NEB (Nebulin) variants and mutations

NEB (also known as Nebulin) is a human protein-coding gene encoding a nebulin protein. It spans much of the skeletal-muscle thin filament and acts as a molecular scaffold that helps specify filament length and optimize actin-myosin interaction. Biallelic pathogenic variants are a major cause of nemaline myopathy and related congenital myopathies. This analysis covers 11,016 NEB variants and mutations. Of these, 91% have computational variant effect predictions. Disease context includes nemaline myopathy 2, arthrogryposis multiplex congenita, and nemaline myopathy. Example NEB variants include A2E, A2S, and D3G.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, gnomAD constraint, Open Targets, ClinGen, MaveDB, LitVar.

Notable NEB variants

Examples include A2E, A2S, D3G, D4E, D4G, D4N, E5K, D6N. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.