COL7A1 (Collagen alpha-1(VII) chain) variants and mutations

COL7A1 (also known as Collagen alpha-1(VII) chain) is a human protein-coding gene encoding a collagen alpha-1(VII) chain protein. It forms anchoring fibrils that secure the epidermal basement membrane to the underlying dermis. Pathogenic variants cause dystrophic epidermolysis bullosa, with skin fragility and scarring ranging from localized disease to severe generalized forms with major complications. This analysis covers 4,078 COL7A1 variants and mutations. Of these, 74% have computational variant effect predictions. Disease context includes recessive dystrophic epidermolysis bullosa, generalized dominant dystrophic epidermolysis bullosa, and dystrophic epidermolysis bullosa pruriginosa. Example COL7A1 variants include M1I, M1R, and M1V.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, gnomAD constraint, Open Targets, ClinGen, MaveDB, LitVar.

Notable COL7A1 variants

Examples include M1I, M1R, M1V, T2M, T2S, R4Q, R4W, L5F. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.