TBCD (Tubulin-specific chaperone D) variants and mutations
TBCD (also known as Tubulin-specific chaperone D) is a human protein-coding gene encoding a tubulin-specific chaperone D protein. A tubulin-folding chaperone that helps assemble tubulin complexes and regulate microtubule dynamics. It also acts as a regulator of the ARL2 GTPase and supports mitotic-spindle formation and neuronal morphogenesis. This analysis covers 1,652 TBCD variants and mutations. Of these, 82% have computational variant effect predictions. Disease context includes early-onset progressive diffuse brain atrophy-microcephaly-muscle weakness-optic, PEHO syndrome, and neurodegenerative disease. Example TBCD variants include A2T, A2V, and A2S.
Variant analysis overview
- Gene: TBCD
- Protein: Tubulin-specific chaperone D
- UniProt accession: Q9BTW9
- Organism: Homo sapiens
- Variants analyzed: 1652
- Variant scope: all variants
- Completed: 2026-06-12
Variant and mutation evidence
- Variant composition: 1,377 unspecified-consequence records; 184 missense variants; 65 synonymous variants; 13 frameshift variants; 3 in-frame deletions; 8 stop-gained variants; 2 splice-region variants
- Prediction scores: 1,362 variants have prediction scores (82% of the analyzed set).
Clinical, disease, and population context
- Disease context: 25 disease associations are represented. Top associations: early-onset progressive diffuse brain atrophy-microcephaly-muscle weakness-optic, PEHO syndrome, neurodegenerative disease, genetic disorder, seborrhea-like dermatitis with psoriasiform elements, mixed connective tissue disease, alcohol drinking, preeclampsia, peripheral vascular disease, seborrheic keratosis, protozoa infectious disease, Intellectual disability.
Data sources
Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, PharmGKB, MaveDB, LitVar.
Notable TBCD variants
Examples include A2T, A2V, A2S, A2G, A2D, A2A, L3M, L3V. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.
- A2T (p.Ala2Thr), TOPMed rs1279157812, gnomAD rs1279157812, REVEL 0.06, CADD 22.90
- A2V (p.Ala2Val), rs1370974061, ClinGen CA401622127, cosmic curated COSV56181, ClinVar RCV001944918, REVEL 0.08, CADD 11.10, Uncertain significance, not provided
- A2S (p.Ala2Ser), gnomAD 17-82752197-G-T, REVEL 0.05, CADD 19.90
- A2G (p.Ala2Gly), gnomAD 17-82752198-C-G, REVEL 0.11, CADD 12.50
- A2D (p.Ala2Asp), gnomAD 17-82752198-C-A, REVEL 0.09, CADD 12.70
- A2A (p.Ala2Ala), gnomAD 17-82752199-C-T, CADD 6.27
- L3M (p.Leu3Met), NCI-TCGA Cosmic COSV5618, cosmic curated COSV56181, REVEL 0.09, CADD 15.60, Variant assessed as somatic; moderate impact.
