ABCC9 (O60706) variants and mutations

ABCC9 (also known as O60706) is a human protein-coding gene encoding an ATP-binding cassette sub-family C member 9 protein. A regulatory subunit of ATP-sensitive potassium (KATP) channels, partnering with KCNJ11 or KCNJ8 to control channel activation. It is a multi-pass membrane protein with important roles in cardiac and smooth-muscle excitability, and altered ABCC9 function is associated with cardiomyopathy, atrial fibrillation, and neurodevelopmental syndromes. This analysis covers 2,246 ABCC9 variants and mutations. Of these, 49% have computational variant effect predictions. Disease context includes Hypertrichotic osteochondrodysplasia, Cantu type, hypertrichotic osteochondrodysplasia Cantu type, and dilated cardiomyopathy 1O. Example ABCC9 variants include M1?, M1I, and S2G.

Variant analysis overview

Variant and mutation evidence

Clinical, disease, and population context

Protein structure and variant hotspots

Data sources

Evidence in this analysis draws on EBI Proteins Variation, UniProt, gnomAD v4, EuropePMC, 3D Hotspot Analysis, Interaction Network Analysis, AlphaFold DB, gnomAD constraint, Open Targets, ClinGen, PharmGKB, MaveDB, LitVar.

Notable ABCC9 variants

Examples include M1?, M1I, S2G, S2N, L3V, G7D, G7S, G7V. Listed records include available protein-change notation, database identifiers, clinical classifications, computational predictions, population evidence, experimental measurements, and disease context.