ETV1 (ETS translocation variant 1) variants and mutations
ETV1 (also known as ETS translocation variant 1) is a human protein-coding gene encoding an ETS translocation variant 1 protein. It controls lineage-specific transcription in neuronal, prostate, and other tissues downstream of MAPK signaling. Gene fusions or overexpression can act oncogenically, especially in prostate cancer and selected gastrointestinal stromal tumors. This analysis covers 939 ETV1 variants and mutations. Of these, 67% have computational variant effect predictions. Disease context includes type 2 diabetes mellitus, hair color, and benign prostatic hyperplasia. Example ETV1 variants include G3E, F4S, and F4Y.
Variant analysis overview
- Gene: ETV1
- Protein: ETS translocation variant 1
- UniProt accession: P50549
- Organism: Homo sapiens
- Variants analyzed: 939
- Variant scope: all variants
- Completed: 2026-08-22
Variant and mutation evidence
- Variant composition: 757 unspecified-consequence records; 1 stop retained variant; 1 stop lost; 81 synonymous variants; 79 missense variants; 9 frameshift variants; 2 in-frame deletions; 10 stop-gained variants; 1 splice-region variants
- Prediction scores: 632 variants have prediction scores (67% of the analyzed set).
Clinical, disease, and population context
- Disease context: 25 disease associations are represented. Top associations: type 2 diabetes mellitus, hair color, benign prostatic hyperplasia, diabetes mellitus, diverticular disease, Abnormality of the skeletal system, prostate carcinoma, lung carcinoma, prostate adenocarcinoma, Ewing sarcoma, esophageal adenocarcinoma, gastric carcinoma.
Protein structure and variant hotspots
- Protein features: 3 post-translational modification sites.
- PTM context: 2 variants overlap post-translational modification sites.
Data sources
Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, MaveDB, LitVar.
Notable ETV1 variants
Examples include G3E, F4S, F4Y, D6E, Q8L, Q8P, Q8R, V9A. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.
- G3E (p.Gly3Glu), NCI-TCGA Cosmic COSV9962, cosmic curated COSV99623, CADD 17.70, Variant assessed as somatic; moderate impact.
- F4S (p.Phe4Ser), ExAC rs777428309, TOPMed rs777428309, gnomAD rs777428309, REVEL 0.30, CADD 31.00
- F4Y (p.Phe4Tyr), cosmic curated COSV10637, ExAC rs777428309, TOPMed rs777428309, gnomAD rs777428309, REVEL 0.21, CADD 24.80
- D6E (p.Asp6Glu), cosmic curated COSV10941, CADD 13.40
- Q8L (p.Gln8Leu), cosmic curated COSV54146
- Q8P (p.Gln8Pro), cosmic curated COSV54149
- Q8R (p.Gln8Arg), gnomAD rs1218883502, REVEL 0.30, CADD 28.00
- V9A (p.Val9Ala), 1000Genomes rs1351415009, gnomAD rs1351415009, CADD 18.80
- P10L (p.Pro10Leu), NCI-TCGA Cosmic COSV5415, cosmic curated COSV54151, Variant assessed as somatic; moderate impact.
- M12L (p.Met12Leu), cosmic curated COSV54152, REVEL 0.12, CADD 18.30
- M12R (p.Met12Arg), ExAC rs753008700, gnomAD rs753008700, REVEL 0.17, CADD 27.50
- M12V (p.Met12Val), ExAC rs757988982, TOPMed rs757988982, gnomAD rs757988982, REVEL 0.11, CADD 16.10
- V13F (p.Val13Phe), gnomAD rs1376879279, REVEL 0.14, CADD 24.10
- N15K (p.Asn15Lys), 1000Genomes rs373945413, ESP rs373945413, ExAC rs373945413, TOPMed rs373945413, REVEL 0.11, CADD 19.40
- N15S (p.Asn15Ser), NCI-TCGA TCGA novel, REVEL 0.03, CADD 20.80, Variant assessed as somatic; moderate impact.