- L3V (p.Leu3Val), gnomAD 17-82752200-C-G, REVEL 0.03, CADD 4.44
- L3L (p.Leu3Leu), rs1229949623, gnomAD 17-82752200-C-T, CADD 4.90
- L3P (p.Leu3Pro), gnomAD 17-82752201-T-C, REVEL 0.16, CADD 22.30
- L3Q (p.Leu3Gln), gnomAD 17-82752201-T-A, REVEL 0.14, CADD 21.70
- S4C (p.Ser4Cys), rs2510347955, ClinGen CA401622133, ClinVar RCV002471788, REVEL 0.12, CADD 14.80, Uncertain significance, Early-onset progressive diffuse brain atrophy-microcephaly-muscle weakness-optic
- S4R (p.Ser4Arg), gnomAD rs1333992290, REVEL 0.05, CADD 14.90
- S4G (p.Ser4Gly), gnomAD 17-82752203-A-G, REVEL 0.04, CADD 7.29
- S4N (p.Ser4Asn), gnomAD 17-82752204-G-A, REVEL 0.04, CADD 11.40
- S4I (p.Ser4Ile), gnomAD 17-82752204-G-T, REVEL 0.03, CADD 18.20
- S4S (p.Ser4Ser), gnomAD 17-82752205-C-T, CADD 9.77
- D5G (p.Asp5Gly), gnomAD rs2047134623, REVEL 0.06, CADD 19.50
- D5H (p.Asp5His), Ensembl rs1354004393, REVEL 0.11, CADD 15.60
- D5N (p.Asp5Asn), gnomAD 17-82752206-G-A, REVEL 0.06, CADD 10.70
- D5Y (p.Asp5Tyr), gnomAD 17-82752206-G-T, REVEL 0.03, CADD 11.50
- D5E (p.Asp5Glu), gnomAD 17-82752207-AC-A, CADD 6.52
- D5D (p.Asp5Asp), gnomAD 17-82752208-C-T, CADD 2.68
- D5A (p.Asp5Ala), rs1255483538, gnomAD 17-82752849-GA-G, CADD 1.44
- D5V (p.Asp5Val), rs2047186096, gnomAD 17-82752850-A-T, CADD 4.29
- E6* (p.Glu6Ter), rs1010575243, ClinGen CA295248404, ClinVar RCV003548440, TOPMed rs1010575243, CADD 36.00, Pathogenic
- E6K (p.Glu6Lys), TOPMed rs1010575243, gnomAD rs1010575243, REVEL 0.05, CADD 13.40, Uncertain significance, not provided
- E6Q (p.Glu6Gln), TOPMed rs1010575243, gnomAD rs1010575243, Pathogenic
- E6G (p.Glu6Gly), gnomAD 17-82752210-A-G, REVEL 0.05, CADD 7.79
- E6D (p.Glu6Asp), gnomAD 17-82752210-AAC-A, CADD 22.10
- E6E (p.Glu6Glu), rs1211299248, gnomAD 17-82752211-A-G, CADD 5.91
- P7Q (p.Pro7Gln), gnomAD rs1291478820, REVEL 0.05, CADD 19.50
- P7T (p.Pro7Thr), TOPMed rs2047134926, gnomAD rs2047134926, REVEL 0.05, CADD 13.40, Uncertain significance, Inborn genetic diseases
- P7R (p.Pro7Arg), gnomAD 17-82752211-AC-A, CADD 21.90
- P7S (p.Pro7Ser), gnomAD 17-82752212-C-T, REVEL 0.02, CADD 13.10
- P7L (p.Pro7Leu), gnomAD 17-82752213-C-T, REVEL 0.04, CADD 16.00
- P7P (p.Pro7Pro), rs768875605, gnomAD 17-82752214-G-A, CADD 11.50
- A8T (p.Ala8Thr), gnomAD rs1203424416, REVEL 0.06, CADD 17.90
- A8V (p.Ala8Val), TOPMed rs1473086651, gnomAD rs1473086651, REVEL 0.03, CADD 17.60
- A8S (p.Ala8Ser), gnomAD 17-82752215-G-T, REVEL 0.07, CADD 16.00
- A8D (p.Ala8Asp), gnomAD 17-82752216-C-A, REVEL 0.10, CADD 22.10
- A8A (p.Ala8Ala), rs1230793692, gnomAD 17-82752217-C-T, CADD 11.10
