BACH2 (Q9BYV9) variants and mutations
BACH2 (also known as Q9BYV9) is a human protein-coding gene encoding a transcription regulator protein. It controls transcriptional programs that balance lymphocyte differentiation, immune tolerance, and effector-cell development. Haploinsufficiency can cause immunodeficiency with autoimmunity, and common variation influences susceptibility to several autoimmune diseases. This analysis covers 1,427 BACH2 variants and mutations. Of these, 69% have computational variant effect predictions. Disease context includes immunodeficiency 60, asthma, and inflammatory bowel disease. Example BACH2 variants include D4E, D4G, and D4V.
Variant analysis overview
- Gene: BACH2
- Protein: Q9BYV9
- UniProt accession: Q9BYV9
- Organism: Homo sapiens
- Variants analyzed: 1427
- Variant scope: all variants
- Completed: 2026-08-20
Variant and mutation evidence
- Variant composition: 1,058 unspecified-consequence records; 1 stop retained variant; 198 synonymous variants; 155 missense variants; 7 frameshift variants; 1 in-frame insertions; 2 splice-region variants; 2 stop-gained variants; 3 in-frame deletions
- Prediction scores: 978 variants have prediction scores (69% of the analyzed set).
Clinical, disease, and population context
- Disease context: 25 disease associations are represented. Top associations: immunodeficiency 60, asthma, inflammatory bowel disease, hypothyroidism, type 1 diabetes mellitus, skin cancer, skin neoplasm, basal cell carcinoma, thyroid gland disorder, Hashimoto thyroiditis, autoimmune disease, Graves disease.
Protein structure and variant hotspots
- Protein features: 2 domains; 2 post-translational modification sites.
- Structural context: 199 variants have structural context.
- PTM context: 2 variants overlap post-translational modification sites.
Data sources
Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, MaveDB, LitVar.
Notable BACH2 variants
Examples include D4E, D4G, D4V, D4Y, E5K, K6N, P7S, D8N. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.
- D4E (p.Asp4Glu), Ensembl rs769138899
- D4G (p.Asp4Gly), TOPMed rs1419275988, gnomAD rs1419275988, REVEL 0.31, CADD 28.30
- D4V (p.Asp4Val), TOPMed rs1419275988, gnomAD rs1419275988, REVEL 0.36, CADD 27.40
- D4Y (p.Asp4Tyr), gnomAD rs1460440753, REVEL 0.32, CADD 25.90, Uncertain significance, not provided
- E5K (p.Glu5Lys), NCI-TCGA Cosmic COSV5760, cosmic curated COSV57601, Variant assessed as somatic; moderate impact.
- K6N (p.Lys6Asn), gnomAD rs1427184506
- P7S (p.Pro7Ser), rs2127780699, ClinGen CA365069704, ClinVar RCV001900185, Ensembl rs2127780699, AlphaMissense 0.08, MetaLR 0.03, Uncertain significance, not provided
- D8N (p.Asp8Asn), cosmic curated COSV57592
- S9F (p.Ser9Phe), gnomAD rs1261481591, REVEL 0.31, CADD 26.50
- P10S (p.Pro10Ser), rs2533639327, ClinGen CA365069671, ClinVar RCV003046672, Uncertain significance, not provided
- M11L (p.Met11Leu), rs1432967879, cosmic curated COSV57610, ClinGen CA365069662, ClinVar RCV001894380, AlphaMissense 0.17, MetaLR 0.03, Uncertain significance, not provided
- M11V (p.Met11Val), TOPMed rs1432967879, REVEL 0.33, AlphaMissense 0.17, Uncertain significance
- E15Q (p.Glu15Gln), NCI-TCGA Cosmic COSV5759, cosmic curated COSV57596, Variant assessed as somatic; moderate impact.
- S16F (p.Ser16Phe), cosmic curated COSV10508
- S16T (p.Ser16Thr), NCI-TCGA Cosmic COSV1000, cosmic curated COSV10000, Variant assessed as somatic; moderate impact.
