COL4A4 (Collagen alpha-4(IV) chain) variants and mutations

COL4A4 (also known as Collagen alpha-4(IV) chain) is a human protein-coding gene encoding a collagen alpha-4(IV) chain protein. It combines with the alpha3 and alpha5 chains to form the mature type IV collagen network of glomerular, cochlear, and ocular basement membranes. Pathogenic variants cause autosomal Alport-spectrum disease and can present with isolated persistent hematuria. This analysis covers 2,719 COL4A4 variants and mutations. Of these, 85% have computational variant effect predictions. Disease context includes autosomal recessive Alport syndrome, hematuria, benign familial, 1, and Hematuria. Example COL4A4 variants include W2*, W2C, and S3F.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, MaveDB, LitVar.

Notable COL4A4 variants

Examples include W2*, W2C, S3F, S3T, L4A, L4P, H5N, H5R. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.