0.34, CADD 32.00, Uncertain significance, not specified
- P26S (p.Pro26Ser), Ensembl rs1714570096
- I28L (p.Ile28Leu), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- R30G (p.Arg30Gly), gnomAD rs1714569980, REVEL 0.39, CADD 25.00
- K33N (p.Lys33Asn), Ensembl rs1714569815, REVEL 0.25, CADD 25.50
- L35W (p.Leu35Trp), cosmic curated COSV10587
- D36V (p.Asp36Val), cosmic curated COSV10511
- T37I (p.Thr37Ile), cosmic curated COSV60500
- D38N (p.Asp38Asn), Ensembl rs2108446640
- L39P (p.Leu39Pro), Ensembl rs1714569753
- H41Y (p.His41Tyr), TOPMed rs1714569636, gnomAD rs1714569636, REVEL 0.19, CADD 24.40
- D42N (p.Asp42Asn), rs1221002517, NCI-TCGA Cosmic COSV1001, cosmic curated COSV10011, gnomAD rs1221002517, REVEL 0.45, CADD 29.50, Variant assessed as somatic; moderate impact.
- E45G (p.Glu45Gly), cosmic curated COSV10440
- Q48H (p.Gln48His), cosmic curated COSV10440
- D49A (p.Asp49Ala), TOPMed rs1433707925, gnomAD rs1433707925, REVEL 0.66, CADD 33.00
- D49E (p.Asp49Glu), NCI-TCGA Cosmic COSV1001, cosmic curated COSV10011, Variant assessed as somatic; moderate impact.
- D49H (p.Asp49His), cosmic curated COSV60500
- D49Y (p.Asp49Tyr), cosmic curated COSV10738, Ensembl rs2108446554
- L50I (p.Leu50Ile), cosmic curated COSV60500
- L50R (p.Leu50Arg), cosmic curated COSV60500
- S51C (p.Ser51Cys), gnomAD rs1362660709, REVEL 0.49, CADD 29.00
- S51G (p.Ser51Gly), cosmic curated COSV10587
- S51N (p.Ser51Asn), gnomAD rs1304164243, REVEL 0.31, CADD 26.30
- A56V (p.Ala56Val), gnomAD rs1358318361, REVEL 0.15, CADD 23.80
- A61V (p.Ala61Val), TOPMed rs1164415688, gnomAD rs1164415688, REVEL 0.30, CADD 32.00
- V63L (p.Val63Leu), gnomAD rs1377960309, REVEL 0.31, CADD 24.70
- P64S (p.Pro64Ser), NCI-TCGA Cosmic COSV6049, cosmic curated COSV60499, Variant assessed as somatic; moderate impact.
- P64T (p.Pro64Thr), gnomAD rs1411421570, REVEL 0.36, CADD 27.40
- D65H (p.Asp65His), cosmic curated COSV60502, TOPMed rs1459088256, gnomAD rs1459088256, REVEL 0.36, CADD 27.20
- D65V (p.Asp65Val), rs1167819091, NCI-TCGA Cosmic COSV1001, cosmic curated COSV10011, gnomAD rs1167819091, REVEL 0.51, CADD 31.00, Variant assessed as somatic; moderate impact.
- D66N (p.Asp66Asn), cosmic curated COSV10511
- Q68L (p.Gln68Leu), TOPMed rs1429227347, gnomAD rs1429227347, REVEL 0.52, CADD 27.40
- Q68R (p.Gln68Arg), TOPMed rs1429227347, gnomAD rs1429227347
- F69S (p.Phe69Ser), gnomAD rs1371359850
- P71L (p.Pro71Leu), Ensembl rs1319038497
- D72N (p.Asp72Asn), ExAC rs751536392, gnomAD rs751536392, REVEL 0.46, CADD 29.20
- D72Y (p.Asp72Tyr), NCI-TCGA Cosmic COSV1001, cosmic curated COSV10011, REVEL 0.51, CADD 31.00, Variant assessed as somatic; moderate impact.
- F73V (p.Phe73Val), cosmic curated COSV60506
- Q74H (p.Gln74His), ESP rs142245897, ExAC rs142245897, TOPMed rs142245897, gnomAD rs142245897, REVEL 0.25, CADD 22.40
- Q74P (p.Gln74Pro), Ensembl rs2108446515
- S75A (p.Ser75Ala), cosmic curated COSV10587
- S75C (p.Ser75Cys), Ensembl rs1714561780, REVEL 0.35, CADD 28.70
- N77H (p.Asn77His), cosmic curated COSV60507
- L78V (p.Leu78Val), ESP rs372433151, ExAC rs372433151, TOPMed rs372433151, gnomAD rs372433151, REVEL 0.10, CADD 17.60
- L80I (p.Leu80Ile), NCI-TCGA Cosmic COSV6050, cosmic curated COSV60501, CADD 8.13, Variant assessed as somatic; moderate impact.