- C20S (p.Cys20Ser), Ensembl rs1777547310, REVEL 0.34, CADD 23.10
- T21A (p.Thr21Ala), rs2533639266, ClinGen CA365069543, ClinVar RCV002686054, REVEL 0.03, CADD 15.00, Uncertain significance, not provided
- L24F (p.Leu24Phe), cosmic curated COSV57609, cosmic curated COSV10508
- L24P (p.Leu24Pro), rs1562364898, ClinGen CA365069503, ClinVar RCV000767852, Ensembl rs1562364898, AlphaMissense 1.00, MetaLR 0.30, Pathogenic, Immunodeficiency 60
- L25M (p.Leu25Met), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- N28D (p.Asn28Asp), 1000Genomes rs184583433, ExAC rs184583433, gnomAD rs184583433, REVEL 0.60, CADD 23.90
- N28S (p.Asn28Ser), NCI-TCGA TCGA novel, TOPMed rs1777545909, Uncertain significance, not specified
- R31Q (p.Arg31Gln), rs1777545442, ClinGen CA365069432, NCI-TCGA Cosmic COSV5758, cosmic curated COSV57584, REVEL 0.46, CADD 28.00, Uncertain significance, not provided
- R31W (p.Arg31Trp), cosmic curated COSV57605, ExAC rs746587410, gnomAD rs746587410, REVEL 0.36, CADD 25.80
- K32N (p.Lys32Asn), cosmic curated COSV57601
- D34N (p.Asp34Asn), rs779790057, ClinGen CA3928231, ClinVar RCV002003576, ClinVar RCV005626575, REVEL 0.22, CADD 26.80, Uncertain significance, Autosomal recessive congenital ichthyosis; Immunodeficiency 60; not provided
- L36I (p.Leu36Ile), cosmic curated COSV57588
- C37Y (p.Cys37Tyr), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- D38N (p.Asp38Asn), cosmic curated COSV57586
- V39A (p.Val39Ala), Ensembl rs1777544808
- V39L (p.Val39Leu), cosmic curated COSV57591
- V39M (p.Val39Met), NCI-TCGA Cosmic COSV5759, NCI-TCGA Cosmic COSV5761, cosmic curated COSV57611, Variant assessed as somatic; moderate impact.
- T40N (p.Thr40Asn), NCI-TCGA Cosmic COSV9999, cosmic curated COSV99999, Variant assessed as somatic; moderate impact.
- I42V (p.Ile42Val), rs758086634, ClinGen CA3928230, ClinVar RCV003872633, ExAC rs758086634, REVEL 0.09, CADD 21.00, Uncertain significance, not provided
- V43M (p.Val43Met), rs1460936502, NCI-TCGA Cosmic COSV5759, cosmic curated COSV57599, gnomAD rs1460936502, REVEL 0.47, CADD 26.00, Variant assessed as somatic; moderate impact.
- R45K (p.Arg45Lys), ESP rs144485006, ExAC rs144485006, TOPMed rs144485006, gnomAD rs144485006, REVEL 0.06, CADD 22.00
- K46N (p.Lys46Asn), ExAC rs753759917, gnomAD rs753759917, REVEL 0.41, CADD 24.90, Likely benign
- E47A (p.Glu47Ala), rs1777543091, ClinGen CA365069241, ClinVar RCV004327097, TOPMed rs1777543091, REVEL 0.48, CADD 27.60, Uncertain significance, not specified
- E47K (p.Glu47Lys), ExAC rs764083605, gnomAD rs764083605, REVEL 0.37, CADD 25.90
- F48I (p.Phe48Ile), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- F48L (p.Phe48Leu), NCI-TCGA Cosmic COSV5758, cosmic curated COSV57585, Variant assessed as somatic; moderate impact.