- S16G (p.Ser16Gly), gnomAD rs1453046202, REVEL 0.10, CADD 24.40
- R18C (p.Arg18Cys), 1000Genomes rs555395802, ExAC rs555395802, gnomAD rs555395802, REVEL 0.17, CADD 33.00
- R18H (p.Arg18His), gnomAD rs1338879591, REVEL 0.15, CADD 23.70
- G19A (p.Gly19Ala), ExAC rs776051542, gnomAD rs776051542, REVEL 0.26, CADD 23.60
- G19R (p.Gly19Arg), 1000Genomes rs535092479, ExAC rs535092479, TOPMed rs535092479, gnomAD rs535092479, REVEL 0.29, CADD 28.60
- R20I (p.Arg20Ile), NCI-TCGA Cosmic COSV5414, cosmic curated COSV54141, Variant assessed as somatic; moderate impact.
- R20K (p.Arg20Lys), ExAC rs770257114, TOPMed rs770257114
- R20T (p.Arg20Thr), ExAC rs770257114, TOPMed rs770257114, REVEL 0.16, CADD 22.70
- E24D (p.Glu24Asp), NCI-TCGA Cosmic COSV5414, cosmic curated COSV54141, REVEL 0.13, CADD 21.60, Variant assessed as somatic; moderate impact.
- E24K (p.Glu24Lys), ESP rs367998229, TOPMed rs367998229, REVEL 0.22, CADD 22.50
- E24Q (p.Glu24Gln), ESP rs367998229, TOPMed rs367998229
- K25N (p.Lys25Asn), ExAC rs781735914, TOPMed rs781735914, gnomAD rs781735914, REVEL 0.14, CADD 24.80
- P26S (p.Pro26Ser), ExAC rs747119926, TOPMed rs747119926, gnomAD rs747119926, REVEL 0.16, CADD 22.80
- P26T (p.Pro26Thr), ExAC rs747119926, TOPMed rs747119926, gnomAD rs747119926, REVEL 0.13, CADD 22.50
- T27A (p.Thr27Ala), Ensembl rs1782716403, REVEL 0.17, CADD 20.30
- T27K (p.Thr27Lys), TOPMed rs1782716201, REVEL 0.18, CADD 22.90
- N28S (p.Asn28Ser), ExAC rs777711910, gnomAD rs777711910, REVEL 0.17, CADD 19.30
- V29D (p.Val29Asp), ExAC rs752895151, gnomAD rs752895151, REVEL 0.13, CADD 22.00
- V29I (p.Val29Ile), cosmic curated COSV10584
- V29L (p.Val29Leu), cosmic curated COSV10584
- R30M (p.Arg30Met), cosmic curated COSV54154
- R32G (p.Arg32Gly), ExAC rs750167942, gnomAD rs750167942, REVEL 0.37, CADD 26.90
- R32I (p.Arg32Ile), NCI-TCGA Cosmic COSV5415, REVEL 0.41, CADD 32.00, Variant assessed as somatic; moderate impact.
- K33Q (p.Lys33Gln), cosmic curated COSV54137
- F34I (p.Phe34Ile), cosmic curated COSV54140
- F34L (p.Phe34Leu), NCI-TCGA Cosmic COSV5413, NCI-TCGA Cosmic COSV9962, cosmic curated COSV54138, REVEL 0.10, CADD 23.30, Variant assessed as somatic; moderate impact.
- F34Y (p.Phe34Tyr), TOPMed rs1782714540
- N36D (p.Asn36Asp), NCI-TCGA Cosmic COSV5415, cosmic curated COSV54151, Variant assessed as somatic; moderate impact.
