E354V (p.Glu354Val) variant of ACAT1 (P24752)

E354V (p.Glu354Val) in ACAT1 (P24752) is a missense change. Clinical records from ClinVar, EBI, and UniProt describe it as likely pathogenic in the context of Deficiency of acetyl-CoA acetyltransferase. The available variant effect predictions contribute to a CATVariant prioritization score of 0.97 / 1. The record also includes structural context.

E354V (p.Glu354Val) variant details