AVPR2 (Vasopressin V2 receptor) variants and mutations
AVPR2 (also known as Vasopressin V2 receptor) is a human protein-coding gene encoding a vasopressin V2 receptor protein. Its annotated function is g protein-coupled receptor for arginine vasopressin, an antidiuretic that promotes renal water reabsorption. It is annotated at the cell membrane. This analysis covers 872 AVPR2 variants and mutations. Of these, 76% have computational variant effect predictions. Disease context includes nephrogenic diabetes insipidus, nephrogenic syndrome of inappropriate antidiuresis, and Hyponatremia. Example AVPR2 variants include M1?, L2P, and M3I.
Variant analysis overview
- Gene: AVPR2
- Protein: Vasopressin V2 receptor
- UniProt accession: P30518
- Organism: Homo sapiens
- Variants analyzed: 872
- Variant scope: all variants
- Completed: 2026-08-28
Variant and mutation evidence
- Variant composition: 490 unspecified-consequence records; 203 missense variants; 155 synonymous variants; 2 splice-region variants; 8 in-frame deletions; 6 stop-gained variants; 3 frameshift variants; 1 stop lost; 1 stop retained variant; 5 substitution
- Prediction scores: 665 variants have prediction scores (76% of the analyzed set).
Clinical, disease, and population context
- Disease context: 25 disease associations are represented. Top associations: nephrogenic diabetes insipidus, nephrogenic syndrome of inappropriate antidiuresis, Hyponatremia, diabetes insipidus, heart failure, autosomal dominant polycystic kidney disease, hemorrhage, enuresis, hepatorenal syndrome, Nasal congestion, inappropriate ADH syndrome, Central diabetes insipidus.
Protein structure and variant hotspots
- Protein features: 7 transmembrane segments; 12 post-translational modification sites.
- Structural context: 368 variants have structural context.
- PTM context: 26 variants overlap post-translational modification sites.
Data sources
Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, Interaction Network Analysis, Protein Data Bank, AlphaFold DB, gnomAD constraint, Open Targets, ClinGen, MaveDB, LitVar.
Notable AVPR2 variants
Examples include M1?, L2P, M3I, M3V, M3L, A4T, A4V, A4E. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.
- M1?, NCI-TCGA TCGA novel, Variant assessed as somatic; high impact.
- L2P (p.Leu2Pro), cosmic curated COSV61687, CADD 10.30, PolyPhen-2 0.00
- M3I (p.Met3Ile), TOPMed rs2064953668, CADD 5.51, PolyPhen-2 0.00
- M3V (p.Met3Val), cosmic curated COSV10590
- M3L (p.Met3Leu), gnomAD X-153905152-A-C, CADD 0.02, PolyPhen-2 0.00
- A4T (p.Ala4Thr), NCI-TCGA Cosmic COSV1005, cosmic curated COSV10050, Variant assessed as somatic; moderate impact.
- A4V (p.Ala4Val), ExAC rs782726046, gnomAD rs782726046, CADD 2.81, PolyPhen-2 0.00
- A4E (p.Ala4Glu), gnomAD X-153905156-C-A, CADD 5.88, PolyPhen-2 0.04
- A4A (p.Ala4Ala), rs61748993, gnomAD X-153905157-G-A, CADD 0.25
- S5P (p.Ser5Pro), gnomAD rs1557100300, CADD 11.60, PolyPhen-2 0.00
- S5Y (p.Ser5Tyr), TOPMed rs1197684219, gnomAD rs1197684219, CADD 10.40, PolyPhen-2 0.01
- T6A (p.Thr6Ala), gnomAD X-153905161-A-G, CADD 5.09, PolyPhen-2 0.00
- T6T (p.Thr6Thr), rs1473798821, gnomAD X-153905163-C-T, CADD 4.94
- T7S (p.Thr7Ser), rs5196, ClinGen CA10554909, ClinVar RCV000270798, ClinVar RCV000972199, CADD 1.10, PolyPhen-2 0.01, Benign, Diabetes insipidus, nephrogenic, X-linked; not provided
- S8=, rs201419746, NCI-TCGA Cosmic COSV6168, Variant assessed as somatic; low impact.
- S8S (p.Ser8Ser), rs201419746, gnomAD X-153905169-C-T, CADD 0.01
- A9G (p.Ala9Gly), TOPMed rs1170533809, gnomAD rs1170533809
- A9T (p.Ala9Thr), rs368567969, NCI-TCGA Cosmic COSV6168, cosmic curated COSV61686, ExAC rs368567969, CADD 24.60, PolyPhen-2 0.00, Variant assessed as somatic; moderate impact.
