RYR2 (Ryanodine receptor 2) variants and mutations

RYR2 (also known as Ryanodine receptor 2) is a human protein-coding gene encoding a ryanodine receptor 2 protein. It releases calcium from the cardiac sarcoplasmic reticulum in response to trigger calcium entering during each action potential, thereby initiating contraction. Pathogenic variants can destabilize calcium release and are a major cause of catecholaminergic polymorphic ventricular tachycardia. This analysis covers 7,795 RYR2 variants and mutations. Of these, 82% have computational variant effect predictions. Disease context includes catecholaminergic polymorphic ventricular tachycardia 1, catecholaminergic polymorphic ventricular tachycardia, and ventricular arrhythmias due to cardiac ryanodine receptor calcium release defici. Example RYR2 variants include M1T, A2S, and A2P.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, Protein Data Bank, gnomAD constraint, Open Targets, ClinGen, MaveDB, LitVar.

Notable RYR2 variants

Examples include M1T, A2S, A2P, A2T, A2D, A2V, A2G, A2A. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.