M1I (p.Met1Ile) variant of MLH1 (DNA mismatch repair protein Mlh1)

M1I (p.Met1Ile) in MLH1 (DNA mismatch repair protein Mlh1) is a missense change. Clinical records from ClinVar, EBI, and UniProt describe it as likely pathogenic in the context of Lynch syndrome 1. The available variant effect predictions contribute to a CATVariant prioritization score of 0.85 / 1. The record also includes published literature and structural context.

M1I (p.Met1Ile) variant details