- A9V (p.Ala9Val), cosmic curated COSV61686, TOPMed rs1170533809, gnomAD rs1170533809, CADD 16.30, PolyPhen-2 0.00
- A9D (p.Ala9Asp), gnomAD X-153905532-C-A, CADD 15.90, PolyPhen-2 0.21
- V10M (p.Val10Met), TOPMed rs2064956784, CADD 11.10, PolyPhen-2 0.20
- V10L (p.Val10Leu), gnomAD X-153905534-G-T, CADD 6.94, PolyPhen-2 0.01
- V10V (p.Val10Val), gnomAD X-153905536-G-C, CADD 2.60
- P11T (p.Pro11Thr), gnomAD X-153905537-C-A, CADD 10.20, PolyPhen-2 0.01
- P11S (p.Pro11Ser), gnomAD X-153905537-C-T, CADD 8.57, PolyPhen-2 0.07
- P11H (p.Pro11His), gnomAD X-153905538-C-A, CADD 13.00, PolyPhen-2 0.40
- P11P (p.Pro11Pro), gnomAD X-153905539-T-C, CADD 1.52
- G12E (p.Gly12Glu), rs2071126, ClinGen CA10554938, cosmic curated COSV61685, ClinVar RCV000247065, CADD 8.04, PolyPhen-2 0.00, Benign, not specified; not provided; Diabetes insipidus, nephrogenic, X-linked
- G12R (p.Gly12Arg), gnomAD X-153905540-G-A, CADD 0.36, PolyPhen-2 0.00
- G12V (p.Gly12Val), gnomAD X-153905541-G-T, CADD 8.61, PolyPhen-2 0.01
- G12G (p.Gly12Gly), gnomAD X-153905542-G-A, CADD 3.01
- H13Y (p.His13Tyr), gnomAD rs1557100409
- H13N (p.His13Asn), gnomAD X-153905543-C-A, CADD 1.90, PolyPhen-2 0.00
- H13R (p.His13Arg), gnomAD X-153905544-A-G, CADD 0.76, PolyPhen-2 0.00
- P14L (p.Pro14Leu), Ensembl rs2064956917, CADD 1.08, PolyPhen-2 0.00
- P14S (p.Pro14Ser), gnomAD X-153905546-C-T, CADD 2.31, PolyPhen-2 0.00
- P14T (p.Pro14Thr), gnomAD X-153905546-C-A, CADD 1.79, PolyPhen-2 0.01
- P14H (p.Pro14His), gnomAD X-153905547-C-A, CADD 1.42, PolyPhen-2 0.00
- P14P (p.Pro14Pro), gnomAD X-153905548-C-A, CADD 4.51
- S15P (p.Ser15Pro), gnomAD rs1557100413, CADD 11.20, PolyPhen-2 0.00
- S15Y (p.Ser15Tyr), gnomAD X-153905550-C-A, CADD 5.54, PolyPhen-2 0.01
- S15S (p.Ser15Ser), gnomAD X-153905551-T-G, CADD 0.59
- L16M (p.Leu16Met), gnomAD X-153905552-C-A, CADD 0.54, PolyPhen-2 0.09
- L16P (p.Leu16Pro), gnomAD X-153905553-T-C, CADD 0.04, PolyPhen-2 0.00
- L16L (p.Leu16Leu), gnomAD X-153905554-G-T, CADD 0.29
- P17H (p.Pro17His), NCI-TCGA TCGA novel, CADD 6.33, PolyPhen-2 0.00, Variant assessed as somatic; moderate impact.
- P17T (p.Pro17Thr), gnomAD X-153905555-C-A, CADD 5.30, PolyPhen-2 0.00
- P17L (p.Pro17Leu), gnomAD X-153905556-C-T, CADD 5.24, PolyPhen-2 0.00
- P17P (p.Pro17Pro), gnomAD X-153905557-C-T, CADD 3.98
- S18R (p.Ser18Arg), TOPMed rs2064957104
- S18N (p.Ser18Asn), gnomAD X-153905559-G-A, CADD 5.48, PolyPhen-2 0.00
- p.Leu19 Ser21del, rs782021693, gnomAD X-153905551-TCTGC, CADD 11.80
- L19M (p.Leu19Met), gnomAD X-153905561-C-A, CADD 5.01, PolyPhen-2 0.06
- L19P (p.Leu19Pro), gnomAD X-153905562-T-C, CADD 9.97, PolyPhen-2 0.00
- P20T (p.Pro20Thr), gnomAD X-153905564-C-A, CADD 5.17, PolyPhen-2 0.01
- P20S (p.Pro20Ser), gnomAD X-153905564-C-T, CADD 4.13, PolyPhen-2 0.00
- P20P (p.Pro20Pro), gnomAD X-153905566-C-A, CADD 1.07
- S21G (p.Ser21Gly), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact.
