I27V (p.Ile27Val) variant of ADA (Adenosine deaminase)

I27V (p.Ile27Val) in ADA (Adenosine deaminase) is a missense change. Clinical records from ClinVar and UniProt describe it as uncertain significance in the context of Severe combined immunodeficiency, autosomal recessive, T cell-negative, B cell-n. The available variant effect predictions contribute to a CATVariant prioritization score of 0.50 / 1. The record also includes population frequency data and structural context.

I27V (p.Ile27Val) variant details