- R49P (p.Arg49Pro), rs2533639178, ClinGen CA365069210, ClinVar RCV003543985, Uncertain significance, not provided
- R49Q (p.Arg49Gln), cosmic curated COSV57590, REVEL 0.49, CADD 27.10
- R49W (p.Arg49Trp), cosmic curated COSV57586
- R52L (p.Arg52Leu), NCI-TCGA Cosmic COSV5760, Variant assessed as somatic; moderate impact.
- R52Q (p.Arg52Gln), cosmic curated COSV57600, Ensembl rs2127780658, REVEL 0.49, CADD 27.00
- R52W (p.Arg52Trp), TOPMed rs747200186, gnomAD rs747200186, REVEL 0.67, CADD 29.50, Likely benign
- A53P (p.Ala53Pro), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- A53V (p.Ala53Val), NCI-TCGA Cosmic COSV5760, cosmic curated COSV57604, Variant assessed as somatic; moderate impact.
- V54A (p.Val54Ala), cosmic curated COSV57584
- A56V (p.Ala56Val), rs1469024903, NCI-TCGA Cosmic COSV5759, cosmic curated COSV57598, gnomAD rs1469024903, REVEL 0.79, CADD 27.10, Variant assessed as somatic; moderate impact.
- A57S (p.Ala57Ser), ExAC rs766462405, TOPMed rs766462405, gnomAD rs766462405, REVEL 0.38, CADD 24.70
- A57V (p.Ala57Val), cosmic curated COSV99998
- Y61C (p.Tyr61Cys), NCI-TCGA Cosmic COSV9999, cosmic curated COSV99999, Variant assessed as somatic; moderate impact.
- F62I (p.Phe62Ile), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- W63C (p.Trp63Cys), TOPMed rs1777540721, gnomAD rs1777540721, REVEL 0.21, CADD 26.00, Uncertain significance, not provided
- Q64H (p.Gln64His), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- Q64R (p.Gln64Arg), ExAC rs763268377, gnomAD rs763268377, REVEL 0.52, CADD 23.60
- A65G (p.Ala65Gly), NCI-TCGA Cosmic COSV1000, cosmic curated COSV10000, NCI-TCGA Cosmic COSV5758, Variant assessed as somatic; moderate impact.
- A65T (p.Ala65Thr), gnomAD rs1777540345, REVEL 0.19, CADD 22.20
- A65V (p.Ala65Val), rs1250663291, NCI-TCGA Cosmic COSV1000, NCI-TCGA Cosmic COSV5758, cosmic curated COSV57586, REVEL 0.07, CADD 21.90, Variant assessed as somatic; moderate impact.
- V67A (p.Val67Ala), TOPMed rs1300893800, gnomAD rs1300893800, REVEL 0.08, CADD 22.10
- V67I (p.Val67Ile), ExAC rs748584222, gnomAD rs748584222, REVEL 0.14, CADD 19.90
- G68E (p.Gly68Glu), cosmic curated COSV57601, Ensembl rs45509798, REVEL 0.37, CADD 25.00
- G68R (p.Gly68Arg), NCI-TCGA Cosmic COSV5760, cosmic curated COSV57603, Variant assessed as somatic; moderate impact.
- Q69H (p.Gln69His), cosmic curated COSV57595, ExAC rs777275715, gnomAD rs777275715, REVEL 0.25, CADD 22.30
- Q69P (p.Gln69Pro), cosmic curated COSV57604
- T70A (p.Thr70Ala), gnomAD rs1371210319, REVEL 0.06, CADD 20.20
- N72S (p.Asn72Ser), Ensembl rs1777538231, Uncertain significance
- N72T (p.Asn72Thr), rs1777538231, ClinGen CA365068978, ClinVar RCV003431957, Ensembl rs1777538231, REVEL 0.15, CADD 21.70, Uncertain significance, not provided
- S77N (p.Ser77Asn), TOPMed rs1302804378, gnomAD rs1302804378, REVEL 0.10, CADD 23.10, Uncertain significance
- S77T (p.Ser77Thr), rs1302804378, ClinGen CA365068942, ClinVar RCV003829931, ClinVar RCV004366826, REVEL 0.14, CADD 17.40, Uncertain significance, not specified; not provided
- L78V (p.Leu78Val), NCI-TCGA Cosmic COSV5759, cosmic curated COSV57591, Variant assessed as somatic; moderate impact.