- L80P (p.Leu80Pro), cosmic curated COSV10883
- A82V (p.Ala82Val), TOPMed rs1713925890, gnomAD rs1713925890, REVEL 0.23, CADD 26.70
- P83A (p.Pro83Ala), TOPMed rs1412277860, REVEL 0.26, CADD 23.10, Uncertain significance, not specified
- P84L (p.Pro84Leu), cosmic curated COSV10965, REVEL 0.27, CADD 29.40
- P85A (p.Pro85Ala), NCI-TCGA Cosmic COSV6050, cosmic curated COSV60506, Variant assessed as somatic; moderate impact.
- P85L (p.Pro85Leu), TOPMed rs907103876, REVEL 0.11, CADD 24.60
- P85T (p.Pro85Thr), TOPMed rs540138059, gnomAD rs540138059, REVEL 0.14, CADD 23.70
- T86A (p.Thr86Ala), TOPMed rs1713925542
- T86S (p.Thr86Ser), ExAC rs775007271, gnomAD rs775007271, REVEL 0.06, CADD 20.10
- K87R (p.Lys87Arg), gnomAD rs1345723205, REVEL 0.24, CADD 24.40
- I88V (p.Ile88Val), Ensembl rs1578552734
- R90L (p.Arg90Leu), 1000Genomes rs767971453, ExAC rs767971453, TOPMed rs767971453, gnomAD rs767971453
- R90Q (p.Arg90Gln), rs767971453, 1000Genomes rs767971453, ExAC rs767971453, TOPMed rs767971453, REVEL 0.21, CADD 24.80, Variant assessed as somatic; moderate impact.
- R90W (p.Arg90Trp), rs1276673113, NCI-TCGA Cosmic COSV1001, cosmic curated COSV10011, TOPMed rs1276673113, REVEL 0.42, CADD 31.00, Variant assessed as somatic; moderate impact.
- S94G (p.Ser94Gly), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- S94I (p.Ser94Ile), cosmic curated COSV10965
- S94N (p.Ser94Asn), cosmic curated COSV60501
- P95S (p.Pro95Ser), cosmic curated COSV60502, REVEL 0.54, CADD 26.00
- S96A (p.Ser96Ala), TOPMed rs1713925035
- S96F (p.Ser96Phe), cosmic curated COSV60499
- S97A (p.Ser97Ala), ExAC rs774972931, gnomAD rs774972931, REVEL 0.06, CADD 20.40
- E98K (p.Glu98Lys), ExAC rs771188086, TOPMed rs771188086, gnomAD rs771188086, Uncertain significance, not specified
- L99M (p.Leu99Met), NCI-TCGA Cosmic COSV1001, cosmic curated COSV10011, Variant assessed as somatic; moderate impact.
- S100L (p.Ser100Leu), cosmic curated COSV10440, ExAC rs773508609, TOPMed rs773508609, gnomAD rs773508609, REVEL 0.29, CADD 25.20
- S100P (p.Ser100Pro), cosmic curated COSV10511, REVEL 0.31, CADD 26.20
- C102Y (p.Cys102Tyr), 1000Genomes rs202139916, REVEL 0.47, CADD 25.60, Uncertain significance, not specified
- H104D (p.His104Asp), gnomAD rs1713924186, REVEL 0.23, CADD 23.80
- H104Q (p.His104Gln), cosmic curated COSV60503
- H104R (p.His104Arg), rs752940067, ClinGen CA89856278, ClinVar RCV004239652, Ensembl rs752940067, AlphaMissense 0.06, MetaLR 0.04, Uncertain significance, not specified
- E105K (p.Glu105Lys), NCI-TCGA Cosmic COSV6050, cosmic curated COSV60503, Variant assessed as somatic; moderate impact.
- Q106* (p.Gln106Ter), cosmic curated COSV10011
- Q106E (p.Gln106Glu), ExAC rs755131256, gnomAD rs755131256
- Q106H (p.Gln106His), NCI-TCGA Cosmic COSV1001, cosmic curated COSV10011, Variant assessed as somatic; moderate impact.
