G441R (p.Gly441Arg) variant of COL3A1 (Collagen alpha-1(III) chain)

G441R (p.Gly441Arg) in COL3A1 (Collagen alpha-1(III) chain) is a missense change. Clinical records from ClinVar, EBI, and UniProt describe it as likely pathogenic in the context of Familial thoracic aortic aneurysm and aortic dissection; Ehlers-Danlos syndrome. The record also includes published literature and structural context.

G441R (p.Gly441Arg) variant details