CALM2 (Calmodulin-2) variants and mutations

CALM2 (also known as Calmodulin-2) is a human protein-coding gene encoding a calmodulin-2 protein. It supplies an identical calmodulin protein that couples changes in intracellular calcium to numerous signaling and ion-channel targets. Pathogenic missense variants can cause calmodulinopathy with malignant ventricular arrhythmias, including long-QT syndrome and catecholaminergic polymorphic ventricular tachycardia. This analysis covers 245 CALM2 variants and mutations. Of these, 81% have computational variant effect predictions. Disease context includes long QT syndrome 15, Romano-Ward syndrome, and familial long QT syndrome. Example CALM2 variants include M1?, D3E, and D3H.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, ClinGen, MaveDB, LitVar.

Notable CALM2 variants

Examples include M1?, D3E, D3H, D3N, L5M, T6I, T6S, E8*. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.