- A8P (p.Ala8Pro), rs1019523934, gnomAD 17-82752852-G-C, CADD 5.45
- A9E (p.Ala9Glu), gnomAD rs1184731475, REVEL 0.09, CADD 15.00
- A9P (p.Ala9Pro), TOPMed rs1482289223, gnomAD rs1482289223, REVEL 0.16, CADD 21.30
- A9T (p.Ala9Thr), TOPMed rs1482289223, gnomAD rs1482289223, REVEL 0.09, CADD 15.40
- A9S (p.Ala9Ser), gnomAD 17-82752218-G-T, REVEL 0.06, CADD 14.80
- A9V (p.Ala9Val), gnomAD 17-82752219-C-T, REVEL 0.01, CADD 16.40
- A9A (p.Ala9Ala), gnomAD 17-82752220-G-T, CADD 11.80
- G10C (p.Gly10Cys), rs11550062, ClinGen CA8861495, cosmic curated COSV56181, ClinVar RCV001517315, REVEL 0.06, CADD 23.20, Benign, not provided; not specified; Early-onset progressive diffuse brain atrophy-micro
- G10D (p.Gly10Asp), rs533171147, ClinGen CA8861496, ClinVar RCV001329506, ClinVar RCV003770818, REVEL 0.01, CADD 19.10, Conflicting interpretations, Early-onset progressive diffuse brain atrophy-microcephaly-muscle weakness-optic
- G10R (p.Gly10Arg), gnomAD 17-82752221-G-C, REVEL 0.03, CADD 21.40
- G10S (p.Gly10Ser), gnomAD 17-82752221-G-A, REVEL 0.01, CADD 16.80
- G10V (p.Gly10Val), gnomAD 17-82752222-G-T, REVEL 0.03, CADD 19.30
- G10G (p.Gly10Gly), gnomAD 17-82752223-C-A, CADD 10.20
- G10E (p.Gly10Glu), rs537509482, gnomAD 17-82752847-G-A, CADD 1.09
- G11D (p.Gly11Asp), TOPMed rs1406007129, gnomAD rs1406007129, REVEL 0.01, CADD 11.10
- G11R (p.Gly11Arg), TOPMed rs1044663167, gnomAD rs1044663167, REVEL 0.01, CADD 11.80
- G11S (p.Gly11Ser), TOPMed rs1044663167, gnomAD rs1044663167, REVEL 0.00, CADD 6.78
- G11C (p.Gly11Cys), gnomAD 17-82752224-G-T, REVEL 0.09, CADD 14.80
- G11V (p.Gly11Val), gnomAD 17-82752225-G-T, REVEL 0.01, CADD 13.90
- G11G (p.Gly11Gly), rs773849891, gnomAD 17-82752226-C-A, CADD 11.40
- P12S (p.Pro12Ser), TOPMed rs1449546253, REVEL 0.00, CADD 11.20
- P12L (p.Pro12Leu), gnomAD 17-82752228-C-T, REVEL 0.01, CADD 15.00
- P12H (p.Pro12His), gnomAD 17-82752228-C-A, REVEL 0.03, CADD 17.80
- P12P (p.Pro12Pro), gnomAD 17-82752229-C-A, CADD 8.26
- P12A (p.Pro12Ala), rs368393853, gnomAD 17-82752906-C-G, CADD 4.36
- P12R (p.Pro12Arg), rs572553646, gnomAD 17-82752907-C-G, CADD 5.29
- E13K (p.Glu13Lys), TOPMed rs1411439196, gnomAD rs1411439196, REVEL 0.03, CADD 21.90
- E13Q (p.Glu13Gln), TOPMed rs1411439196, gnomAD rs1411439196
- E13R (p.Glu13Arg), gnomAD 17-82752225-G-GC, CADD 22.60
- E13* (p.Glu13Ter), gnomAD 17-82752230-G-T, CADD 36.00
- E13G (p.Glu13Gly), gnomAD 17-82752231-A-G, REVEL 0.03, CADD 19.80
- E13E (p.Glu13Glu), rs1330927173, gnomAD 17-82752232-G-A, CADD 8.11