- A107D (p.Ala107Asp), cosmic curated COSV60505
- A107P (p.Ala107Pro), ExAC rs745776119, TOPMed rs745776119, gnomAD rs745776119, REVEL 0.07, CADD 16.90, Uncertain significance
- A107S (p.Ala107Ser), rs745776119, ClinGen CA89856277, ClinVar RCV004364116, ExAC rs745776119, REVEL 0.02, CADD 17.30, Uncertain significance, not specified
- A107T (p.Ala107Thr), cosmic curated COSV60501, ExAC rs745776119, TOPMed rs745776119, gnomAD rs745776119, REVEL 0.04, CADD 20.20, Uncertain significance
- A107V (p.Ala107Val), rs1165631447, NCI-TCGA Cosmic COSV6050, cosmic curated COSV60501, REVEL 0.04, CADD 23.20, Variant assessed as somatic; moderate impact.
- L108F (p.Leu108Phe), TOPMed rs1249712516, gnomAD rs1249712516, REVEL 0.09, CADD 18.10
- L108H (p.Leu108His), TOPMed rs1713923633, REVEL 0.18, CADD 25.50
- G109V (p.Gly109Val), TOPMed rs1482734733
- A110T (p.Ala110Thr), Ensembl rs1713923480
- N111I (p.Asn111Ile), Ensembl rs1578552686
- N111S (p.Asn111Ser), Ensembl rs1578552686, REVEL 0.09, CADD 14.90
- Y112* (p.Tyr112Ter), Ensembl rs1713923202
- Y112C (p.Tyr112Cys), 1000Genomes rs61760177, ESP rs61760177, ExAC rs61760177, TOPMed rs61760177, REVEL 0.48, CADD 25.30
- Y112H (p.Tyr112His), rs200054486, ClinGen CA2742671, ClinVar RCV004383177, ExAC rs200054486, REVEL 0.21, CADD 24.00, Uncertain significance, not specified
- G113R (p.Gly113Arg), TOPMed rs1010586417, REVEL 0.17, CADD 24.00
- E114A (p.Glu114Ala), 1000Genomes rs557148325
- E114G (p.Glu114Gly), 1000Genomes rs557148325, REVEL 0.29, CADD 27.60
- K115N (p.Lys115Asn), Ensembl rs1713922789
- K115R (p.Lys115Arg), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- K115T (p.Lys115Thr), cosmic curated COSV10587, REVEL 0.41, CADD 27.80
- C116G (p.Cys116Gly), ExAC rs763691220, gnomAD rs763691220, REVEL 0.66, CADD 29.00
- L117P (p.Leu117Pro), ExAC rs755799638, gnomAD rs755799638, REVEL 0.60, CADD 29.80
- Y118S (p.Tyr118Ser), TOPMed rs1713922611, REVEL 0.50, CADD 26.30
- Y120D (p.Tyr120Asp), TOPMed rs1205730921, gnomAD rs1205730921, REVEL 0.41, CADD 24.90
- C121R (p.Cys121Arg), gnomAD rs1272437619
- A122D (p.Ala122Asp), cosmic curated COSV60505
- A122T (p.Ala122Thr), TOPMed rs1332934017, gnomAD rs1332934017, REVEL 0.16, CADD 28.30, Uncertain significance, not specified
- Y123C (p.Tyr123Cys), Ensembl rs1713895711, REVEL 0.25, CADD 22.90
- D124H (p.Asp124His), cosmic curated COSV10587, REVEL 0.29, CADD 25.90
- D124N (p.Asp124Asn), rs377678658, ClinGen CA2742650, ClinVar RCV004275312, ESP rs377678658, REVEL 0.25, CADD 28.80, Uncertain significance, not specified
- R125T (p.Arg125Thr), ExAC rs752336984, gnomAD rs752336984
- P128S (p.Pro128Ser), TOPMed rs1473039511, gnomAD rs1473039511, REVEL 0.14, CADD 22.70
- S129C (p.Ser129Cys), rs780967082, ClinGen CA2742648, ClinVar RCV004383178, ExAC rs780967082, REVEL 0.12, CADD 25.90, Uncertain significance, not specified
- G130V (p.Gly130Val), cosmic curated COSV10462, REVEL 0.26, CADD 25.10, Uncertain significance, not specified
- F131L (p.Phe131Leu), ExAC rs183104300, gnomAD rs183104300, REVEL 0.14, CADD 23.10
- F131V (p.Phe131Val), Ensembl rs1578552185
- F131Y (p.Phe131Tyr), ExAC rs754385394, REVEL 0.19, CADD 22.90
- P133S (p.Pro133Ser), TOPMed rs868275534, REVEL 0.24, CADD 23.50, Uncertain significance, not specified