- S21N (p.Ser21Asn), gnomAD X-153905568-G-A, CADD 14.70, PolyPhen-2 0.02
- S21S (p.Ser21Ser), gnomAD X-153905569-C-T, CADD 10.20
- N22D (p.Asn22Asp), gnomAD X-153905570-A-G, CADD 22.60, PolyPhen-2 0.68
- N22K (p.Asn22Lys), gnomAD X-153905572-C-A, CADD 20.20, PolyPhen-2 0.26
- N22N (p.Asn22Asn), gnomAD X-153905572-C-T, CADD 8.79
- S23I (p.Ser23Ile), gnomAD X-153905574-G-T, CADD 19.60, PolyPhen-2 0.05
- S23R (p.Ser23Arg), gnomAD X-153905575-C-G, CADD 16.00, PolyPhen-2 0.00
- S23S (p.Ser23Ser), rs377144623, gnomAD X-153905575-C-T, CADD 10.50
- S24I (p.Ser24Ile), cosmic curated COSV61686, CADD 22.90, PolyPhen-2 0.02
- Q25R (p.Gln25Arg), Ensembl rs2064957197
- Q25L (p.Gln25Leu), gnomAD X-153905580-A-T, CADD 11.70, PolyPhen-2 0.01
- Q25Q (p.Gln25Gln), rs1557100423, gnomAD X-153905581-G-A, CADD 5.49
- E26Q (p.Glu26Gln), rs2521150781, ClinGen CA415103325, ClinVar RCV002698617, NCI-TCGA TCGA novel, Uncertain significance, Inborn genetic diseases
- E26* (p.Glu26Ter), gnomAD X-153905582-G-T, CADD 33.00
- R27G (p.Arg27Gly), 1000Genomes rs782494738, ExAC rs782494738, gnomAD rs782494738, CADD 8.84, PolyPhen-2 0.00
- R27S (p.Arg27Ser), rs1221495795, ClinGen CA415103337, ClinVar RCV001165926, TOPMed rs1221495795, CADD 5.87, PolyPhen-2 0.00, Uncertain significance, Diabetes insipidus, nephrogenic, X-linked
- R27R (p.Arg27Arg), rs1221495795, gnomAD X-153905587-G-A, CADD 4.24
- P28P (p.Pro28Pro), rs782289888, gnomAD X-153905590-A-C, CADD 1.57
- D30E (p.Asp30Glu), Ensembl rs2064957467
- D30N (p.Asp30Asn), rs2521150888, ClinGen CA415103349, ClinVar RCV002787982, Uncertain significance, Inborn genetic diseases
- T31N (p.Thr31Asn), gnomAD X-153905598-C-A, CADD 1.08, PolyPhen-2 0.01
- T31T (p.Thr31Thr), rs782394141, gnomAD X-153905599-C-T, CADD 1.57
- R32Q (p.Arg32Gln), cosmic curated COSV61686, TOPMed rs1228462503, CADD 23.20, PolyPhen-2 1.00, Uncertain significance, Inborn genetic diseases
- R32W (p.Arg32Trp), TOPMed rs1276736538, gnomAD rs1276736538, CADD 20.20, PolyPhen-2 1.00
- D33H (p.Asp33His), TOPMed rs1338243434, gnomAD rs1338243434
- D33N (p.Asp33Asn), TOPMed rs1338243434, gnomAD rs1338243434, CADD 8.71, PolyPhen-2 0.04
- P34A (p.Pro34Ala), Ensembl rs1010873312, CADD 4.34, PolyPhen-2 0.00
- P34L (p.Pro34Leu), rs781991255, ClinGen CA10554944, ClinVar RCV002677867, ClinVar RCV005050768, CADD 3.45, PolyPhen-2 0.00, Conflicting interpretations, Inborn genetic diseases; Nephrogenic syndrome of inappropriate antidiuresis; Dia
- P34P (p.Pro34Pro), rs782103110, gnomAD X-153905608-G-A, CADD 0.50
- L35R (p.Leu35Arg), gnomAD rs1557100443, CADD 9.73, PolyPhen-2 0.00
- L35V (p.Leu35Val), gnomAD rs1557100441, CADD 2.47, PolyPhen-2 0.00
- L35L (p.Leu35Leu), gnomAD X-153905611-G-T, CADD 3.71
- L36P (p.Leu36Pro), rs2148514200, ClinGen CA415103388, ClinVar RCV002049533, Ensembl rs2148514200, AlphaMissense 0.35, MetaLR 0.23, Uncertain significance, not provided
