GABRG2 (P18507) variants and mutations

GABRG2 (also known as P18507) is a human protein-coding gene encoding a gamma-aminobutyric acid receptor subunit gamma-2 protein. The gene product supplies the gamma-2 subunit of synaptic GABA-A receptors, which are pentameric chloride channels activated by the inhibitory neurotransmitter GABA. The subunit helps receptor assembly and localization at neuronal membranes, and GABRG2 variants are associated with several epilepsy syndromes. This analysis covers 850 GABRG2 variants and mutations. Of these, 56% have computational variant effect predictions. Disease context includes Generalized epilepsy with febrile seizures-plus, childhood absence epilepsy, and epilepsy. Example GABRG2 variants include M1?, M1I, and M1V.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, ClinGen, MaveDB, LitVar.

Notable GABRG2 variants

Examples include M1?, M1I, M1V, M1L, M1T, S2G, S2R, S2I. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.