- N36S (p.Asn36Ser), gnomAD rs1782714424, REVEL 0.14, CADD 23.90
- R37G (p.Arg37Gly), TOPMed rs1782714207, REVEL 0.13, CADD 23.60
- R37S (p.Arg37Ser), cosmic curated COSV54154, ESP rs374496805, ExAC rs374496805
- D38G (p.Asp38Gly), rs761586548, ClinGen CA4167221, ClinVar RCV004383128, ExAC rs761586548, REVEL 0.17, CADD 23.40, Uncertain significance, not specified
- D38N (p.Asp38Asn), rs972620421, ClinGen CA154005924, cosmic curated COSV10637, ClinVar RCV004227204, REVEL 0.27, CADD 29.10, Uncertain significance, not specified
- D38Y (p.Asp38Tyr), NCI-TCGA TCGA novel, gnomAD rs972620421, Uncertain significance
- L39M (p.Leu39Met), NCI-TCGA Cosmic COSV5413, cosmic curated COSV54139, Variant assessed as somatic; moderate impact.
- A40G (p.Ala40Gly), rs1397294224, ClinGen CA366870629, ClinVar RCV004290262, TOPMed rs1397294224, REVEL 0.33, CADD 32.00, Uncertain significance, not specified
- A40S (p.Ala40Ser), TOPMed rs939052748
- H41Q (p.His41Gln), TOPMed rs1334696169, gnomAD rs1334696169, REVEL 0.11, CADD 21.50
- E44K (p.Glu44Lys), cosmic curated COSV54151
- E45D (p.Glu45Asp), Ensembl rs1782580999, REVEL 0.12, CADD 23.10
- E45K (p.Glu45Lys), gnomAD rs1782712186, REVEL 0.34, CADD 36.00
- E45V (p.Glu45Val), ExAC rs771177778, gnomAD rs771177778, REVEL 0.52, CADD 33.00
- Q48* (p.Gln48Ter), NCI-TCGA Cosmic COSV9962, cosmic curated COSV99623, Variant assessed as somatic; high impact.
- Q48K (p.Gln48Lys), gnomAD rs1782580479, REVEL 0.46, CADD 31.00
- D49N (p.Asp49Asn), Ensembl rs1782580079
- D49V (p.Asp49Val), ExAC rs773621570, gnomAD rs773621570, REVEL 0.69, CADD 32.00
- D49Y (p.Asp49Tyr), NCI-TCGA Cosmic COSV5414, cosmic curated COSV54144, Variant assessed as somatic; moderate impact.
- L50I (p.Leu50Ile), cosmic curated COSV54150, gnomAD rs1782579541, REVEL 0.40, CADD 28.50
- L50R (p.Leu50Arg), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- Q52* (p.Gln52Ter), cosmic curated COSV54147
- Q52E (p.Gln52Glu), cosmic curated COSV54139
- Q52H (p.Gln52His), ExAC rs772517181, TOPMed rs772517181, gnomAD rs772517181, REVEL 0.23, CADD 22.40
- Q52R (p.Gln52Arg), cosmic curated COSV10584, Ensembl rs945739812, REVEL 0.41, CADD 26.70
- Q54K (p.Gln54Lys), cosmic curated COSV54145
- E55K (p.Glu55Lys), Ensembl rs2128514156, REVEL 0.52, CADD 29.90
- E55Q (p.Glu55Gln), NCI-TCGA Cosmic COSV5414, cosmic curated COSV54142, Variant assessed as somatic; moderate impact.
- E55V (p.Glu55Val), cosmic curated COSV54149
- T56A (p.Thr56Ala), TOPMed rs1782578744, REVEL 0.18, CADD 22.10
- T56I (p.Thr56Ile), ExAC rs748240043, gnomAD rs748240043, REVEL 0.29, CADD 22.90
- T56K (p.Thr56Lys), ExAC rs748240043, gnomAD rs748240043, REVEL 0.36, CADD 28.40
- W57* (p.Trp57Ter), gnomAD rs1265128802, CADD 39.00
- W57G (p.Trp57Gly), ExAC rs768930207, gnomAD rs768930207, REVEL 0.74, CADD 33.00
- L58F (p.Leu58Phe), gnomAD rs1209187179, REVEL 0.36, CADD 29.00
- L58R (p.Leu58Arg), cosmic curated COSV10959
- A59G (p.Ala59Gly), cosmic curated COSV10959
- E60D (p.Glu60Asp), cosmic curated COSV99623
- E60K (p.Glu60Lys), NCI-TCGA Cosmic COSV5415, cosmic curated COSV54150, REVEL 0.43, CADD 32.00, Variant assessed as somatic; moderate impact.
