COL2A1 (Collagen alpha-1(II) chain) variants and mutations

COL2A1 (also known as Collagen alpha-1(II) chain) is a human protein-coding gene encoding a collagen alpha-1(II) chain protein. It provides the principal fibrillar collagen framework of cartilage and is also important in the vitreous and inner ear. Pathogenic variants cause a broad type II collagenopathy spectrum including Stickler syndrome, spondyloepiphyseal dysplasia, and severe skeletal dysplasias. This analysis covers 2,467 COL2A1 variants and mutations. Of these, 74% have computational variant effect predictions. Disease context includes spondyloepiphyseal dysplasia congenita, Stickler syndrome type 1, and achondrogenesis type II. Example COL2A1 variants include M1L, M1V, and R3C.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, AlphaFold DB, gnomAD constraint, Open Targets, ClinGen, MaveDB, LitVar.

Notable COL2A1 variants

Examples include M1L, M1V, R3C, R3G, R3H, R3L, R3S, L4P. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.