- E13D (p.Glu13Asp), gnomAD 17-82752232-G-T, REVEL 0.03, CADD 10.20
- E14K (p.Glu14Lys), TOPMed rs907337469, REVEL 0.04, CADD 21.50
- E14* (p.Glu14Ter), gnomAD 17-82752233-G-T, CADD 39.00
- E14V (p.Glu14Val), gnomAD 17-82752234-A-T, REVEL 0.02, CADD 22.30
- E14G (p.Glu14Gly), gnomAD 17-82752234-A-G, REVEL 0.04, CADD 22.50
- E14D (p.Glu14Asp), gnomAD 17-82752235-G-T, REVEL 0.02, CADD 12.30
- E14E (p.Glu14Glu), rs1568079966, gnomAD 17-82752235-G-A, CADD 10.90
- E15A (p.Glu15Ala), ExAC rs761196902, gnomAD rs761196902, REVEL 0.01, CADD 12.30, Uncertain significance, Inborn genetic diseases
- E15del (p.Glu15del), rs1209134139, gnomAD 17-82752229-CGAG-, CADD 15.10
- E15* (p.Glu15Ter), gnomAD 17-82752236-G-T, CADD 37.00
- E15K (p.Glu15Lys), gnomAD 17-82752236-G-A, REVEL 0.02, CADD 18.20
- E15G (p.Glu15Gly), gnomAD 17-82752237-A-G, REVEL 0.01, CADD 15.80
- E15V (p.Glu15Val), gnomAD 17-82752237-A-T, REVEL 0.01, CADD 14.60
- E15D (p.Glu15Asp), gnomAD 17-82752238-G-T, REVEL 0.02, CADD 15.00
- E15E (p.Glu15Glu), gnomAD 17-82752238-G-A, CADD 12.70
- A16T (p.Ala16Thr), ExAC rs769438572, gnomAD rs769438572, REVEL 0.01, CADD 19.60
- A16S (p.Ala16Ser), gnomAD 17-82752239-G-T, REVEL 0.01, CADD 16.80
- A16G (p.Ala16Gly), gnomAD 17-82752239-GC-G, CADD 24.10
- A16V (p.Ala16Val), gnomAD 17-82752240-C-T, REVEL 0.05, CADD 17.70
- A16E (p.Ala16Glu), gnomAD 17-82752240-C-A, REVEL 0.05, CADD 15.30
- A16A (p.Ala16Ala), gnomAD 17-82752241-G-A, CADD 14.70
- E17Q (p.Glu17Gln), ExAC rs775011890, TOPMed rs775011890, gnomAD rs775011890, REVEL 0.06, CADD 25.40, Uncertain significance, Inborn genetic diseases
- E17K (p.Glu17Lys), gnomAD 17-82752242-G-A, REVEL 0.07, CADD 24.10
- E17* (p.Glu17Ter), gnomAD 17-82752242-G-T, CADD 41.00
- E17G (p.Glu17Gly), gnomAD 17-82752243-A-G, REVEL 0.06, CADD 23.30
- E17V (p.Glu17Val), gnomAD 17-82752243-A-T, REVEL 0.11, CADD 25.40
- E17E (p.Glu17Glu), gnomAD 17-82752244-G-A, CADD 14.00
- E17D (p.Glu17Asp), gnomAD 17-82752244-G-T, REVEL 0.10, CADD 22.60
- D18E (p.Asp18Glu), rs1003016750, ClinGen CA295248477, ClinVar RCV002896286, TOPMed rs1003016750, REVEL 0.01, CADD 0.31, Uncertain significance, Inborn genetic diseases
- D18N (p.Asp18Asn), ExAC rs762541329, TOPMed rs762541329, gnomAD rs762541329, REVEL 0.04, CADD 22.80
- D18V (p.Asp18Val), Ensembl rs2143701266
- D18Y (p.Asp18Tyr), gnomAD 17-82752245-G-T, REVEL 0.04, CADD 24.20
- D18G (p.Asp18Gly), gnomAD 17-82752246-A-G, REVEL 0.02, CADD 17.00
- D18D (p.Asp18Asp), rs1003016750, gnomAD 17-82752247-C-T, CADD 6.02
- E19* (p.Glu19Ter), TOPMed rs1348366650, gnomAD rs1348366650, CADD 36.00
