G827R (p.Gly827Arg) variant of COL4A3 (Collagen alpha-3(IV) chain)

G827R (p.Gly827Arg) in COL4A3 (Collagen alpha-3(IV) chain) is a missense change. Clinical records from ClinVar and UniProt describe it as likely pathogenic in the context of Alport syndrome; Hematuria. The available variant effect predictions contribute to a CATVariant prioritization score of 0.90 / 1. The record also includes population frequency data and structural context.

G827R (p.Gly827Arg) variant details