- E80D (p.Glu80Asp), rs746464663, ClinGen CA365068918, ClinVar RCV001891398, ExAC rs746464663, AlphaMissense 0.18, MetaLR 0.06, Uncertain significance, not provided
- E80K (p.Glu80Lys), NCI-TCGA Cosmic COSV5758, cosmic curated COSV57584, NCI-TCGA Cosmic COSV9999, Variant assessed as somatic; moderate impact.
- E80Q (p.Glu80Gln), NCI-TCGA Cosmic COSV5758, NCI-TCGA Cosmic COSV9999, cosmic curated COSV99998, Variant assessed as somatic; moderate impact.
- E81D (p.Glu81Asp), cosmic curated COSV57602
- E81K (p.Glu81Lys), ExAC rs779642556, gnomAD rs779642556, REVEL 0.39, CADD 23.60
- V82F (p.Val82Phe), NCI-TCGA Cosmic COSV5760, cosmic curated COSV57607, Variant assessed as somatic; moderate impact.
- A84V (p.Ala84Val), gnomAD rs1473547695, REVEL 0.11, CADD 20.90
- R85K (p.Arg85Lys), rs775887547, ClinGen CA3928195, ClinVar RCV002908305, ClinVar RCV004887700, REVEL 0.24, CADD 19.00, Uncertain significance, not provided; not specified
- R85S (p.Arg85Ser), cosmic curated COSV10000
- R85T (p.Arg85Thr), rs775887547, ClinGen CA3928196, ClinVar RCV003732779, ClinVar RCV006382123, REVEL 0.40, CADD 25.30, Uncertain significance, not specified; not provided
- G86D (p.Gly86Asp), NCI-TCGA Cosmic COSV5760, TOPMed rs1774147125, Variant assessed as somatic; moderate impact.
- G86V (p.Gly86Val), cosmic curated COSV57600
- F87L (p.Phe87Leu), NCI-TCGA TCGA novel, Variant assessed as somatic; high impact.
- G88A (p.Gly88Ala), NCI-TCGA Cosmic COSV5761, NCI-TCGA Cosmic COSV9999, cosmic curated COSV99999, Variant assessed as somatic; moderate impact.
- G88E (p.Gly88Glu), cosmic curated COSV57611, TOPMed rs1774146822
- G88R (p.Gly88Arg), cosmic curated COSV57611
- G88V (p.Gly88Val), TOPMed rs1774146822
- P89L (p.Pro89Leu), gnomAD rs1442773915
- P89Q (p.Pro89Gln), cosmic curated COSV57599
- L91* (p.Leu91Ter), NCI-TCGA TCGA novel, Variant assessed as somatic; high impact.
- L91I (p.Leu91Ile), TOPMed rs1774145624
- Q92K (p.Gln92Lys), Ensembl rs1023239312
- Y95C (p.Tyr95Cys), cosmic curated COSV57589, Ensembl rs1774144945, REVEL 0.95, CADD 28.60
- T96A (p.Thr96Ala), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- K98N (p.Lys98Asn), cosmic curated COSV57592
- L100S (p.Leu100Ser), ExAC rs372470918, gnomAD rs372470918
- S102G (p.Ser102Gly), cosmic curated COSV10723
- S102N (p.Ser102Asn), rs2533568352, ClinGen CA365073326, ClinVar RCV003845792, Uncertain significance, not provided
- R103K (p.Arg103Lys), cosmic curated COSV10585, TOPMed rs1184528807, gnomAD rs1184528807, REVEL 0.07, CADD 20.60
- R103S (p.Arg103Ser), rs2533568343, ClinGen CA365073315, ClinVar RCV003693022, Uncertain significance, not provided
- E104D (p.Glu104Asp), NCI-TCGA Cosmic COSV9999, cosmic curated COSV99998, Variant assessed as somatic; moderate impact.