- E19K (p.Glu19Lys), TOPMed rs1348366650, gnomAD rs1348366650, REVEL 0.02, CADD 17.90
- E19Q (p.Glu19Gln), TOPMed rs1348366650, gnomAD rs1348366650, REVEL 0.03, CADD 16.60
- E19V (p.Glu19Val), gnomAD 17-82752249-A-T, REVEL 0.01, CADD 15.60
- E19G (p.Glu19Gly), gnomAD 17-82752249-A-G, REVEL 0.01, CADD 16.40
- E19D (p.Glu19Asp), gnomAD 17-82752250-G-T, REVEL 0.01, CADD 0.70
- E19E (p.Glu19Glu), rs1213422270, gnomAD 17-82752250-G-A, CADD 4.90
- T20I (p.Thr20Ile), TOPMed rs1026336168, gnomAD rs1026336168, REVEL 0.02, CADD 13.90
- T20A (p.Thr20Ala), gnomAD 17-82752251-A-G, REVEL 0.01, CADD 5.04
- T20R (p.Thr20Arg), gnomAD 17-82752252-C-G, REVEL 0.03, CADD 13.10
- T20T (p.Thr20Thr), rs1343772602, gnomAD 17-82752253-A-G, CADD 2.28
- L21M (p.Leu21Met), gnomAD 17-82752254-C-A, REVEL 0.06, CADD 13.60
- L21L (p.Leu21Leu), rs763768319, gnomAD 17-82752254-C-T, CADD 8.08
- L21V (p.Leu21Val), gnomAD 17-82752254-C-G, REVEL 0.01, CADD 8.31
- L21Q (p.Leu21Gln), gnomAD 17-82752255-T-A, REVEL 0.02, CADD 13.20
- L21P (p.Leu21Pro), gnomAD 17-82752255-T-C, REVEL 0.04, CADD 14.70
- A22V (p.Ala22Val), TOPMed rs1253057697, gnomAD rs1253057697, REVEL 0.02, CADD 9.57
- A22P (p.Ala22Pro), gnomAD 17-82752255-TG-T, CADD 12.10
- A22S (p.Ala22Ser), gnomAD 17-82752257-G-T, REVEL 0.08, CADD 8.44
- A22T (p.Ala22Thr), gnomAD 17-82752257-G-A, REVEL 0.06, CADD 9.81
- A22D (p.Ala22Asp), gnomAD 17-82752258-C-A, REVEL 0.04, CADD 10.30
- A22G (p.Ala22Gly), gnomAD 17-82752258-C-G, REVEL 0.01, CADD 7.45
- A22A (p.Ala22Ala), gnomAD 17-82752259-C-A, CADD 6.42
- F23L (p.Phe23Leu), gnomAD 17-82752259-CT-C, CADD 10.50
- F23I (p.Phe23Ile), gnomAD 17-82752260-T-A, REVEL 0.01, CADD 2.98
- F23S (p.Phe23Ser), gnomAD 17-82752261-T-C, REVEL 0.01, CADD 5.75
- F23F (p.Phe23Phe), rs557234788, gnomAD 17-82752262-T-C, CADD 9.28
- G24D (p.Gly24Asp), Ensembl rs2047137652, REVEL 0.06, CADD 18.40
- G24C (p.Gly24Cys), gnomAD 17-82752263-G-T, REVEL 0.04, CADD 21.90
- G24A (p.Gly24Ala), gnomAD 17-82752264-G-C, REVEL 0.02, CADD 11.20
- G24V (p.Gly24Val), gnomAD 17-82752264-G-T, REVEL 0.04, CADD 17.60
- G24G (p.Gly24Gly), rs1239676655, gnomAD 17-82752265-C-G, CADD 8.63
- G24R (p.Gly24Arg), rs1368930181, gnomAD 17-82752897-G-A, CADD 6.32
- A25T (p.Ala25Thr), gnomAD rs1473185255, REVEL 0.01, CADD 7.71
- A25V (p.Ala25Val), gnomAD 17-82752267-C-T, REVEL 0.00, CADD 13.10
- A25E (p.Ala25Glu), gnomAD 17-82752267-C-A, REVEL 0.01, CADD 12.00
- A25A (p.Ala25Ala), gnomAD 17-82752268-G-A, CADD 5.09
- A26S (p.Ala26Ser), gnomAD 17-82752269-G-T, REVEL 0.03, CADD 11.50