- L134S (p.Leu134Ser), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- T135N (p.Thr135Asn), ExAC rs766752832, gnomAD rs766752832, REVEL 0.17, CADD 23.10
- P136T (p.Pro136Thr), ExAC rs763481967, gnomAD rs763481967, REVEL 0.32, CADD 24.90
- T138A (p.Thr138Ala), cosmic curated COSV10511, REVEL 0.02, CADD 8.33
- T138I (p.Thr138Ile), ExAC rs751015849, gnomAD rs751015849, REVEL 0.10, CADD 23.10
- T139I (p.Thr139Ile), ExAC rs765682543, TOPMed rs765682543, gnomAD rs765682543, REVEL 0.22, CADD 25.40
- T139N (p.Thr139Asn), ExAC rs765682543, TOPMed rs765682543, gnomAD rs765682543, REVEL 0.14, CADD 24.70
- T139P (p.Thr139Pro), cosmic curated COSV60501, REVEL 0.18, CADD 24.30
- T139S (p.Thr139Ser), ExAC rs765682543, TOPMed rs765682543, gnomAD rs765682543
- P140H (p.Pro140His), TOPMed rs1713894354, gnomAD rs1713894354
- P140L (p.Pro140Leu), cosmic curated COSV60502, REVEL 0.31, CADD 25.50
- P140R (p.Pro140Arg), TOPMed rs1713894354, gnomAD rs1713894354, REVEL 0.43, CADD 25.80
- P140S (p.Pro140Ser), rs971551407, NCI-TCGA Cosmic COSV1001, cosmic curated COSV10011, TOPMed rs971551407, REVEL 0.25, CADD 23.80, Variant assessed as somatic; moderate impact.
- L141F (p.Leu141Phe), ExAC rs768938900, gnomAD rs768938900
- L141P (p.Leu141Pro), cosmic curated COSV60505, REVEL 0.18, CADD 25.80
- L141S (p.Leu141Ser), NCI-TCGA Cosmic COSV1001, Variant assessed as somatic; high impact.
- L141V (p.Leu141Val), NCI-TCGA Cosmic COSV1001, cosmic curated COSV10011, Variant assessed as somatic; moderate impact.
- P143L (p.Pro143Leu), Ensembl rs1713894124, REVEL 0.30, CADD 25.50
- T144I (p.Thr144Ile), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- T144P (p.Thr144Pro), Ensembl rs1578552152, REVEL 0.03, CADD 17.30
- H145P (p.His145Pro), Ensembl rs1713893994, REVEL 0.14, CADD 22.20
- H145Q (p.His145Gln), cosmic curated COSV10965, REVEL 0.05, CADD 15.40
- P148H (p.Pro148His), NCI-TCGA Cosmic COSV6049, Variant assessed as somatic; moderate impact.
- P148L (p.Pro148Leu), cosmic curated COSV60499, ExAC rs760624416, gnomAD rs760624416
- P148S (p.Pro148Ser), cosmic curated COSV10511
- L149P (p.Leu149Pro), cosmic curated COSV10738, REVEL 0.09, CADD 23.30
- L149V (p.Leu149Val), rs78506201, ClinGen CA2742637, ClinVar RCV000962064, 1000Genomes rs78506201, REVEL 0.06, CADD 15.60, Benign, not provided
- F150L (p.Phe150Leu), cosmic curated COSV10609, ExAC rs772085062, TOPMed rs772085062, gnomAD rs772085062, REVEL 0.03, CADD 16.60
- P151A (p.Pro151Ala), ESP rs369950562, ExAC rs369950562, TOPMed rs369950562, gnomAD rs369950562, REVEL 0.06, CADD 21.00
- P151L (p.Pro151Leu), cosmic curated COSV60505, REVEL 0.10, CADD 23.80
- P151S (p.Pro151Ser), cosmic curated COSV10440, ESP rs369950562, ExAC rs369950562, TOPMed rs369950562, REVEL 0.07, CADD 22.20
- P152H (p.Pro152His), NCI-TCGA TCGA novel, Variant assessed as somatic; high impact.
- P152Q (p.Pro152Gln), rs537105512, ClinGen CA2742634, cosmic curated COSV60500, ClinVar RCV004325720, REVEL 0.10, CADD 23.80, Uncertain significance, not specified
- P153L (p.Pro153Leu), TOPMed rs1713893262
- Q154H (p.Gln154His), ExAC rs769575342, gnomAD rs769575342, REVEL 0.07, CADD 20.50
Public ETV5 analysis runs
- ETV5 analysis run — ETV5 (816 variants) — completed 2026-08-20