- N105T (p.Asn105Thr), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- I106M (p.Ile106Met), Ensembl rs1381216647
- R107C (p.Arg107Cys), ExAC rs531266975, TOPMed rs531266975, gnomAD rs531266975, REVEL 0.29, CADD 29.80, Uncertain significance, not provided
- R107H (p.Arg107His), rs749061519, ClinGen CA3928190, NCI-TCGA Cosmic COSV5758, cosmic curated COSV57588, REVEL 0.20, CADD 22.80, Uncertain significance, not provided
- E108K (p.Glu108Lys), cosmic curated COSV57601
- I110V (p.Ile110Val), gnomAD rs1449293089, REVEL 0.24, CADD 21.20
- R111C (p.Arg111Cys), NCI-TCGA Cosmic COSV5760, cosmic curated COSV57609, REVEL 0.55, CADD 26.50, Variant assessed as somatic; moderate impact.
- R111H (p.Arg111His), rs150524925, ClinGen CA3928186, ClinVar RCV002036290, ClinVar RCV004044791, REVEL 0.12, CADD 22.50, Uncertain significance, not provided; not specified
- R111L (p.Arg111Leu), ESP rs150524925, ExAC rs150524925, TOPMed rs150524925, gnomAD rs150524925, REVEL 0.27, CADD 23.70, Uncertain significance
- C112F (p.Cys112Phe), NCI-TCGA Cosmic COSV5758, cosmic curated COSV57584, Variant assessed as somatic; moderate impact.
- E114Q (p.Glu114Gln), rs2533568247, ClinGen CA365073246, ClinVar RCV003561628, Uncertain significance, not provided
- F115L (p.Phe115Leu), NCI-TCGA Cosmic COSV5759, cosmic curated COSV57596, TOPMed rs1774139691, gnomAD rs1774139691, REVEL 0.20, CADD 22.10, Variant assessed as somatic; moderate impact.
- R117C (p.Arg117Cys), cosmic curated COSV57608, REVEL 0.61, CADD 31.00
- R117H (p.Arg117His), rs1774139493, ClinGen CA365073221, ClinVar RCV002672139, Ensembl rs1774139493, REVEL 0.19, CADD 22.80, Uncertain significance, not provided
- N120T (p.Asn120Thr), cosmic curated COSV57602, REVEL 0.47, CADD 26.90
- E122D (p.Glu122Asp), cosmic curated COSV10000
- D123A (p.Asp123Ala), 1000Genomes rs200626236, ExAC rs200626236, gnomAD rs200626236
- S124A (p.Ser124Ala), gnomAD rs1473047103, REVEL 0.41, CADD 26.80
- S124P (p.Ser124Pro), gnomAD rs1473047103, REVEL 0.78, CADD 28.70
- F126L (p.Phe126Leu), Ensembl rs993582784, REVEL 0.41, CADD 25.10, Uncertain significance, not provided
- L129M (p.Leu129Met), cosmic curated COSV10000
- Q130* (p.Gln130Ter), NCI-TCGA Cosmic COSV5761, cosmic curated COSV57612, Variant assessed as somatic; high impact.