- A26T (p.Ala26Thr), gnomAD 17-82752269-G-A, REVEL 0.03, CADD 13.80
- A26G (p.Ala26Gly), gnomAD 17-82752270-C-G, REVEL 0.02, CADD 15.00
- A26E (p.Ala26Glu), gnomAD 17-82752270-C-A, REVEL 0.05, CADD 15.40
- A26V (p.Ala26Val), gnomAD 17-82752270-C-T, REVEL 0.02, CADD 13.00
- A26A (p.Ala26Ala), gnomAD 17-82752271-G-A, CADD 8.98
- L27G (p.Leu27Gly), gnomAD 17-82752267-CGG-C, CADD 22.00
- L27L (p.Leu27Leu), rs2143701660, gnomAD 17-82752272-C-T, CADD 9.67
- L27M (p.Leu27Met), gnomAD 17-82752272-C-A, REVEL 0.07, CADD 22.70
- L27Q (p.Leu27Gln), gnomAD 17-82752273-T-A, REVEL 0.11, CADD 24.60
- L27P (p.Leu27Pro), gnomAD 17-82752273-T-C, REVEL 0.13, CADD 24.80
- E28K (p.Glu28Lys), rs916503100, ClinGen CA295248545, ClinVar RCV002571710, ClinVar RCV002571711, REVEL 0.09, CADD 23.70, Uncertain significance, Inborn genetic diseases; not provided
- E28Q (p.Glu28Gln), gnomAD 17-82752275-G-C, REVEL 0.08, CADD 23.20
- E28* (p.Glu28Ter), gnomAD 17-82752275-G-T, CADD 42.00
- E28G (p.Glu28Gly), gnomAD 17-82752276-A-G, REVEL 0.05, CADD 22.40
- E28V (p.Glu28Val), gnomAD 17-82752276-A-T, REVEL 0.12, CADD 24.10
- E28A (p.Glu28Ala), gnomAD 17-82752276-A-C, REVEL 0.07, CADD 22.20
- E28E (p.Glu28Glu), rs1388569821, gnomAD 17-82752277-A-G, CADD 11.40
- E28D (p.Glu28Asp), gnomAD 17-82752277-A-T, REVEL 0.05, CADD 15.40
- A29T (p.Ala29Thr), gnomAD 17-82752278-G-A, REVEL 0.03, CADD 16.10
- A29S (p.Ala29Ser), gnomAD 17-82752278-G-T, REVEL 0.02, CADD 13.80
- A29E (p.Ala29Glu), gnomAD 17-82752279-C-A, REVEL 0.01, CADD 20.90
- A29V (p.Ala29Val), gnomAD 17-82752279-C-T, REVEL 0.02, CADD 20.60
- A29A (p.Ala29Ala), gnomAD 17-82752280-G-T, CADD 11.10
- A29G (p.Ala29Gly), rs1302882686, gnomAD 17-82752925-C-G, CADD 7.71
- F30I (p.Phe30Ile), gnomAD rs1431928097, REVEL 0.15, CADD 26.40
- F30S (p.Phe30Ser), gnomAD 17-82752280-GT-G, CADD 25.50
- F30V (p.Phe30Val), gnomAD 17-82752281-T-G, REVEL 0.12, CADD 26.40
- F30L (p.Phe30Leu), gnomAD 17-82752281-T-C, REVEL 0.14, CADD 27.10
- F30Y (p.Phe30Tyr), gnomAD 17-82752282-T-A, REVEL 0.15, CADD 26.70
- F30F (p.Phe30Phe), gnomAD 17-82752283-C-T, CADD 15.10
- G31D (p.Gly31Asp), rs1169464820, ClinGen CA401622308, ClinVar RCV001919467, ClinVar RCV005749922, REVEL 0.01, CADD 21.70, Uncertain significance, Inborn genetic diseases; not provided
- G31S (p.Gly31Ser), gnomAD 17-82752284-G-A, REVEL 0.03, CADD 19.10
- G31C (p.Gly31Cys), gnomAD 17-82752284-G-T, REVEL 0.10, CADD 23.90
- G31R (p.Gly31Arg), gnomAD 17-82752284-G-C, REVEL 0.03, CADD 21.50
Public TBCD analysis runs
- TBCD analysis run — TBCD (1,652 variants) — completed 2026-06-12