- A61T (p.Ala61Thr), cosmic curated COSV54149, REVEL 0.23, CADD 36.00
- Q62E (p.Gln62Glu), ExAC rs376325638, gnomAD rs376325638, REVEL 0.27, CADD 25.00, Uncertain significance, not specified
- V63L (p.Val63Leu), Ensembl rs2128501358, REVEL 0.27, CADD 25.40
- P64H (p.Pro64His), gnomAD rs1283182375, REVEL 0.47, CADD 30.00
- P64S (p.Pro64Ser), TOPMed rs1377461633, gnomAD rs1377461633, REVEL 0.43, CADD 27.90
- P64T (p.Pro64Thr), TOPMed rs1377461633, gnomAD rs1377461633, REVEL 0.46, CADD 27.40
- D65E (p.Asp65Glu), rs1295869839, ClinGen CA366865803, ClinVar RCV004366186, gnomAD rs1295869839, REVEL 0.29, CADD 26.30, Uncertain significance, not specified
- D65H (p.Asp65His), gnomAD rs1341827936, REVEL 0.48, CADD 27.50
- D65N (p.Asp65Asn), gnomAD rs1341827936, REVEL 0.43, CADD 30.00
- N66S (p.Asn66Ser), Ensembl rs1781566261, REVEL 0.11, CADD 18.90
- D67E (p.Asp67Glu), rs1583875334, ClinGen CA366865762, ClinVar RCV004383129, TOPMed rs1583875334, REVEL 0.23, CADD 22.80, Uncertain significance, not specified
- E68D (p.Glu68Asp), cosmic curated COSV10453, REVEL 0.32, CADD 24.60
- E68K (p.Glu68Lys), gnomAD rs1399298408
- Q69* (p.Gln69Ter), TOPMed rs1193052352, gnomAD rs1193052352, CADD 45.00
- V71I (p.Val71Ile), cosmic curated COSV10806, REVEL 0.24, CADD 25.30
- V71L (p.Val71Leu), TOPMed rs1403337828, gnomAD rs1403337828, REVEL 0.28, CADD 25.60, Uncertain significance, not specified
- D73H (p.Asp73His), gnomAD rs1412813233, REVEL 0.43, CADD 28.40
- Y74* (p.Tyr74Ter), ExAC rs768811949, gnomAD rs768811949
- Y74N (p.Tyr74Asn), TOPMed rs985561471
- Q75E (p.Gln75Glu), cosmic curated COSV54138, REVEL 0.23, CADD 22.60
- A76T (p.Ala76Thr), gnomAD rs1781563495, REVEL 0.12, CADD 21.00
- E77K (p.Glu77Lys), cosmic curated COSV54150, TOPMed rs1435454184, REVEL 0.30, CADD 31.00
- S78I (p.Ser78Ile), NCI-TCGA Cosmic COSV5413, Variant assessed as somatic; moderate impact.
- S78N (p.Ser78Asn), cosmic curated COSV54137, REVEL 0.20, CADD 17.50
- L79F (p.Leu79Phe), cosmic curated COSV10941, gnomAD rs1487823864, REVEL 0.32, CADD 27.20
- L79M (p.Leu79Met), cosmic curated COSV54152
- A80G (p.Ala80Gly), TOPMed rs1247959899, REVEL 0.13, CADD 23.60
- A80S (p.Ala80Ser), gnomAD rs1246463552, REVEL 0.10, CADD 22.70
- A80V (p.Ala80Val), TOPMed rs1247959899, REVEL 0.18, CADD 22.70
- F81L (p.Phe81Leu), ExAC rs749235215, gnomAD rs749235215, REVEL 0.18, CADD 22.30
- F81V (p.Phe81Val), NCI-TCGA Cosmic COSV5415, cosmic curated COSV54152, Variant assessed as somatic; moderate impact.