- L36V (p.Leu36Val), gnomAD X-153905612-C-G, CADD 18.30, PolyPhen-2 0.79
- L36L (p.Leu36Leu), rs1331353572, gnomAD X-153905612-C-T, CADD 3.84
- R38L (p.Arg38Leu), cosmic curated COSV61686
- R38Q (p.Arg38Gln), rs782052413, ClinGen CA10554948, NCI-TCGA Cosmic COSV6168, ClinVar RCV002961467, CADD 0.02, PolyPhen-2 0.00, Likely benign, Inborn genetic diseases
- R38W (p.Arg38Trp), 1000Genomes rs781902048, ExAC rs781902048, TOPMed rs781902048, gnomAD rs781902048, CADD 17.50, PolyPhen-2 0.70
- R38R (p.Arg38Arg), gnomAD X-153905620-G-A, CADD 3.21
- A39V (p.Ala39Val), TOPMed rs2064957926, CADD 0.80, PolyPhen-2 0.01
- A39T (p.Ala39Thr), gnomAD X-153905621-G-A, CADD 16.10, PolyPhen-2 0.34
- A39E (p.Ala39Glu), gnomAD X-153905622-C-A, CADD 16.50, PolyPhen-2 0.86
- A39A (p.Ala39Ala), rs374487946, gnomAD X-153905623-G-A, CADD 0.21
- E40E (p.Glu40Glu), rs12842582, gnomAD X-153905626-G-A, CADD 5.26
- L41L (p.Leu41Leu), gnomAD X-153905629-G-C, CADD 4.78
- A42G (p.Ala42Gly), 1000Genomes rs5198, ESP rs5198, ExAC rs5198, TOPMed rs5198, Benign
- A42V (p.Ala42Val), rs5198, ClinGen CA10554950, ClinVar RCV000274580, ClinVar RCV000882981, CADD 16.40, PolyPhen-2 0.31, Benign, not provided; not specified; Diabetes insipidus, nephrogenic, X-linked
- A42T (p.Ala42Thr), gnomAD X-153905630-G-A, CADD 17.00, PolyPhen-2 0.28
- A42A (p.Ala42Ala), rs2234695, gnomAD X-153905632-G-A, CADD 7.35
- L43P (p.Leu43Pro), UniProt VAR 015297, Pathogenic, in NDI1
- L43L (p.Leu43Leu), rs1557100451, gnomAD X-153905635-G-A, CADD 6.84
- L44F (p.Leu44Phe), rs2521151410, ClinGen CA415103871, ClinVar RCV003560305, ClinVar RCV006562213, Pathogenic/Likely pathogenic, Diabetes insipidus, nephrogenic, X-linked; not provided
- L44P (p.Leu44Pro), UniProt VAR 003517, Pathogenic, in NDI1
- I46K (p.Ile46Lys), rs104894759, ClinGen CA255578, ClinVar RCV000011599, UniProt VAR 015298, AlphaMissense 0.11, MetaLR 0.03, Pathogenic, Diabetes insipidus, nephrogenic, X-linked
- I46M (p.Ile46Met), ExAC rs782757546, gnomAD rs782757546, CADD 0.01, PolyPhen-2 0.03
- I46T (p.Ile46Thr), gnomAD rs104894759, AlphaMissense 0.11, MetaLR 0.03, Uncertain significance, Diabetes insipidus, nephrogenic, X-linked; Nephrogenic syndrome of inappropriate
- I46I (p.Ile46Ile), rs782757546, gnomAD X-153905644-A-C, CADD 1.23
- F48S (p.Phe48Ser), gnomAD X-153905649-T-C, CADD 24.80, PolyPhen-2 0.97
- F48F (p.Phe48Phe), gnomAD X-153905650-T-C, CADD 6.25
- V49A (p.Val49Ala), gnomAD rs1557100457, CADD 17.00, PolyPhen-2 0.04
- V49M (p.Val49Met), TOPMed rs2064958244, gnomAD rs2064958244, CADD 18.70
- V51G (p.Val51Gly), ExAC rs781837679, gnomAD rs781837679, CADD 23.40, PolyPhen-2 0.36
- V51A (p.Val51Ala), gnomAD X-153905658-T-C, CADD 17.00, PolyPhen-2 0.01
- A52G (p.Ala52Gly), ExAC rs782464773, gnomAD rs782464773, CADD 17.90, PolyPhen-2 0.01
- A52S (p.Ala52Ser), NCI-TCGA Cosmic COSV6168, cosmic curated COSV61686, Variant assessed as somatic; moderate impact.
