OCRL (Q01968) variants and mutations

OCRL (also known as Q01968) is a human protein-coding gene encoding an inositol polyphosphate 5-phosphatase protein. It dephosphorylates specific phosphoinositides on endosomal and Golgi membranes and thereby regulates membrane trafficking, actin dynamics, and primary-cilium function. Loss-of-function variants cause Lowe syndrome and Dent disease type 2. This analysis covers 885 OCRL variants and mutations. Of these, 87% have computational variant effect predictions. Disease context includes oculocerebrorenal syndrome, Dent disease type 2, and Dent disease. Example OCRL variants include E2D, E2*, and E2G.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, ClinGen, MaveDB, LitVar.

Notable OCRL variants

Examples include E2D, E2*, E2G, E2E, P3L, P3T, P3S, P3Q. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.