- Q130E (p.Gln130Glu), ExAC rs776001544, gnomAD rs776001544, REVEL 0.09, CADD 18.50, Uncertain significance
- Q130K (p.Gln130Lys), rs776001544, ClinGen CA3928178, ClinVar RCV003857193, ExAC rs776001544, REVEL 0.21, CADD 21.00, Uncertain significance, not provided
- Q130R (p.Gln130Arg), TOPMed rs1161097280
- T131S (p.Thr131Ser), gnomAD rs1248228055, REVEL 0.14, CADD 22.10
- S136R (p.Ser136Arg), rs2128357100, ClinGen CA365073093, ClinVar RCV002035738, Ensembl rs2128357100, REVEL 0.11, CADD 3.35, Uncertain significance, not provided
- E137* (p.Glu137Ter), cosmic curated COSV10000
- D138N (p.Asp138Asn), NCI-TCGA Cosmic COSV1000, cosmic curated COSV10000, Variant assessed as somatic; moderate impact.
- G139D (p.Gly139Asp), NCI-TCGA Cosmic COSV9999, cosmic curated COSV99998, Variant assessed as somatic; moderate impact.
- G139S (p.Gly139Ser), TOPMed rs1374629645, gnomAD rs1374629645, REVEL 0.12, CADD 22.60, Uncertain significance, not provided
- L140V (p.Leu140Val), rs1774134869, ClinGen CA365073060, ClinVar RCV002944255, TOPMed rs1774134869, REVEL 0.12, CADD 22.70, Uncertain significance, not provided
- V142A (p.Val142Ala), NCI-TCGA Cosmic COSV5758, Variant assessed as somatic; moderate impact.
- V142E (p.Val142Glu), NCI-TCGA Cosmic COSV5758, cosmic curated COSV57589, Variant assessed as somatic; moderate impact.
- C143R (p.Cys143Arg), ExAC rs770539643, gnomAD rs770539643, REVEL 0.20, CADD 23.30
- C143S (p.Cys143Ser), ExAC rs748898352, gnomAD rs748898352, REVEL 0.19, CADD 22.60
- R144Q (p.Arg144Gln), rs142517589, ClinGen CA3928172, cosmic curated COSV99999, ClinVar RCV001896956, REVEL 0.07, CADD 19.10, Uncertain significance, not specified; not provided
- R144W (p.Arg144Trp), rs1227106751, cosmic curated COSV10723, TOPMed rs1227106751, gnomAD rs1227106751, REVEL 0.16, CADD 24.80, Uncertain significance, not provided
- K145N (p.Lys145Asn), gnomAD rs1008925614, REVEL 0.05, CADD 16.80, Uncertain significance
- D146N (p.Asp146Asn), cosmic curated COSV57593
- A147D (p.Ala147Asp), cosmic curated COSV10000
- A147T (p.Ala147Thr), ExAC rs769519112, gnomAD rs769519112, REVEL 0.06, CADD 1.16
- A147V (p.Ala147Val), cosmic curated COSV57601, gnomAD rs1393834853, REVEL 0.08, CADD 14.20
- A148G (p.Ala148Gly), TOPMed rs1265099818, gnomAD rs1265099818, REVEL 0.04, CADD 13.10
- A148T (p.Ala148Thr), TOPMed rs956897586, gnomAD rs956897586, REVEL 0.09, CADD 8.74
- A148V (p.Ala148Val), rs1265099818, NCI-TCGA Cosmic COSV9999, cosmic curated COSV99999, TOPMed rs1265099818, REVEL 0.06, CADD 12.50, Uncertain significance, not provided; Immunodeficiency 60
- C149Y (p.Cys149Tyr), rs1415826095, ClinGen CA365073002, ClinVar RCV004086271, ClinVar RCV006472854, REVEL 0.23, CADD 18.30, Uncertain significance, not specified; not provided
- Q150H (p.Gln150His), ExAC rs781182243, gnomAD rs781182243, REVEL 0.05, CADD 18.20
- Q150R (p.Gln150Arg), gnomAD rs1474948432, REVEL 0.04, CADD 13.20