- A52V (p.Ala52Val), ExAC rs782464773, gnomAD rs782464773, CADD 18.80, PolyPhen-2 0.01
- A52A (p.Ala52Ala), rs781791407, gnomAD X-153905662-C-T, CADD 8.87
- L53R (p.Leu53Arg), UniProt VAR 015299, Pathogenic, in NDI1
- L53L (p.Leu53Leu), gnomAD X-153905665-G-C, CADD 7.98
- S54G (p.Ser54Gly), gnomAD X-153905666-A-G, CADD 16.70, PolyPhen-2 0.00
- S54R (p.Ser54Arg), gnomAD X-153905666-A-C, CADD 23.30, PolyPhen-2 0.81
- S54I (p.Ser54Ile), gnomAD X-153905667-G-T, CADD 25.30, PolyPhen-2 0.62
- S54T (p.Ser54Thr), gnomAD X-153905667-G-C, CADD 22.70, PolyPhen-2 0.57
- S54S (p.Ser54Ser), gnomAD X-153905668-C-T, CADD 11.70
- N55D (p.Asn55Asp), UniProt VAR 015300, Pathogenic, in NDI1
- N55H (p.Asn55His), UniProt VAR 015301, Pathogenic, in NDI1
- N55S (p.Asn55Ser), NCI-TCGA TCGA novel, Variant assessed as somatic; moderate impact., in NDI1
- N55N (p.Asn55Asn), rs782545799, gnomAD X-153905671-T-C, CADD 1.69
- G56S (p.Gly56Ser), ESP rs377695589, ExAC rs377695589, gnomAD rs377695589
- G56V (p.Gly56Val), gnomAD X-153905673-G-T, CADD 15.80, PolyPhen-2 0.01
- G56G (p.Gly56Gly), gnomAD X-153905674-C-T, CADD 9.24
- L57L (p.Leu57Leu), gnomAD X-153905675-C-T, CADD 5.95
- V58A (p.Val58Ala), ExAC rs782247846, gnomAD rs782247846, CADD 24.60, PolyPhen-2 0.96
- V58M (p.Val58Met), gnomAD X-153905678-G-A, CADD 24.50, PolyPhen-2 0.99
- V58V (p.Val58Val), rs201810684, gnomAD X-153905680-G-A, CADD 6.03
- L59M (p.Leu59Met), NCI-TCGA Cosmic COSV1005, cosmic curated COSV10050, Variant assessed as somatic; moderate impact., in NDI1
- L59P (p.Leu59Pro), rs193922112, ClinGen CA260158, ClinVar RCV000029386, UniProt VAR 015302, CADD 25.30, PolyPhen-2 1.00, Likely pathogenic, Nephrogenic diabetes insipidus
- L59V (p.Leu59Val), NCI-TCGA Cosmic COSV1005, Variant assessed as somatic; moderate impact., in NDI1
- A60V (p.Ala60Val), cosmic curated COSV61687, ExAC rs782598402, TOPMed rs782598402, gnomAD rs782598402, CADD 13.50, PolyPhen-2 0.01, Uncertain significance, Inborn genetic diseases
- A60T (p.Ala60Thr), gnomAD X-153905684-G-A, CADD 16.90, PolyPhen-2 0.18
- A60A (p.Ala60Ala), rs5199, gnomAD X-153905686-G-A, CADD 5.87
- A61G (p.Ala61Gly), Ensembl rs2148514272
- A61P (p.Ala61Pro), ESP rs148230511, ExAC rs148230511, TOPMed rs148230511, gnomAD rs148230511
- A61T (p.Ala61Thr), ESP rs148230511, ExAC rs148230511, TOPMed rs148230511, gnomAD rs148230511, CADD 19.30, PolyPhen-2 0.10
- A61V (p.Ala61Val), UniProt VAR 015303, CADD 12.40, PolyPhen-2 0.01
- L62P (p.Leu62Pro), rs2521151990, ClinGen CA415104099, ClinVar RCV003336651, UniProt VAR 015304, Likely pathogenic, Nephrogenic syndrome of inappropriate antidiuresis
- L62V (p.Leu62Val), ExAC rs782024865, gnomAD rs782024865, CADD 22.70, PolyPhen-2 1.00
- A63T (p.Ala63Thr), cosmic curated COSV61686