- H82R (p.His82Arg), cosmic curated COSV54140, REVEL 0.66, CADD 25.60
- G83A (p.Gly83Ala), TOPMed rs1583710223
- G83S (p.Gly83Ser), cosmic curated COSV54148
- P85Q (p.Pro85Gln), TOPMed rs1217388375, gnomAD rs1217388375, REVEL 0.27, CADD 23.90
- P85S (p.Pro85Ser), gnomAD rs1302857335, REVEL 0.37, CADD 26.60
- L86R (p.Leu86Arg), TOPMed rs1787185749
- L86V (p.Leu86Val), Ensembl rs1787186241
- I88M (p.Ile88Met), cosmic curated COSV54139, Ensembl rs1787184914, REVEL 0.26, CADD 24.80
- K89N (p.Lys89Asn), cosmic curated COSV10959, cosmic curated COSV54139
- K89R (p.Lys89Arg), cosmic curated COSV54151, gnomAD rs1280099827
- P92H (p.Pro92His), cosmic curated COSV10453
- P92L (p.Pro92Leu), cosmic curated COSV54149
- P92T (p.Pro92Thr), TOPMed rs1787183628, REVEL 0.31, CADD 23.80
- S94G (p.Ser94Gly), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- P95S (p.Pro95Ser), TOPMed rs1787182209, gnomAD rs1787182209, REVEL 0.55, CADD 24.20
- C96F (p.Cys96Phe), ExAC rs769910514, TOPMed rs769910514, gnomAD rs769910514, REVEL 0.36, CADD 22.90
- C96R (p.Cys96Arg), 1000Genomes rs2128459518, REVEL 0.29, CADD 23.30
- C96W (p.Cys96Trp), NCI-TCGA Cosmic COSV5415, cosmic curated COSV54150, Variant assessed as somatic; moderate impact.
- S97P (p.Ser97Pro), ESP rs371614424, ExAC rs371614424, TOPMed rs371614424, gnomAD rs371614424, REVEL 0.22, CADD 24.40
- E98K (p.Glu98Lys), cosmic curated COSV10806, gnomAD rs1359804481, REVEL 0.32, CADD 23.90
- I99M (p.Ile99Met), cosmic curated COSV54152
- I99V (p.Ile99Val), ExAC rs758881224, gnomAD rs758881224, REVEL 0.09, CADD 16.10
- S100C (p.Ser100Cys), 1000Genomes rs9639168, ESP rs9639168, ExAC rs9639168, TOPMed rs9639168
- S100G (p.Ser100Gly), rs9639168, cosmic curated COSV54136, UniProt VAR 048948, 1000Genomes rs9639168, REVEL 0.14, CADD 15.60
- S100I (p.Ser100Ile), Ensembl rs1787178444
- S100R (p.Ser100Arg), TOPMed rs1442372291, gnomAD rs1442372291, REVEL 0.14, CADD 15.10, Uncertain significance, not specified
- A102V (p.Ala102Val), cosmic curated COSV54143
- S104T (p.Ser104Thr), Ensembl rs1562649064
- Q105E (p.Gln105Glu), ExAC rs753912647, gnomAD rs753912647, REVEL 0.20, CADD 23.40
- Q105H (p.Gln105His), cosmic curated COSV54146, gnomAD rs1197619453, REVEL 0.19, CADD 16.60
- E106* (p.Glu106Ter), NCI-TCGA Cosmic COSV5413, NCI-TCGA Cosmic COSV5414, cosmic curated COSV54149, CADD 42.00, Variant assessed as somatic; high impact.
- E106D (p.Glu106Asp), ExAC rs766711230, gnomAD rs766711230
- E106G (p.Glu106Gly), TOPMed rs1257214692, gnomAD rs1257214692, REVEL 0.41, CADD 27.20
- E106K (p.Glu106Lys), cosmic curated COSV54137
- E106Q (p.Glu106Gln), rs936225135, NCI-TCGA Cosmic COSV5413, NCI-TCGA Cosmic COSV5414, TOPMed rs936225135, REVEL 0.24, CADD 25.10, Variant assessed as somatic; moderate impact.