- R151H (p.Arg151His), rs144637668, ClinGen CA3928168, cosmic curated COSV57584, ClinVar RCV002031796, REVEL 0.08, CADD 16.80, Uncertain significance, not provided
- R151P (p.Arg151Pro), rs144637668, ClinGen CA3928167, ClinVar RCV002202181, ClinVar RCV003950926, REVEL 0.14, CADD 16.60, Likely benign, not provided
- P152L (p.Pro152Leu), rs200976634, ClinGen CA3928166, ClinVar RCV002208761, ClinVar RCV003089104, REVEL 0.04, CADD 17.50, Uncertain significance, Immunodeficiency 60; not specified; not provided
- H153Q (p.His153Gln), cosmic curated COSV10723, REVEL 0.02, CADD 0.38
- E154D (p.Glu154Asp), TOPMed rs1245277380, Uncertain significance, not provided
- E154K (p.Glu154Lys), cosmic curated COSV57604, TOPMed rs1774128748, REVEL 0.03, CADD 8.93, Uncertain significance, not provided
- E154Q (p.Glu154Gln), TOPMed rs1774128748
- D155G (p.Asp155Gly), Ensembl rs2128357075, REVEL 0.04, CADD 15.80
- E157* (p.Glu157Ter), cosmic curated COSV99998
- E157G (p.Glu157Gly), cosmic curated COSV10508, 1000Genomes rs567759599, ExAC rs567759599, gnomAD rs567759599, REVEL 0.02, CADD 15.10
- E157K (p.Glu157Lys), rs138868869, ClinGen CA3928164, ClinVar RCV002908253, ClinVar RCV004066085, REVEL 0.11, CADD 13.70, Conflicting interpretations, not provided; not specified
- N158S (p.Asn158Ser), Ensembl rs867336129, REVEL 0.11, CADD 15.20
- N158Y (p.Asn158Tyr), gnomAD rs1271472140, REVEL 0.15, CADD 20.40
- S159F (p.Ser159Phe), cosmic curated COSV57597, REVEL 0.18, CADD 23.40
- A160P (p.Ala160Pro), ExAC rs756544902, gnomAD rs756544902, REVEL 0.03, CADD 14.20
- A160T (p.Ala160Thr), ExAC rs756544902, gnomAD rs756544902, REVEL 0.03, CADD 10.30
- A160V (p.Ala160Val), ExAC rs753062024, TOPMed rs753062024, gnomAD rs753062024, REVEL 0.03, CADD 13.50, Uncertain significance, not specified
- G161E (p.Gly161Glu), rs760001259, ClinGen CA3928159, ClinVar RCV002580197, ExAC rs760001259, REVEL 0.09, CADD 16.20, Uncertain significance, not provided
- G161R (p.Gly161Arg), cosmic curated COSV57602, REVEL 0.09, CADD 18.00
- E162A (p.Glu162Ala), rs765825161, ClinGen CA3928157, ClinVar RCV001872173, ExAC rs765825161, REVEL 0.06, CADD 19.90, Uncertain significance, not provided
- E162K (p.Glu162Lys), ExAC rs774952715, TOPMed rs774952715, gnomAD rs774952715, REVEL 0.09, AlphaMissense 0.09, Uncertain significance
- E162Q (p.Glu162Gln), rs774952715, ClinGen CA365072920, ClinVar RCV001971056, ExAC rs774952715, AlphaMissense 0.09, MetaLR 0.04, Uncertain significance, not provided
- E163D (p.Glu163Asp), cosmic curated COSV10508
- E163K (p.Glu163Lys), gnomAD rs1351596447, REVEL 0.18, CADD 22.20
- E164D (p.Glu164Asp), cosmic curated COSV57610, Uncertain significance, not provided
- D165E (p.Asp165Glu), cosmic curated COSV10585
- D165N (p.Asp165Asn), ExAC rs762461351, gnomAD rs762461351, REVEL 0.09, CADD 16.90
Public BACH2 analysis runs
- BACH2 analysis run — BACH2 (1,427 variants) — completed 2026-08-20