- A63V (p.Ala63Val), gnomAD X-153905694-C-T, CADD 0.08, PolyPhen-2 0.01
- A63A (p.Ala63Ala), rs140156037, gnomAD X-153905695-T-C, CADD 1.64
- R64Q (p.Arg64Gln), TOPMed rs963081717, gnomAD rs963081717, CADD 22.80, PolyPhen-2 0.97
- R64W (p.Arg64Trp), rs150351033, ClinGen CA10554968, cosmic curated COSV61686, ClinVar RCV000889333, CADD 22.00, PolyPhen-2 1.00, Likely benign, not provided
- R64R (p.Arg64Arg), rs781992482, gnomAD X-153905698-G-A, CADD 2.05
- R65Q (p.Arg65Gln), rs782106562, ExAC rs782106562, TOPMed rs782106562, gnomAD rs782106562, CADD 13.50, PolyPhen-2 0.01, Likely benign, Inborn genetic diseases
- R65W (p.Arg65Trp), rs138019778, ClinGen CA337263518, cosmic curated COSV61685, ClinVar RCV002789065, CADD 22.90, PolyPhen-2 0.83, Conflicting interpretations, Nephrogenic syndrome of inappropriate antidiuresis; Diabetes insipidus, nephroge
- R65R (p.Arg65Arg), rs138019778, gnomAD X-153905699-C-A, CADD 5.60
- G66S (p.Gly66Ser), ExAC rs782735128, gnomAD rs782735128, CADD 18.90, PolyPhen-2 0.94
- G66C (p.Gly66Cys), gnomAD X-153905702-G-T, CADD 22.60, PolyPhen-2 0.98
- R67P (p.Arg67Pro), TOPMed rs1557100504, gnomAD rs1557100504, Uncertain significance
- R67Q (p.Arg67Gln), TOPMed rs1557100504, gnomAD rs1557100504, CADD 12.60, PolyPhen-2 0.12, Uncertain significance, Diabetes insipidus, nephrogenic, X-linked; Nephrogenic syndrome of inappropriate
- R67W (p.Arg67Trp), cosmic curated COSV61687, ExAC rs781937818, TOPMed rs781937818, gnomAD rs781937818, CADD 23.40, PolyPhen-2 0.98
- p.Arg67 Gly69del, rs782292545, gnomAD X-153905695-TCGGC, CADD 12.20
- R67G (p.Arg67Gly), gnomAD X-153905705-C-G, CADD 22.80, PolyPhen-2 0.86
- R68P (p.Arg68Pro), 1000Genomes rs61733408, ESP rs61733408, ExAC rs61733408, TOPMed rs61733408, CADD 24.60, PolyPhen-2 0.99, Benign
- R68Q (p.Arg68Gln), rs61733408, ClinGen CA10554974, ClinVar RCV000882812, 1000Genomes rs61733408, CADD 23.00, PolyPhen-2 0.50, Benign, not provided
- R68W (p.Arg68Trp), rs782054894, ClinGen CA10554973, NCI-TCGA Cosmic COSV6168, cosmic curated COSV61686, CADD 21.80, PolyPhen-2 1.00, Uncertain significance, not provided; Diabetes insipidus, nephrogenic, X-linked
- R68R (p.Arg68Arg), gnomAD X-153905710-G-A, CADD 5.66
- H70Q (p.His70Gln), TOPMed rs2064959317, gnomAD rs2064959317, CADD 12.40, PolyPhen-2 0.01
- W71* (p.Trp71Ter), rs2521152444, ClinGen CA415104260, ClinVar RCV003559467, Pathogenic
- W71R (p.Trp71Arg), TOPMed rs2064959351, gnomAD rs2064959351, CADD 19.60, PolyPhen-2 0.02
- A72T (p.Ala72Thr), gnomAD rs1557100522, CADD 23.00, PolyPhen-2 0.68
- A72V (p.Ala72Val), TOPMed rs1344096618, gnomAD rs1344096618, CADD 24.10, PolyPhen-2 0.97
Public AVPR2 analysis runs
- AVPR2 analysis run — AVPR2 (872 variants) — completed 2026-08-28