- Q107* (p.Gln107Ter), NCI-TCGA Cosmic COSV5415, cosmic curated COSV54150, Variant assessed as somatic; high impact.
- Q107E (p.Gln107Glu), gnomAD rs1787173565, REVEL 0.17, CADD 24.20, Uncertain significance, not specified
- Q107R (p.Gln107Arg), TOPMed rs1583709631
- P108H (p.Pro108His), TOPMed rs1374621781, REVEL 0.23, CADD 25.80
- P108L (p.Pro108Leu), cosmic curated COSV54153
- P108T (p.Pro108Thr), TOPMed rs1787173033
- F109C (p.Phe109Cys), Ensembl rs2128459439
- F109L (p.Phe109Leu), TOPMed rs943501720, gnomAD rs943501720, REVEL 0.26, CADD 16.20
- K110I (p.Lys110Ile), Ensembl rs1787171846, REVEL 0.23, CADD 24.00
- F111L (p.Phe111Leu), ExAC rs774071237, TOPMed rs774071237, gnomAD rs774071237, REVEL 0.11, CADD 21.90
- S112G (p.Ser112Gly), gnomAD rs1308339889
- S112I (p.Ser112Ile), TOPMed rs1446300469, gnomAD rs1446300469
- S112T (p.Ser112Thr), TOPMed rs1446300469, gnomAD rs1446300469, REVEL 0.11, CADD 18.60
- Y113H (p.Tyr113His), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- G114* (p.Gly114Ter), cosmic curated COSV10584
- G114A (p.Gly114Ala), rs762835509, NCI-TCGA Cosmic COSV9962, cosmic curated COSV99622, ExAC rs762835509, REVEL 0.46, CADD 23.70, Variant assessed as somatic; moderate impact.
- G114R (p.Gly114Arg), ExAC rs768475054, gnomAD rs768475054, REVEL 0.46, CADD 26.70
- E115K (p.Glu115Lys), cosmic curated COSV10502
- K116N (p.Lys116Asn), rs775525239, ClinGen CA4167102, cosmic curated COSV54141, ClinVar RCV004383130, REVEL 0.19, CADD 25.80, Uncertain significance, not specified
- K116Q (p.Lys116Gln), Ensembl rs1787169348, REVEL 0.16, CADD 22.10
- C117* (p.Cys117Ter), cosmic curated COSV54146
- C117F (p.Cys117Phe), ExAC rs1131845, gnomAD rs1131845, REVEL 0.52, CADD 25.80
- C117Y (p.Cys117Tyr), cosmic curated COSV10878, ExAC rs1131845, gnomAD rs1131845, REVEL 0.56, CADD 25.80
- L118P (p.Leu118Pro), cosmic curated COSV54147
- L118R (p.Leu118Arg), NCI-TCGA Cosmic COSV5414, Variant assessed as somatic; high impact.
- L118V (p.Leu118Val), ExAC rs780679319, TOPMed rs780679319, gnomAD rs780679319, REVEL 0.18, CADD 26.10
- Y119* (p.Tyr119Ter), cosmic curated COSV54148, gnomAD rs1424792522, CADD 38.00
- Y119C (p.Tyr119Cys), ESP rs368739038, ExAC rs368739038, TOPMed rs368739038, gnomAD rs368739038, REVEL 0.49, CADD 27.90
- Y119H (p.Tyr119His), TOPMed rs1288074041, gnomAD rs1288074041, REVEL 0.46, CADD 27.40
- Y119S (p.Tyr119Ser), ESP rs368739038, ExAC rs368739038, TOPMed rs368739038, gnomAD rs368739038
- N120S (p.Asn120Ser), ExAC rs746647484, gnomAD rs746647484, REVEL 0.03, CADD 15.20
- A123T (p.Ala123Thr), ExAC rs779138336, TOPMed rs779138336, gnomAD rs779138336, REVEL 0.14, CADD 35.00, Uncertain significance, not specified
Public ETV1 analysis runs
- ETV1 analysis run — ETV1 (939 variants) — completed 2026-08-22